2026 ICD-10-CM Diagnosis Code K74.3Primary biliary cirrhosis

ICD-10-CM Codes›K00–K95›K70-K77›K74

ICD-10-CM K74.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

K74.3 is a billable ICD-10-CM diagnosis code for primary biliary cirrhosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 432 through 434. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified liver disease.

Code Identity

ICD-10-CM Code
K74.3
Billable Status
Yes — Valid for Submission
Code Describes
Primary biliary cirrhosis
Short Description
Primary biliary cirrhosis
Same as the full description in the CMS dataset.
Parent Code
K74
Fibrosis and cirrhosis of liver

Code Classification

ChapterK00–K95Diseases of the digestive system
SectionK70-K77Diseases of liver
CategoryK74Fibrosis and cirrhosis of liver
This CodeK74.3Primary biliary cirrhosis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autoimmune cholangitis
  • Autoimmune hepatitis
  • Autoimmune liver disease
  • Biliary cirrhosis
  • Cholangiohepatitis
  • Cholangiolitic cirrhosis
  • Cholangiolitis
  • Fibrosis of bile duct
  • Florid cirrhosis
  • Limited systemic sclerosis
  • Primary biliary cholangitis
  • Progressive systemic sclerosis
  • Reynolds syndrome
  • Systemic sclerosis with limited cutaneous involvement

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Chronic nonsuppurative destructive cholangitis
  • Primary biliary cholangitis

Type 2 Excludes

  • primary sclerosing cholangitis K83.01

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Charcot's
      • cirrhosis
    • Cholangitis(ascending) (recurrent) (secondary) (stenosing) (suppurative)
      • chronic nonsuppurative destructive
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • biliary (cholangiolitic) (cholangitic) (hypertrophic) (obstructive) (pericholangiolitic)
        • primary
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • Charcot's
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • cholangiolitic, cholangitic, cholostatic (primary)
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • Hanot's (hypertrophic)
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • hypertrophic
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • monolobular
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • Todd's
    • Cirrhosis, cirrhotic(hepatic) (liver)
      • unilobar
    • Hanot's cirrhosis or disease
    • Todd's
      • cirrhosis

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR DIG019
Other specified and unspecified liver disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Bile Duct Diseases

Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert K74.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
571.6 Biliary cirrhosis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About K74.3Overview

Is K74.3 (Fibrosis and cirrhosis of liver) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report primary biliary cirrhosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does K74.3 group to?

When primary biliary cirrhosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 432, 433, 434, with relative weights from 0.7125 to 1.9682 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of K74.3?

Under the General Equivalence Mappings, primary biliary cirrhosis converts to ICD-9-CM 571.6 (biliary cirrhosis). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.