2026 ICD-10-CM Diagnosis Code Q76.49Other congenital malformations of spine, not associated with scoliosis

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q76

ICD-10-CM Q76.49
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q76.49 is a billable ICD-10-CM diagnosis code for other congenital malformations of spine, not associated with scoliosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 551 through 552. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q76.49
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of spine, not associated with scoliosis
Short Description
Oth congenital malform of spine, not associated w scoliosis
Parent Code
Q76.4
Other congenital malformations of spine, not associated with scoliosis

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ76Congenital malformations of spine and bony thorax
This CodeQ76.49Other congenital malformations of spine, not associated with scoliosis

Present on Admission (POA)Billing

Q76.49 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Absence of clavicle
  • Agenesis of cervical vertebra
  • Agenesis of vertebra
  • Anal atresia
  • Aphalangy, hemivertebra, urogenital, intestinal dysgenesis syndrome
  • Aplasia of bone of pelvis
  • Aplasia of bone of sacrum
  • Aplasia of cervical vertebral column
  • Aplasia of clavicle
  • Aplasia of vertebra
  • Aplasia of vertebral column
  • Arthropathy of cervical spine facet joint
  • Assimilation pelvis
  • Atlanto-occipital malformation
  • Autosomal dominant brachyolmia
  • Autosomal dominant spondylocostal dysostosis
  • Autosomal recessive brachyolmia
  • Bertolotti's syndrome
  • Bipartite ossification
  • Bipartite ossification of centrum of cervical vertebra
  • Bipartite ossification of centrum of lumbar vertebra
  • Bipartite ossification of centrum of sacral vertebra
  • Bipartite ossification of centrum of thoracic vertebra
  • Brachyolmia
  • Brachyolmia - Maroteaux type
  • Butterfly vertebra
  • Caudal appendage deafness syndrome
  • Cervical hemivertebra
  • Cervical hemivertebra - unbalanced
  • Cervical hemivertebra- balanced
  • Cleft cartilaginous centrum of cervical vertebra
  • Cleft cartilaginous centrum of lumbar vertebra
  • Cleft cartilaginous centrum of sacral vertebra
  • Cleft cartilaginous centrum of thoracic vertebra
  • Cleft palate with short stature and vertebral anomaly syndrome
  • Congenital abnormal fusion of arch of cervical vertebra
  • Congenital abnormal fusion of arch of lumbar vertebra
  • Congenital abnormal fusion of arch of sacral vertebra
  • Congenital abnormal fusion of arch of thoracic vertebra
  • Congenital abnormal fusion of centrum cartilage of cervical vertebra
  • Congenital abnormal fusion of centrum cartilage of lumbar vertebra
  • Congenital abnormal fusion of centrum cartilage of sacral vertebra
  • Congenital abnormal fusion of centrum cartilage of thoracic vertebra
  • Congenital abnormal fusion of centrum of cervical vertebra
  • Congenital abnormal fusion of centrum of lumbar vertebra
  • Congenital abnormal fusion of centrum of sacral vertebra
  • Congenital abnormal fusion of centrum of thoracic vertebra
  • Congenital abnormal shape of arch of cervical vertebra
  • Congenital abnormal shape of arch of lumbar vertebra
  • Congenital abnormal shape of arch of sacral vertebra
  • Congenital abnormal shape of arch of thoracic vertebra
  • Congenital abnormal shape of centrum of cervical vertebra
  • Congenital abnormal shape of centrum of lumbar vertebra
  • Congenital abnormal shape of centrum of sacral vertebra
  • Congenital abnormal shape of centrum of thoracic vertebra
  • Congenital absence of arch of cervical vertebra
  • Congenital absence of arch of lumbar vertebra
  • Congenital absence of arch of sacral vertebra
  • Congenital absence of arch of thoracic vertebra
  • Congenital absence of centrum of cervical vertebra
  • Congenital absence of centrum of lumbar vertebra
