ICD-10 Code E88.89

Other specified metabolic disorders

Version 2019 Billable Code

Valid for Submission

E88.89 is a billable code used to specify a medical diagnosis of other specified metabolic disorders. The code is valid for the year 2020 for the submission of HIPAA-covered transactions.

ICD-10: E88.89
Short Description:Other specified metabolic disorders
Long Description:Other specified metabolic disorders

Code Classification

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Metabolic disorders (E70-E88)
      • Other and unspecified metabolic disorders (E88)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (first year ICD-10-CM implemented into the HIPAA mandated code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Medical Professionals

Convert E88.89 to ICD-9

The following crosswalk between ICD-10 to ICD-9 is based based on the General Equivalence Mappings (GEMS) information:

  • 272.8 - Lipoid metabol dis NEC (Approximate Flag)
  • 277.89 - Metabolism disorder NEC (Approximate Flag)

Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adenosine deaminase overproduction
  • Angioedema due to disorder of kinin metabolism
  • Aromatase excess syndrome
  • Arylsulfatase deficiency without MLD
  • Autosomal recessive ataxia due to ubiquinone deficiency
  • Brunner syndrome
  • Cerebral folate transport deficiency
  • Chronic diarrhea due to glucoamylase deficiency
  • Chronic diarrhea of infants AND/OR young children
  • Circulating enzyme deficiency
  • Clinical manifestation of enzyme deficiency
  • Coenzyme Q10 deficiency
  • Complete deficiency of methylmalonyl-CoA mutase
  • Congenital defect of folate absorption
  • Corticosteroid 11-reductase deficiency
  • CYP2B6 poor metabolizer
  • CYP2B6 rapid metabolizer
  • CYP2B6 ultra-rapid metabolizer
  • CYP2C19 poor metabolizer
  • CYP2C19 ultra-rapid metabolizer
  • CYP2C9 poor metabolizer
  • CYP2D6 poor metabolizer
  • CYP2D6 ultra-rapid metabolizer
  • CYP3A5 poor metabolizer
  • Cytochrome p450 CYP1A2 enzyme deficiency
  • Cytochrome p450 CYP2E1 enzyme deficiency
  • Cytochrome p450 CYP3A enzyme deficiency
  • Cytochrome p450 enzyme deficiency
  • Cytosolic acetoacetyl-CoA thiolase deficiency
  • Decreased metabolic requirement
  • Decreased nutritional requirement
  • Decreased oxygen affinity
  • Deficiency of 1,3-beta-glucan synthase
  • Deficiency of 1,4-alpha-glucan 6alpha-glucosyltransferase
  • Deficiency of 1,4-alpha-glucan branching enzyme
  • Deficiency of 2,5-diaminovalerate aminotransferase
  • Deficiency of -20-hydroxysteroid dehydrogenase
  • Deficiency of -2-hydroxy-acid oxidase
  • Deficiency of 3alpha-hydroxycholanate dehydrogenase
  • Deficiency of 3-mercaptopyruvate sulfurtransferase
  • Deficiency of 3-oxoacid CoA-transferase
  • Deficiency of 3-oxoadipate CoA-transferase
  • Deficiency of acetate kinase
  • Deficiency of acetylcholinesterase
  • Deficiency of acetyl-CoA acetyltransferase
  • Deficiency of acetyl-CoA acetyltransferase
  • Deficiency of acetylesterase
  • Deficiency of acid-ammonia ligase
  • Deficiency of aconitate hydratase
  • Deficiency of adenosine kinase
  • Deficiency of adenosinetriphosphatase
  • Deficiency of adenylate kinase
  • Deficiency of adenylylsulfate kinase
  • Deficiency of ADP deaminase
  • Deficiency of alcohol sulfotransferase
  • Deficiency of aldehyde dehydrogenase
  • Deficiency of aldehyde oxidase
  • Deficiency of aldehyde-lyase
  • Deficiency of alkaline phosphatase
  • Deficiency of alkaline phosphomonoesterase
