2027 ICD-10-CM Diagnosis Code I78.0Hereditary hemorrhagic telangiectasia
ICD-10-CM Codes›I00–I99›I70-I79›I78
- Billable — Valid for Submission
- Chronic Condition
I78.0 is a billable ICD-10-CM diagnosis code for hereditary hemorrhagic telangiectasia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 299 through 301. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified circulatory disease.
I78.0 no longer risk-adjusts for Medicare Advantage: it mapped to HCC 108 under the retired CMS-HCC V24 model through payment year 2025 but maps to no category in the live V28 model. It still risk-adjusts in the PACE (CMS-HCC V22) category 108, ESRD (V21) category 108, and ESRD (V24) category 108 for payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
I78.0 no longer risk-adjusts for Medicare Advantage: it maps to no payment category in the live CMS-HCC V28 model, although it still risk-adjusts in the other CMS models shown below.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Abnormally short little finger
- Congenital vascular anomaly of eye
- Conjunctival telangiectasis
- Epilepsy telangiectasia syndrome
- Familial cutaneous telangiectasia and oropharyngeal cancer predisposition syndrome
- Hamartomatous polyposis of gastrointestinal tract
- Hereditary benign telangiectasia
- Hereditary dysplasia of blood vessel
- Hereditary hemorrhagic telangiectasia of gingiva
- Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
- Juvenile polyposis syndrome
- Juvenile polyposis syndrome with hereditary hemorrhagic telangiectasia
- Osler hemorrhagic telangiectasia syndrome
- Vascular abnormality of conjunctiva
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to I78.0: its own notes plus those printed at Chapter 9. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Rendu-Osler-Weber disease
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Angioma See Also: Hemangioma, by site;
hemorrhagic familial I78.0
hereditary familial I78.0
Disease, diseased See Also: Syndrome;
Syndrome See Also: Disease;
Osler-Weber-Rendu I78.0
Rendu-Osler-Weber I78.0
Weber-Osler syndrome I78.0
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Telangiectasia, Hereditary Hemorrhagic
an autosomal dominant vascular anomaly characterized by telangiectases of the skin and mucous membranes and by recurrent gastrointestinal bleeding. this disorder is caused by mutations of a gene (on chromosome 9q3) which encodes endoglin, a membrane glycoprotein that binds transforming growth factor beta.
Patient EducationClinical
Bleeding Disorders
Normally, if you get hurt, your body forms a blood clot to stop the bleeding. For blood to clot, your body needs cells called platelets and proteins known as clotting factors. If you have a bleeding disorder, you either do not have enough platelets or clotting factors or they don't work the way they should.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert I78.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About I78.0Overview
What is the ICD-10 code for hereditary hemorrhagic telangiectasia?
The ICD-10-CM code for hereditary hemorrhagic telangiectasia is I78.0 (sometimes written as I780). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is I78.0 (Diseases of capillaries) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report hereditary hemorrhagic telangiectasia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does I78.0 group to?
When hereditary hemorrhagic telangiectasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 301, 300, 299, with relative weights from 0.7132 to 1.5840 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of I78.0?
Under the General Equivalence Mappings, hereditary hemorrhagic telangiectasia converts to ICD-9-CM 448.0 (heredit hemorr telangiec). The mapping is a direct match.
Does I78.0 risk-adjust for Medicare Advantage payment?
Not for Medicare Advantage. I78.0 mapped to HCC 108 in the retired CMS-HCC V24 model, which last determined payment in 2025, but it maps to no category in the live V28 model; see all codes that no longer risk-adjust. It still risk-adjusts in the PACE (CMS-HCC V22) category 108 (Vascular Disease), ESRD (V21) category 108 (Vascular Disease), and ESRD (V24) category 108 (Vascular Disease).