  • Congenital absence of centrum of sacral vertebra
  • Congenital absence of centrum of thoracic vertebra
  • Congenital absence of cervical vertebra
  • Congenital absence of coccyx bone
  • Congenital absence of lumbar vertebra
  • Congenital absence of sacral vertebra
  • Congenital absence of spine
  • Congenital absence of thoracic vertebra
  • Congenital absence of vertebra
  • Congenital anomaly of caudal vertebra
  • Congenital anomaly of cervical vertebra
  • Congenital anomaly of craniovertebral junction
  • Congenital anomaly of lumbar vertebra
  • Congenital anomaly of sacral vertebra
  • Congenital anomaly of spine
  • Congenital anomaly of thoracic vertebra
  • Congenital anomaly of vertebral region of back
  • Congenital aplasia of odontoid process
  • Congenital atresia of pharynx
  • Congenital brachyesophagus, intrathoracic stomach, vertebral anomalies syndrome
  • Congenital complete fusion of spine
  • Congenital coronal cleft of vertebra
  • Congenital deformity of lumbosacral joint
  • Congenital deformity of lumbosacral region
  • Congenital deformity of spine
  • Congenital diaphragmatic hernia
  • Congenital displacement of stomach
  • Congenital dysplasia of cervical vertebra
  • Congenital dysplasia of second lumbar vertebra
  • Congenital dysplasia of spine
  • Congenital facial asymmetry
  • Congenital fusion of spine
  • Congenital hemivertebra
  • Congenital hypoplasia of arch of cervical vertebra
  • Congenital hypoplasia of arch of lumbar vertebra
  • Congenital hypoplasia of arch of sacral vertebra
  • Congenital hypoplasia of arch of thoracic vertebra
  • Congenital hypoplasia of bone of pelvis
  • Congenital hypoplasia of centrum of vertebra
  • Congenital hypoplasia of cervical vertebral column
  • Congenital hypoplasia of facet joint of cervical spine
  • Congenital hypoplasia of odontoid process of axis
  • Congenital hypoplasia of vertebra
  • Congenital hypoplasia of vertebral column
  • Congenital instability of spine
  • Congenital kyphosis
  • Congenital kyphosis of thoracic spine
  • Congenital lumbosacral fusion
  • Congenital malposition of arch of cervical vertebra
  • Congenital malposition of arch of lumbar vertebra
  • Congenital malposition of arch of sacral vertebra
  • Congenital malposition of arch of thoracic vertebra
  • Congenital malposition of cervical vertebra
  • Congenital malposition of lumbar vertebra
  • Congenital malposition of sacral vertebra
  • Congenital malposition of thoracic vertebra
  • Congenital misalignment of arch of cervical vertebra
  • Congenital misalignment of arch of lumbar vertebra
  • Congenital misalignment of arch of sacral vertebra
  • Congenital misalignment of arch of thoracic vertebra
  • Congenital misalignment of centrum of cervical vertebra
  • Congenital misalignment of centrum of lumbar vertebra
  • Congenital misalignment of centrum of sacral vertebra
  • Congenital misalignment of centrum of thoracic vertebra
  • Congenital partial fusion of spine
  • Congenital partial fusion of spine - balanced
  • Congenital partial fusion of spine - unbalanced
  • Congenital partial fusion of spine with hemivertebra - balanced
  • Congenital partial fusion of spine with hemivertebra - unbalanced
  • Congenital sacrococcygeal anomaly
  • Congenital short esophagus
  • Congenital stenosis of cervical spinal canal
  • Congenital stenosis of spinal canal
  • Congenital vertebral, cardiac, renal anomalies syndrome
  • Crane Heise syndrome
  • Craniofacial microsomia
  • Cutaneous lesion resulting from spinal dysraphism
  • Defect of vertebral segmentation
  • Developmental anomaly of odontoid process of axis
  • Dumbbell ossification
  • Dumbbell ossification of centrum of cervical vertebra
  • Dumbbell ossification of centrum of lumbar vertebra
  • Dumbbell ossification of centrum of sacral vertebra
  • Dumbbell ossification of centrum of thoracic vertebra
  • Dumbbell-shaped cartilaginous centrum of cervical vertebra