  • Deficiency of alkylhalidase
  • Deficiency of alpha- and beta-trypsin
  • Deficiency of alpha-1,4-glucan-protein synthase
  • Deficiency of alpha-aminoacylpeptide hydrolase
  • Deficiency of alpha-ketoglutarate dehydrogenase
  • Deficiency of amidase
  • Deficiency of amidinotransferase
  • Deficiency of amidophosphoribosyltransferase
  • Deficiency of amine oxidase
  • Deficiency of amine oxidase
  • Deficiency of aryl sulfotransferase
  • Deficiency of arylamine acetyltransferase
  • Deficiency of arylesterase
  • Deficiency of aspartic proteinase
  • Deficiency of ATP pyrophosphatase
  • Deficiency of azobenzene reductase
  • Deficiency of benzoylcholinesterase
  • Deficiency of butyrate-acetoacetate CoA-transferase
  • Deficiency of carbamate kinase
  • Deficiency of carbon-carbon lyase
  • Deficiency of carbon-halide lyase
  • Deficiency of carbon-nitrogen lyase
  • Deficiency of carbon-oxygen lyase
  • Deficiency of carbon-sulfur lyase
  • Deficiency of carboxylesterase
  • Deficiency of carboxylic ester hydrolase
  • Deficiency of catechol oxidase
  • Deficiency of cathepsin C
  • Deficiency of cathepsin D
  • Deficiency of cellulase
  • Deficiency of chlorophyllase
  • Deficiency of choline acetyltransferase
  • Deficiency of choline kinase
  • Deficiency of choline-phosphate cytidylyltransferase
  • Deficiency of cholinephosphotransferase
  • Deficiency of cholinesterase
  • Deficiency of chymosin
  • Deficiency of chymotrypsin
  • Deficiency of chymotrypsin A and B
  • Deficiency of citrate-synthase
  • Deficiency of creatine kinase
  • Deficiency of D-2-hydroxy-acid dehydrogenase
  • Deficiency of dehydrogenase
  • Deficiency of dehydrogluconate dehydrogenase
  • Deficiency of dehydrogluconokinase
  • Deficiency of deoxyribonuclease I
  • Deficiency of deoxyribonuclease II
  • Deficiency of dephospho-CoA kinase
  • Deficiency of dextranase
  • Deficiency of dihydroorotase
  • Deficiency of diisopropyl-fluorophosphatase
  • Deficiency of dimethylallyltranstransferase
  • Deficiency of dioxygenase
  • Deficiency of dipeptidase
  • Deficiency of dipeptide hydrolase
  • Deficiency of dipeptidyl peptidase I
  • Deficiency of dipeptidyl-amino-peptidase I
  • Deficiency of dipeptidylpeptide hydrolase
  • Deficiency of diphosphomevalonate decarboxylase
  • Deficiency of diphosphoric monoester hydrolase
  • Deficiency of DNA nucleotidylexotransferase
  • Deficiency of DNA-directed DNA polymerase
  • Deficiency of DNA-directed RNA polymerase
  • Deficiency of endopeptidase
  • Deficiency of endoribonuclease
  • Deficiency of enolase
  • Deficiency of enteropeptidase
  • Deficiency of epimerase
  • Deficiency of erythritol kinase
  • Deficiency of estradiol 6beta-monooxygenase
  • Deficiency of ethanolamine-phosphate cytidylyltransferase
  • Deficiency of ethanolaminephosphotransferase
  • Deficiency of ether hydrolase
  • Deficiency of exoribonuclease
  • Deficiency of FMN adenylyltransferase
  • Deficiency of formaldehyde dehydrogenase
  • Deficiency of formamidase
  • Deficiency of formate dehydrogenase
  • Deficiency of formate-tetrahydrofolate ligase
  • Deficiency of formiminotetrahydrofolate cyclodeaminase
  • Deficiency of formyltetrahydrofolate deformylase
  • Deficiency of fumarate hydratase
  • Deficiency of fumarylacetoacetase
  • Deficiency of galactonolactone dehydrogenase
  • Deficiency of glucosamine acetyltransferase
  • Deficiency of glucosamine kinase
  • Deficiency of glucosamine-phosphate acetyltransferase
