2026 ICD-10-CM Diagnosis Code C75.4Malignant neoplasm of carotid body

ICD-10-CM Codes›C00–D49›C73-C75›C75

ICD-10-CM C75.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

C75.4 is a billable ICD-10-CM diagnosis code for malignant neoplasm of carotid body. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Endocrine system cancers - all other types.

Code Identity

ICD-10-CM Code
C75.4
Billable Status
Yes — Valid for Submission
Code Describes
Malignant neoplasm of carotid body
Short Description
Malignant neoplasm of carotid body
Same as the full description in the CMS dataset.
Parent Code
C75
Malignant neoplasm of other endocrine glands and related structures

Code Classification

ChapterC00–D49Neoplasms
SectionC73-C75Malignant neoplasms of thyroid and other endocrine glands
CategoryC75Malignant neoplasm of other endocrine glands and related structures
This CodeC75.4Malignant neoplasm of carotid body

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adenocarcinoma of carotid body
  • Adenocarcinoma of paraganglia
  • Malignant neoplasm of carotid body
  • Neoplasm of carotid body
  • Primary adenocarcinoma of carotid body
  • Primary adenocarcinoma of paraganglia
  • Primary malignant neoplasm of carotid body
  • Primary malignant neoplasm of paraganglion
  • Primary malignant paraganglioma of carotid body

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Paraganglioma
      • carotid body
        • malignant
    • Tumor
      • carotid body
        • malignant

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO056
Endocrine system cancers - all other types
Default principal diagnosis: inpatient Yes · outpatient Yes

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary		Malig.
Secondary		Ca
in situ		BenignUncertainUnspec.
carotid (artery) › bodyC75.4C79.89–D35.5D44.6D49.7

Patient EducationClinical

Cancer

Cancer is not just one disease but many diseases. Cancer begins in your cells, which are the building blocks of your body. Usually, your body forms new cells as needed, replacing old cells that die. Sometimes this process goes wrong. New cells grow even when you don't need them, and old cells don't die when they should.

The full article covers:

  • What is cancer?
  • What are the types of cancer?
  • How does cancer develop?
  • What are the symptoms of cancer?
  • How is cancer diagnosed?
  • What are the treatments for cancer?
  • Can cancer be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert C75.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
194.5 Mal neo carotid body
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About C75.4Overview

Is C75.4 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report malignant neoplasm of carotid body on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of C75.4?

Under the General Equivalence Mappings, malignant neoplasm of carotid body converts to ICD-9-CM 194.5 (mal neo carotid body). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.