  • Dumbbell-shaped cartilaginous centrum of lumbar vertebra
  • Dumbbell-shaped cartilaginous centrum of sacral vertebra
  • Dumbbell-shaped cartilaginous centrum of thoracic vertebra
  • Familial caudal dysgenesis
  • Hypoplasia of sacrum
  • Hypoplasia of spine
  • Imperforate oropharynx, costovertebral anomalies syndrome
  • Incomplete ossification of arch of cervical vertebra
  • Incomplete ossification of arch of lumbar vertebra
  • Incomplete ossification of arch of sacral vertebra
  • Incomplete ossification of arch of thoracic vertebra
  • Incomplete ossification of centrum of cervical vertebra
  • Incomplete ossification of centrum of lumbar vertebra
  • Incomplete ossification of centrum of sacral vertebra
  • Incomplete ossification of centrum of thoracic vertebra
  • Incomplete ossification of vertebra
  • Kyphosis of thoracic spine
  • Lack of ossification of arch of cervical vertebra
  • Lack of ossification of arch of lumbar vertebra
  • Lack of ossification of arch of sacral vertebra
  • Lack of ossification of arch of thoracic vertebra
  • Lack of ossification of centrum of cervical vertebra
  • Lack of ossification of centrum of lumbar vertebra
  • Lack of ossification of centrum of sacral vertebra
  • Lack of ossification of centrum of thoracic vertebra
  • Low assimilation pelvis
  • Lumbar hemivertebra
  • Lumbar hemivertebra - balanced
  • Lumbar hemivertebra - unbalanced
  • Lumbarized first sacral vertebra
  • Microcephaly with cervical spine fusion anomaly
  • Mirror polydactyly, vertebral segmentation and limb defect syndrome
  • Multiple congenital defects of vertebral segmentation
  • Occipitalization of atlas
  • Oculo-auriculo-vertebral spectrum
  • Pain in lumbar spine
  • Persistent human tail
  • PHAVER syndrome
  • Platyspondylia
  • Postaxial polydactyly, dental, vertebral anomalies syndrome
  • Posterior fusion of lumbosacral vertebrae and blepharoptosis syndrome
  • Progressive non-infectious anterior vertebral fusion
  • Sacral agenesis
  • Sacral agenesis, abnormal ossification of vertebral bodies, persistent notochordal canal syndrome
  • Sacral hemivertebra
  • Sacralization of fifth lumbar vertebra
  • Sacralization of lumbar vertebra
  • Spinal dysgenesis
  • Spinal stenosis in cervical region
  • Spondylocostal dysostosis with anal atresia and genitourinary malformation syndrome
  • Spondyloschisis
  • Straight back syndrome
  • Supernumerary arch of cervical vertebra
  • Supernumerary arch of lumbar vertebra
  • Supernumerary arch of sacral vertebra
  • Supernumerary arch of thoracic vertebra
  • Supernumerary centrum of cervical vertebra
  • Supernumerary centrum of lumbar vertebra
  • Supernumerary centrum of sacral vertebra
  • Supernumerary centrum of thoracic vertebra
  • Supernumerary cervical vertebra
  • Supernumerary lumbar vertebra
  • Supernumerary sacral vertebra
  • Supernumerary thoracic vertebra
  • Supernumerary vertebra
  • Thoracic hemivertebra
  • Thoracic hemivertebra - unbalanced
  • Thoracic hemivertebra- balanced
  • Transitional lumbosacral vertebra
  • Transitional vertebra
  • VACTEL syndrome
  • VACTERL syndrome with hydrocephalus
  • Verloes Bourguignon syndrome
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome
  • X-linked intellectual disability, global development delay, facial dysmorphism, sacral caudal remnant syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital absence of vertebra NOS
  • Congenital fusion of spine NOS
  • Congenital malformation of lumbosacral (joint) (region) NOS
  • Congenital malformation of spine NOS
  • Hemivertebra NOS
  • Malformation of spine NOS
  • Platyspondylisis NOS
  • Supernumerary vertebra NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • coccyx, congenital
    • Absence(of) (organ or part) (complete or partial)
      • sacrum, congenital
    • Absence(of) (organ or part) (complete or partial)
      • spine, congenital
    • Absence(of) (organ or part) (complete or partial)