  • Deficiency of glutathione reductase
  • Deficiency of glycerate kinase
  • Deficiency of glycerol-3-phosphate acyltransferase
  • Deficiency of glycerophosphatase
  • Deficiency of glycogen synthase a kinase
  • Deficiency of guanine deaminase
  • Deficiency of guanylate cyclase 2C
  • Deficiency of halogenase
  • Deficiency of heparin lyase
  • Deficiency of hexose oxidase
  • Deficiency of hexosyltransferase
  • Deficiency of histidinol dehydrogenase
  • Deficiency of hyaluronate lyase
  • Deficiency of hyaluronoglucosaminidase
  • Deficiency of hydrogen-sulfide acetyltransferase
  • Deficiency of hydrolase
  • Deficiency of hydrolyase
  • Deficiency of hydroxyacylglutathione hydrolase
  • Deficiency of hydroxyalkyl-protein kinase
  • Deficiency of hydroxymethylglutaryl-CoA hydrolase
  • Deficiency of hydroxymethylglutaryl-CoA reductase
  • Deficiency of hydroxymethylglutaryl-CoA synthase
  • Deficiency of imidodipeptidase
  • Deficiency of iminodipeptidase
  • Deficiency of IMP cyclohydrolase
  • Deficiency of IMP dehydrogenase
  • Deficiency of inorganic pyrophosphatase
  • Deficiency of inosinase
  • Deficiency of isobutyryl-CoA dehydrogenase
  • Deficiency of isocitrate lyase
  • Deficiency of isomerase
  • Deficiency of isopentenyl-diphosphate delta-isomerase
  • Deficiency of ketotetrose-phosphate aldolase
  • Deficiency of lactonase
  • Deficiency of lactoylglutathione lyase
  • Deficiency of L-arabinose dehydrogenase
  • Deficiency of lecithinase D
  • Deficiency of leucine aminopeptidase
  • Deficiency of leukotriene C4 synthase
  • Deficiency of L-gulonate dehydrogenase
  • Deficiency of lichenase
  • Deficiency of ligase
  • Deficiency of limit dextrinase
  • Deficiency of lipophosphodiesterase II
  • Deficiency of L-prolylglycine dipeptidase
  • Deficiency of lyase
  • Deficiency of lysine-tRNA ligase
  • Deficiency of lysolecithin acylmutase
  • Deficiency of lysophospholipase
  • Deficiency of lysozyme
  • Deficiency of malate dehydrogenase
  • Deficiency of malate dehydrogenase
  • Deficiency of malate dehydrogenase
  • Deficiency of malate oxidase
  • Deficiency of mannitol dehydrogenase
  • Deficiency of mannose-6-phosphate isomerase
  • Deficiency of metallocarboxypeptidase
  • Deficiency of metalloproteinase
  • Deficiency of methenyltetrahydrofolate cyclohydrolase
  • Deficiency of methylaspartate mutase
  • Deficiency of methylenetetrahydrofolate dehydrogenase
  • Deficiency of methylglutaconyl-CoA hydratase
  • Deficiency of methylmalonyl-CoA mutase
  • Deficiency of methyltransferase
  • Deficiency of mevaldate reductase
  • Deficiency of mevalonate kinase
  • Deficiency of monodehydroascorbate reductase
  • Deficiency of monooxygenase
  • Deficiency of mutase
  • Deficiency of myo-inositol oxygenase
  • Deficiency of N-acetyl-beta-glucosaminidase
  • Deficiency of N-acetylneuraminate lyase
  • Deficiency of NAD
  • Deficiency of NAD^+^ kinase
  • Deficiency of NAD^+^ nucleosidase
  • Deficiency of NAD^+^ nucleosidase
  • Deficiency of NAD^+^ synthase
  • Deficiency of NAD^+^ transhydrogenase
  • Deficiency of NADase
  • Deficiency of NADH dehydrogenase
  • Deficiency of nicotinamide methyltransferase
  • Deficiency of nicotinamide phosphoribosyltransferase
  • Deficiency of nicotinamide-nucleotide adenylyltransferase
  • Deficiency of nicotinate dehydrogenase
  • Deficiency of nicotinate phosphoribosyltransferase
  • Deficiency of nitrate reductase
  • Deficiency of non-specific cholinesterase
