2026 ICD-10-CM Diagnosis Code H53.51Achromatopsia

ICD-10-CM Codes›H00–H59›H53-H54›H53

ICD-10-CM H53.51
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H53.51 is a billable ICD-10-CM diagnosis code for achromatopsia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Blindness and vision defects.

Code Identity

ICD-10-CM Code
H53.51
Billable Status
Yes — Valid for Submission
Code Describes
Achromatopsia
Short Description
Achromatopsia
Same as the full description in the CMS dataset.
Parent Code
H53.5
Color vision deficiencies

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH53-H54Visual disturbances and blindness
CategoryH53Visual disturbances
This CodeH53.51Achromatopsia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Achromatopsia
  • Blue cone monochromatism
  • Color blindness
  • Color vision deficiency
  • Complete achromatopsia
  • Cone dystrophy
  • Congenital color blindness
  • Incomplete achromatopsia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Achromat(ism), achromatopsia (acquired) (congenital)
    • Deficiency, deficient
      • color vision
        • achromatopsia
    • Monochromat(ism), monochromatopsia (acquired) (congenital)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE010
Blindness and vision defects
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cone Dystrophy

    a general term which describes a group of rare eye disorders that affect the cone cells of the retina. cone dystrophy can cause a variety of symptoms including decreased visual clarity or acuity when looking straight ahead (central vision), a reduced ability to see colors, and an increased sensitivity to light (photophobia).

  • Achromatopsia

    an autosomal recessive genetic disorder affecting the cone cells of the eye. it may be complete, in which the individual can only perceive black, white, or shades or gray, or incomplete, in which the individual has a residual amount of color vision.

  • Achromatopsia 2|ACHM2

    an autosomal recessive condition caused by mutation(s) in the cnga3 gene, encoding cyclic nucleotide-gated cation channel subunit alpha-3. it is characterized by achromatopsia.

  • Achromatopsia 5|ACHM5

    an autosomal recessive condition caused by mutation(s) in the pde6c gene, encoding cone cgmp-specific 3',5'-cyclic phosphodiesterase subunit alpha. it is characterized by low visual acuity and severe color vision defects. this condition is closely related to cone dystrophy 4, which is also caused by mutation(s) in the pde6c gene.

Patient EducationClinical

Color Blindness

Most of us see our world in color. We enjoy looking at a lush green lawn or a red rose in full bloom. If you have a color vision defect, you may see these colors differently than most people.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H53.51 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
368.54 Achromatopsia
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H53.51Overview

Is H53.51 (Color vision deficiencies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report achromatopsia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does H53.51 group to?

When achromatopsia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H53.51?

Under the General Equivalence Mappings, achromatopsia converts to ICD-9-CM 368.54 (achromatopsia). The mapping is a direct match.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.