      • vertebra, congenital
    • Accessory(congenital)
      • vertebra
    • Agenesis
      • coccyx
    • Agenesis
      • sacrum
    • Agenesis
      • spine
    • Agenesis
      • vertebra
    • Angulation
      • coccyx (acquired)
        • congenital NEC
    • Angulation
      • sacrum (acquired)
        • congenital NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • coccyx
    • Anomaly, anomalous(congenital) (unspecified type)
      • intervertebral cartilage or disc
    • Anomaly, anomalous(congenital) (unspecified type)
      • lumbosacral (joint) (region)
    • Anomaly, anomalous(congenital) (unspecified type)
      • sacrum NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • spine, spinal NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • spine, spinal NEC
        • column NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • vertebra
    • Bifurcation(congenital)
      • vertebra
    • Brevicollis
    • Deformity
      • lumbosacral (congenital) (joint) (region)
    • Dislocation(articular)
      • lumbosacral (vertebra)
        • congenital
    • Dislocation(articular)
      • spine
        • congenital
    • Dislocation(articular)
      • vertebra (articular process) (body) (traumatic)
        • congenital
    • Distortion(s) (congenital)
      • coccyx
    • Distortion(s) (congenital)
      • lumbar spine
    • Distortion(s) (congenital)
      • lumbosacral (joint) (region)
    • Distortion(s) (congenital)
      • sacrum
    • Distortion(s) (congenital)
      • spine
    • Distortion(s) (congenital)
      • vertebra
    • Failure, failed
      • segmentation
        • vertebra
    • Fusion, fused(congenital)
      • lumbosacral (acquired)
        • congenital
    • Fusion, fused(congenital)
      • spine (acquired) NEC
        • congenital
    • Half vertebra
    • Hemivertebra
    • Hypoplasia, hypoplastic
      • coccyx
    • Hypoplasia, hypoplastic
      • sacrum
    • Hypoplasia, hypoplastic
      • spine
    • Hypoplasia, hypoplastic
      • vertebra
    • Lumbarization, vertebra, congenital
    • Maldevelopment
      • spine
    • Malformation(congenital)
      • joint
        • lumbosacral
    • Malformation(congenital)
      • spine
    • Platyspondylisis
    • Sacralization
    • Segmentation, incomplete(congenital)
      • lumbosacral (joint) (vertebra)
    • Supernumerary(congenital)
      • vertebra
    • Syndrome
      • straight back, congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.

  • Congenital Kyphosis

    an abnormally increased curvature of the thoracic portion of the spine that is present at the time of birth.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q76.49 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.13 Cong absence of vertebra
Approximate The match is approximate rather than exact.
ICD-9-CM
756.14 Hemivertebra
Approximate The match is approximate rather than exact.
ICD-9-CM
756.15 Congen fusion of spine
Approximate The match is approximate rather than exact.
ICD-9-CM
756.19 Anomaly of spine NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q76.49Overview

Is Q76.49 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of spine, not associated with scoliosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q76.49 group to?

When other congenital malformations of spine, not associated with scoliosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 551, 552, with relative weights from 0.9613 to 1.6761 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q76.49 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of spine, not associated with scoliosis on inpatient claims.

What is the ICD-9 equivalent of Q76.49?

Under the General Equivalence Mappings, other congenital malformations of spine, not associated with scoliosis converts to ICD-9-CM 756.13 (cong absence of vertebra), 756.14 (hemivertebra), and 756.15 (congen fusion of spine). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.