  • Deficiency of nucleosidase
  • Deficiency of nucleoside-diphosphatase
  • Deficiency of nucleoside-diphosphate kinase
  • Deficiency of nucleoside-phosphate kinase
  • Deficiency of nucleotidase
  • Deficiency of nucleotide pyrophosphatase
  • Deficiency of nucleotidyltransferase
  • Deficiency of omega peptidase
  • Deficiency of orotate phosphoribosyltransferase
  • Deficiency of oxalate CoA-transferase
  • Deficiency of oxidase
  • Deficiency of oximinotransferase
  • Deficiency of oxo-acid-lyase
  • Deficiency of oxoglutarate dehydrogenase
  • Deficiency of oxygenase
  • Deficiency of pancreatic elastase
  • Deficiency of pantetheine kinase
  • Deficiency of pantetheine-phosphate adenylyltransferase
  • Deficiency of pantothenoylcysteine decarboxylase
  • Deficiency of pectin methoxylase
  • Deficiency of pectin methylesterase
  • Deficiency of pectinesterase
  • Deficiency of pentosyltransferase
  • Deficiency of pepsin A
  • Deficiency of pepsin B
  • Deficiency of peptidase a
  • Deficiency of peptide hydrolase
  • Deficiency of peptidoglycan endopeptidase
  • Deficiency of peroxidase
  • Deficiency of phenylalanine 4-monooxygenase
  • Deficiency of phenylpyruvate tautomerase
  • Deficiency of phosphatase
  • Deficiency of phosphatidate phosphatase
  • Deficiency of phosphoacetylglucosamine mutase
  • Deficiency of phosphoadenylate 3'-nucleotidase
  • Deficiency of phosphoamidase
  • Deficiency of phosphoglucomutase
  • Deficiency of phosphogluconate dehydrogenase
  • Deficiency of phosphogluconate dehydrogenase
  • Deficiency of phosphoglycerate mutase
  • Deficiency of phosphoketolase
  • Deficiency of phospholipase A>2<
  • Deficiency of phospholipase C
  • Deficiency of phospholipase D
  • Deficiency of phosphomevalonate kinase
  • Deficiency of phosphomonoesterase
  • Deficiency of phosphopantothenate-cysteine ligase
  • Deficiency of phosphoprotein phosphatase
  • Deficiency of phosphoribokinase
  • Deficiency of phosphoribosylamine-glycine ligase
  • Deficiency of phosphoribosylglycinamide formyltransferase
  • Deficiency of phosphoric diester hydrolase
  • Deficiency of phosphoric monoester hydrolase
  • Deficiency of phosphorus-oxygen lyase
  • Deficiency of phosphorylase kinase
  • Deficiency of phosphorylase phosphatase
  • Deficiency of phosphotransferase
  • Deficiency of plasmin
  • Deficiency of polygalacturonase
  • Deficiency of polyribonucleotide nucleotidyltransferase
  • Deficiency of progesterone 11alpha-monooxygenase
  • Deficiency of prolidase
  • Deficiency of prolinase
  • Deficiency of prolyl dipeptidase
  • Deficiency of protease
  • Deficiency of protein kinase
  • Deficiency of protocatechuate 3,4-dioxygenase
  • Deficiency of pyridoxal kinase
  • Deficiency of pyridoxamine-phosphate oxidase
  • Deficiency of pyrophosphotransferase
  • Deficiency of pyrroline-2-carboxylate reductase
  • Deficiency of pyruvate kinase
  • Deficiency of racemase
  • Deficiency of reductase
  • Deficiency of renin
  • Deficiency of retinal isomerase
  • Deficiency of retinyl-palmitate esterase
  • Deficiency of riboflavin kinase
  • Deficiency of ribokinase
  • Deficiency of ribonuclease
  • Deficiency of ribose-5-phosphate isomerase
  • Deficiency of ribose-phosphate pyrophosphokinase
  • Deficiency of ribosomal cathepsin
  • Deficiency of ribosomal neutral proteinase
  • Deficiency of ribosylnicotinamide kinase
  • Deficiency of ribulokinase
  • Deficiency of ribulose-phosphate 3-epimerase
