2026 ICD-10-CM Diagnosis Code I78.0Hereditary hemorrhagic telangiectasia

ICD-10-CM Codes›I00–I99›I70-I79›I78

ICD-10-CM I78.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I78.0 is a billable ICD-10-CM diagnosis code for hereditary hemorrhagic telangiectasia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified circulatory disease.

Code Identity

ICD-10-CM Code
I78.0
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary hemorrhagic telangiectasia
Short Description
Hereditary hemorrhagic telangiectasia
Same as the full description in the CMS dataset.
Parent Code
I78
Diseases of capillaries

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI70-I79Diseases of arteries, arterioles and capillaries
CategoryI78Diseases of capillaries
This CodeI78.0Hereditary hemorrhagic telangiectasia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormally short little finger
  • Conjunctival telangiectasis
  • Epilepsy telangiectasia syndrome
  • Familial cutaneous telangiectasia and oropharyngeal cancer predisposition syndrome
  • Hereditary benign telangiectasia
  • Hereditary dysplasia of blood vessel
  • Hereditary hemorrhagic telangiectasia of gingiva
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Juvenile polyposis syndrome
  • Juvenile polyposis syndrome with hereditary hemorrhagic telangiectasia
  • Osler hemorrhagic telangiectasia syndrome
  • Vascular abnormality of conjunctiva

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Rendu-Osler-Weber disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Angioma
      • hemorrhagicum hereditaria
    • Angiomatosis
      • hemorrhagic familial
    • Angiomatosis
      • hereditary familial
    • Babington's disease(familial hemorrhagic telangiectasia)
    • Disease, diseased
      • Babington's (familial hemorrhagic telangiectasia)
    • Disease, diseased
      • Goldstein's (familial hemorrhagic telangiectasia)
    • Disease, diseased
      • Osler-Rendu (familial hemorrhagic telangiectasia)
    • Disease, diseased
      • Rendu-Osler-Weber (familial hemorrhagic telangiectasia)
    • Epistaxis(multiple)
      • hereditary
    • Goldstein's disease(familial hemorrhagic telangiectasia)
    • Osler(-Weber)-Rendu disease
    • Rendu-Osler-Weber disease or syndrome
    • Syndrome
      • Osler-Weber-Rendu
    • Syndrome
      • Rendu-Osler-Weber
    • Telangiectasia, telangiectasis(verrucous)
      • familial
    • Telangiectasia, telangiectasis(verrucous)
      • hemorrhagic, hereditary (congenital) (senile)
    • Telangiectasia, telangiectasis(verrucous)
      • hereditary, hemorrhagic (congenital) (senile)
    • Weber-Osler syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR032
Other specified and unspecified circulatory disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Bleeding Disorders

Normally, if you get hurt, your body forms a blood clot to stop the bleeding. For blood to clot, your body needs cells called platelets and proteins known as clotting factors. If you have a bleeding disorder, you either do not have enough platelets or clotting factors or they don't work the way they should.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I78.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
448.0 Heredit hemorr telangiec
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I78.0Overview

Is I78.0 (Diseases of capillaries) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary hemorrhagic telangiectasia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does I78.0 group to?

When hereditary hemorrhagic telangiectasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I78.0?

Under the General Equivalence Mappings, hereditary hemorrhagic telangiectasia converts to ICD-9-CM 448.0 (heredit hemorr telangiec). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.