2027 ICD-10-CM Diagnosis Code H53.51Achromatopsia

ICD-10-CM Codes›H00–H59›H53-H54›H53

ICD-10-CM H53.51
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

H53.51 is a billable ICD-10-CM diagnosis code for achromatopsia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Blindness and vision defects.

Code Identity

ICD-10-CM Code
H53.51
Billable Status
Yes — Valid for Submission
Code Describes
Achromatopsia
Short Description
Achromatopsia
Same as the full description in the CMS dataset.
Parent Code
H53.5
Color vision deficiencies

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH53-H54Visual disturbances and blindness
CategoryH53Visual disturbances
This CodeH53.51Achromatopsia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Achromatopsia
  • Blue cone monochromatism
  • Color blindness
  • Color vision deficiency
  • Complete achromatopsia
  • Cone dystrophy
  • Congenital color blindness
  • Incomplete achromatopsia

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to H53.51: its own notes plus those printed at H53.5 and Chapter 7. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From H53.5 Color vision deficiencies applies to 7 codes
From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Notes

General instructions on how these codes are used.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE010
Blindness and vision defects
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Achromatopsia

    severely deficient color perception, typically with monochromacy and reduced visual acuity. the atypical form can include normal visual acuity with pseudomonochromacy.

Patient EducationClinical

Color Blindness

Most of us see our world in color. We enjoy looking at a lush green lawn or a red rose in full bloom. If you have a color vision defect, you may see these colors differently than most people.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H53.51 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
368.54 Achromatopsia
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About H53.51Overview

What is the ICD-10 code for achromatopsia?

The ICD-10-CM code for achromatopsia is H53.51 (sometimes written as H5351). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is H53.51 (Color vision deficiencies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report achromatopsia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does H53.51 group to?

When achromatopsia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H53.51?

Under the General Equivalence Mappings, achromatopsia converts to ICD-9-CM 368.54 (achromatopsia). The mapping is a direct match.