2027 ICD-10-CM Diagnosis Code D00.1Carcinoma in situ of esophagus

ICD-10-CM Codes›C00–D49›D00-D09›D00

ICD-10-CM D00.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

D00.1 is a billable ICD-10-CM diagnosis code for carcinoma in situ of esophagus. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 374 through 376. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Gastrointestinal cancers - esophagus.

Code Identity

ICD-10-CM Code
D00.1
Billable Status
Yes — Valid for Submission
Code Describes
Carcinoma in situ of esophagus
Short Description
Carcinoma in situ of esophagus
Same as the full description in the CMS dataset.
Parent Code
Carcinoma in situ of oral cavity, esophagus and stomach

Code Classification

ChapterC00–D49Neoplasms
SectionD00-D09In situ neoplasms
CategoryD00Carcinoma in situ of oral cavity, esophagus and stomach
This CodeD00.1Carcinoma in situ of esophagus

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adenocarcinoma in situ of esophagus
  • Carcinoma in situ of abdominal part of esophagus
  • Carcinoma in situ of cervical esophagus
  • Carcinoma in situ of esophagus
  • Carcinoma in situ of lower third of esophagus
  • Carcinoma in situ of middle third of esophagus
  • Carcinoma in situ of thoracic part of esophagus
  • Carcinoma in situ of upper third of esophagus
  • Esophageal dysplasia
  • High grade squamous intraepithelial neoplasia of esophagus
  • Severe esophageal dysplasia
  • Squamous cell carcinoma in situ of esophagus
  • Squamous intraepithelial neoplasia of esophagus grade 3

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to D00.1: its own notes plus those printed at D00, block D00-D09, and Chapter 2. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

From Block D00-D09 In situ neoplasms applies to 106 codes
  • Bowen's disease
  • erythroplasia
  • grade III intraepithelial neoplasia
  • Queyrat's erythroplasia

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From D00 Carcinoma in situ of oral cavity, esophagus and stomach applies to 11 codes

Notes

General instructions on how these codes are used.

From Chapter 2 (C00-D49) Neoplasms applies to 1,730 codes
  • Functional activity
  • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Morphology [Histology]
  • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Primary malignant neoplasms overlapping site boundaries
  • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Malignant neoplasm of ectopic tissue
  • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name D00.1, its category, or a range that includes it.

Applicable To 1

These notes mention D00.1.

  • Z86.003 Personal history of in-situ neoplasm of oral cavity, esophagus and stomach
    Conditions classifiable to D00 names D00, which includes this code

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO012
Gastrointestinal cancers - esophagus
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Stage 0 Esophageal Cancer AJCC v7

    stage 0 includes: for squamous cell carcinoma: tis (hgd), n0, m0, g1, gx, tumor location: any. for adenocarcinoma: tis (hgd), n0, m0, g1, gx. tis: high-grade dysplasia. n0: no regional lymph node metastasis. m0: no distant metastasis. g1: well differentiated. gx: grade cannot be assessed-stage grouping as g1. tumor location: location of the primary cancer site is defined by the position of the upper (proximal) edge of the tumor in the esophagus. (ajcc 7th ed.)

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary
Malig.
Secondary
Ca
in situ
BenignUncertainUnspec.
esophagusC15.9C78.89D00.1D13.0D37.8D49.0
esophagus › abdominalC15.5C78.89D00.1D13.0D37.8D49.0
esophagus › cervicalC15.3C78.89D00.1D13.0D37.8D49.0
esophagus › distal (third)C15.5C78.89D00.1D13.0D37.8D49.0
esophagus › lower (third)C15.5C78.89D00.1D13.0D37.8D49.0
esophagus › middle (third)C15.4C78.89D00.1D13.0D37.8D49.0
esophagus › proximal (third)C15.3C78.89D00.1D13.0D37.8D49.0
esophagus › thoracicC15.4C78.89D00.1D13.0D37.8D49.0
esophagus › upper (third)C15.3C78.89D00.1D13.0D37.8D49.0

Patient EducationClinical

Esophageal Cancer

The esophagus is a hollow tube that carries food and liquids from your throat to your stomach. Early esophageal cancer usually does not cause symptoms. Later, you may have symptoms such as:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D00.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
230.1 Ca in situ esophagus
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About D00.1Overview

What is the ICD-10 code for carcinoma in situ of esophagus?

The ICD-10-CM code for carcinoma in situ of esophagus is D00.1 (sometimes written as D001). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is D00.1 (Carcinoma in situ of oral cavity, esophagus and stomach) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report carcinoma in situ of esophagus on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does D00.1 group to?

When carcinoma in situ of esophagus is the principal diagnosis on an inpatient stay, it groups to MS-DRG 375, 374, 376, with relative weights from 0.8925 to 2.1101 depending on complications. Higher weights mean higher Medicare reimbursement.

Can D00.1 be reported with a code from D03?

Not as a rule. The Excludes1 note at D00, which applies to D00.1, lists "melanoma in situ (D03.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of D00.1?

Under the General Equivalence Mappings, carcinoma in situ of esophagus converts to ICD-9-CM 230.1 (ca in situ esophagus). The mapping is a direct match.