  • Deficiency of sarcoplasmic reticulum calcium-ATPase 1
  • Deficiency of sedoheptulokinase
  • Deficiency of serine proteinase
  • Deficiency of shikimate dehydrogenase
  • Deficiency of sialidase
  • Deficiency of squalene monooxygenase
  • Deficiency of steroid 17-alpha-monooxygenase
  • Deficiency of steroid delta-isomerase
  • Deficiency of succinate dehydrogenase
  • Deficiency of succinate-CoA ligase
  • Deficiency of succinate-CoA ligase
  • Deficiency of succinate-CoA ligase
  • Deficiency of succinyl-CoA hydrolase
  • Deficiency of sulfate adenylyltransferase
  • Deficiency of sulfinoalanine decarboxylase
  • Deficiency of sulfite reductase
  • Deficiency of sulfotransferase
  • Deficiency of sulfuric ester hydrolase
  • Deficiency of sulfurtransferase
  • Deficiency of tannase
  • Deficiency of thiamine pyridinylase
  • Deficiency of thiamine pyrophosphokinase
  • Deficiency of thioethanolamine acetyltransferase
  • Deficiency of thioether hydrolase
  • Deficiency of thiolester hydrolase
  • Deficiency of thiosulfate sulfurtransferase
  • Deficiency of thrombin
  • Deficiency of transacylase
  • Deficiency of transaldolase
  • Deficiency of transcarbamoylase
  • Deficiency of transcarboxylase
  • Deficiency of transferase
  • Deficiency of transformiminase
  • Deficiency of transformylase
  • Deficiency of transhydroxymethylase
  • Deficiency of transketolase
  • Deficiency of triacylglycerol lipase
  • Deficiency of tripeptide aminopeptidase
  • Deficiency of triphosphoric monoester hydrolase
  • Deficiency of tropinesterase
  • Deficiency of true cholinesterase
  • Deficiency of trypsin
  • Deficiency of tyraminase
  • Deficiency of tyrosine aminotransferase
  • Deficiency of UDPglucose dehydrogenase
  • Deficiency of unspecific monooxygenase
  • Deficiency of uracil dehydrogenase
  • Deficiency of uracil phosphoribosyltransferase
  • Deficiency of urate oxidase
  • Deficiency of uronolactonase
  • Deficiency of UTP-glucose-1-phosphate uridylyltransferase
  • Deficiency of UTP-hexose-1-phosphate uridylyltransferase
  • Deficiency of w-amidase
  • Deficiency of xylan endo-1,3-beta-xylosidase
  • Deficiency of Zeta-chain associated protein kinase 70
  • Diffuse organ or tissue uptake
  • Dilated cardiomyopathy secondary to deficiency
  • Dilated cardiomyopathy secondary to electrolyte deficiency
  • Dilated cardiomyopathy secondary to familial storage disease
  • Disorder due to N-acetyltransferase enzyme variant
  • Disorder of blood gas
  • Disorder of cortisol-cortisone shuttle
  • Disorder of iodine metabolism
  • Disorder of lysosomal enzyme
  • Disorder of organic acid metabolism
  • Disorder of oxygen transport
  • Disorder of propionate AND/OR methylmalonate metabolism
  • Disorder of protein metabolism
  • Disorder of sialic acid metabolism
  • Disorder of sialic acid metabolism
  • Disorder of steroid metabolism
  • DPYD poor metabolizer
  • Enterokinase deficiency
  • Erythrocyte enzyme deficiency
  • Ethanolaminosis
  • Etiocholanolone fever
  • Familial cardiomyopathy
  • Fast acetylator due to N-acetyltransferase enzyme variant
  • Folic acid deficiency
  • Folic acid deficiency
  • Folinic acid responsive seizure syndrome
  • Fumarase deficiency
  • Fumarylacetoacetase deficiency, acute type
  • Glucose phosphate isomerase deficiency
  • Glutathione S-transferase deficiency
  • Gronblad-Strandberg syndrome
  • Hyperimidodipeptiduria
  • Hypermetabolism
  • Hypermethioninemia
  • Hyperthermia-hyperphagia-hypothyroidism syndrome
