ICD-9 Code 277.89

Other specified disorders of metabolism

Not Valid for Submission

277.89 is a legacy non-billable code used to specify a medical diagnosis of other specified disorders of metabolism. This code was replaced on September 30, 2015 by its ICD-10 equivalent.

ICD-9: 277.89
Short Description:Metabolism disorder NEC
Long Description:Other specified disorders of metabolism

Convert 277.89 to ICD-10

The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:

  • C96.5 - Multifocal and unisystemic Langerhans-cell histiocytosis
  • C96.6 - Unifocal Langerhans-cell histiocytosis
  • E71.39 - Other disorders of fatty-acid metabolism
  • E80.3 - Defects of catalase and peroxidase
  • E88.89 - Other specified metabolic disorders
  • E88.9 - Metabolic disorder, unspecified

Code Classification

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism

Information for Medical Professionals

Synonyms

  • Acatalasemia
  • Acatalasia
  • Adenosine deaminase overproduction
  • Alpha-N-acetylgalactosaminidase deficiency
  • Anemia due to disorders of nucleotide metabolism
  • Angioedema due to disorder of kinin metabolism
  • Autosomal variant form of transthyretin
  • Combined complex deficiencies
  • Combined deficiency of long chain 3-hydroxyacyl-coenzyme A dehydrogenase and enoyl-coenzyme A hydratase
  • Defect in post-translational modification of lysosomal enzymes
  • Defective biosynthesis
  • Defective osmoregulation
  • Deficiency in enzyme complexes of mitochondrial respiratory chain
  • Deficiency of amylopectin 6-glucanohydrolase
  • Deficiency of glycosidase
  • Deficiency of halogenase
  • Deficiency of isobutyryl-coenzyme A dehydrogenase
  • Deficiency of limit dextrinase
  • Deficiency of protease
  • Deletion and duplication of mitochondrial deoxyribonucleic acid
  • Depletion of mitochondrial deoxyribonucleic acid
  • Disorder of beta alanine, carnosine AND/OR homocarnosine metabolism
  • Disorder of chromium metabolism
  • Disorder of glucose regulation
  • Disorder of glycoprotein metabolism
  • Disorder of glycosaminoglycan metabolism
  • Disorder of iodine metabolism
  • Disorder of mitochondrial respiratory chain complexes
  • Disorder of organic acid metabolism
  • Disorder of osmoregulation
  • Disorder of oxygen transport
  • Disorder of peroxisomal function
  • Disorder of protein metabolism
  • Disorder of pyruvate metabolism and mitochondrial respiratory chain
  • Disorder of sialic acid metabolism
  • Disorder of steroid metabolism
  • Disorder of strontium metabolism
  • Disorder with defective osteoid mineralization
  • Disorders of pyruvate metabolism and gluconeogenesis
  • Drug resistance to insulin
  • Enterokinase deficiency
  • Eosinophilic granuloma of bone
  • Extensive metabolizer due to cytochrome p450 CYP2D6 variant
  • Familial sea-blue histiocytosis
  • Fast acetylator due to N-acetyltransferase enzyme variant
  • Fat overload syndrome
  • Glutaric aciduria, type 1
  • Glutathione S-transferase deficiency
  • Hand-Schüller-Christian disease
  • Histiocytosis X syndrome
  • Homocarnosinase deficiency
  • Hyper-beta-carnosinemia
  • Hyperimidodipeptiduria due to proline dipeptidase deficiency
  • Hypermanganesemia with dystonia, polycythemia, and cirrhosis
  • Impaired oxygen extraction
  • Inborn error of pyruvate metabolism
  • Increased auto-oxidation
  • Increased fluid pressure
  • Increased oxygen demand
  • Inherited metabolic disorder of nervous system
  • Intermediate metabolizer due to cytochrome p450 CYP2D6 variant
  • Langerhans cell histiocytosis
  • Langerhans cell histiocytosis - Hashimoto-Pritzker type
  • Langerhans cell histiocytosis of lung
  • Langerhans cell histiocytosis, unifocal
  • Macroamylasemia
  • Methylene tetrahydrofolate methyltransferase reductase deficiency AND homocystinuria
  • Mucinous histiocytosis of the colon
  • Pancreatic colipase deficiency
  • Pancreatic triacylglycerol lipase deficiency
  • Phosphoenolpyruvate carboxykinase deficiency
  • Polyostotic sclerosing histiocytosis
  • Poor metabolizer due to cytochrome p450 CYP2C19 variant
  • Poor metabolizer due to cytochrome p450 CYP2C9 variant
  • Poor metabolizer due to cytochrome p450 CYP2D6 variant
  • Pseudoinfantile Refsum's disease
  • Pyruvate carboxylase deficiency
  • Pyruvate dehydrogenase complex deficiency
  • Refeeding syndrome
  • Sepiapterin reductase deficiency
  • Sinus histiocytosis with massive lymphadenopathy
  • Slow acetylator due to N-acetyltransferase enzyme variant
  • Solitary reticulohistiocytoma
  • Tetrahydrobiopterin synthesis defect
  • Trypsinogen deficiency
  • Tumor lysis syndrome
  • UGT1A1*28 polymorphism
  • Ultrarapid metabolizer due to cytochrome p450 CYP2D6 variant
  • Undetermined cell histiocytosis

Index to Diseases and Injuries

References found for the code 277.89 in the Index of Diseases and Injuries:


Information for Patients


Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.

A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.

You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.


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ICD-9 Footnotes

General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

  • And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
  • Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
  • Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
  • Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
  • Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
  • NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
  • See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
  • See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
  • 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
  • With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.