ICD-10-CM Code E34.0

Carcinoid syndrome

Version 2021 Billable Code

Valid for Submission

E34.0 is a billable code used to specify a medical diagnosis of carcinoid syndrome. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code E34.0 might also be used to specify conditions or terms like carcinoid crisis, carcinoid heart disease, carcinoid syndrome, carcinoid syndrome diarrhea, carcinomatous myopathic syndrome, disorder of endocardium and heart valve, etc

Short Description:Carcinoid syndrome
Long Description:Carcinoid syndrome

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code E34.0:

  • May be used as an additional code to identify functional activity associated with a carcinoid tumor.

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code E34.0 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Carcinoid crisis
  • Carcinoid heart disease
  • Carcinoid syndrome
  • Carcinoid syndrome diarrhea
  • Carcinomatous myopathic syndrome
  • Disorder of endocardium and heart valve
  • Secondary myopathy

Clinical Information

  • MALIGNANT CARCINOID SYNDROME-. a symptom complex associated with carcinoid tumor and characterized by attacks of severe flushing of the skin diarrheal watery stools bronchoconstriction sudden drops in blood pressure edema and ascites. the carcinoid tumors are usually located in the gastrointestinal tract and metastasize to the liver. symptoms are caused by tumor secretion of serotonin prostaglandins and other biologically active substances. cardiac manifestations constitute carcinoid heart disease. dorland 27th ed; stedman 25th ed

Diagnostic Related Groups

The ICD-10 code E34.0 is grouped in the following groups for version MS-DRG V38.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2020 through 09/30/2021.


Convert E34.0 to ICD-9

  • 259.2 - Carcinoid syndrome

Code Classification

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Disorders of other endocrine glands (E20-E35)
      • Other endocrine disorders (E34)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients

Carcinoid Tumors

Carcinoid tumors are rare, slow-growing cancers. They usually start in the lining of the digestive tract or in the lungs. They grow slowly and don't produce symptoms in the early stages. As a result, the average age of people diagnosed with digestive or lung carcinoids is about 60.

In later stages the tumors sometimes produce hormones that can cause carcinoid syndrome. The syndrome causes flushing of the face and upper chest, diarrhea, and trouble breathing.

Surgery is the main treatment for carcinoid tumors. If they haven't spread to other parts of the body, surgery can cure the cancer.

  • 5-HIAA (Medical Encyclopedia)
  • Carcinoid syndrome (Medical Encyclopedia)
  • Serum serotonin level (Medical Encyclopedia)

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