  • Impaired oxygen delivery
  • Impaired oxygen extraction
  • Increased auto-oxidation
  • Increased metabolic requirement
  • Increased nutritional requirement
  • Increased oxygen affinity
  • Increased oxygen demand
  • Inherited disorder of folate metabolism
  • Intestinal enteropeptidase deficiency
  • Intestinal obstruction in newborn due to guanylate cyclase 2C deficiency
  • Ketonemia
  • Ketosis
  • Ketotic hypoglycemia
  • Liposynovitis prepatellaris
  • Meconium ileus
  • Metabolic disorder of transport
  • Metabolic myopathy due to lactate transporter defect
  • Methylcrotonic aciduria
  • Mevalonic aciduria
  • Mitochondrial 2-methylacetoacetyl-CoA thiolase deficiency - non-potassium stimulated
  • Mucolipidosis
  • Muscle D-lactate dehydrogenase deficiency
  • Non-amino organic acidemia AND/OR aciduria
  • NUDT15 intermediate metabolizer
  • NUDT15 poor metabolizer
  • NUDT15 possible intermediate metabolizer
  • Pancreatic colipase deficiency
  • Pancreatic malabsorption
  • Partial deficiency of methylmalonyl-CoA mutase
  • Patchy organ or tissue uptake
  • Perinatal intestinal obstruction
  • Phosphoglycerokinase deficiency
  • Prepatellar bursitis
  • Progressive polyneuropathy with bilateral striatal necrosis
  • Progressive retinal dystrophy due to retinol transport defect
  • Proteinosis
  • Pseudohypoaldosteronism
  • Pseudohypoaldosteronism type 2A
  • Pseudohypoaldosteronism, type 1
  • Pseudohypoaldosteronism, type 1, dominant form
  • Pseudohypoaldosteronism, type 1, recessive form
  • Pseudohypoaldosteronism, type 2
  • Psychomotor retardation due to S-adenosylhomocysteine hydrolase deficiency
  • Rowley-Rosenberg syndrome
  • S-adenosylhomocysteine hydrolase deficiency
  • Sialic acid storage disease, severe infantile type
  • Sialic storage disease
  • Sialuria
  • SLCO1B1 decreased function
  • SLCO1B1 poor function
  • Slow acetylator due to N-acetyltransferase enzyme variant
  • Specific enzyme deficiency
  • Steroid dehydrogenase deficiency and dental anomaly syndrome
  • Testosterone 17-beta-dehydrogenase deficiency
  • TPMT poor metabolizer
  • Transient pseudohypoaldosteronism
  • Trypsinogen deficiency
  • UGT1A1 poor metabolizer

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code E88.89 are found in the index:


Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references for the code E88.89 are found in the tabular index:

  • Inclusion Terms:
    • Launois-Bensaude adenolipomatosis
  • Type 1 Excludes Notes:
    • adult pulmonary Langerhans cell histiocytosis (J84.82)

Information for Patients


Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.

A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.

You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.


[Learn More]

ICD-10 Footnotes

General Equivalence Map Definitions
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

  • And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
  • Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
  • Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
  • Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
  • Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
  • NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
  • See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
  • See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
  • 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
  • With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.