2027 ICD-10-CM Diagnosis Code D18.1Lymphangioma, any site
ICD-10-CM Codes›C00–D49›D10-D36›D18
- Billable — Valid for Submission
- Not Chronic
D18.1 is a billable ICD-10-CM diagnosis code for lymphangioma, any site. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 814 through 816. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acquired lymphangioma
- Acquired progressive lymphangioma
- Benign extra-axial hygroma
- Cavernous lymphangioma
- Cavernous lymphangioma of skin
- Chronic disease of lymphatic vessels
- Congenital anomaly of lymphatic structure of trunk
- Congenital lymphangioma
- Cystic hygroma
- Diffuse lymphangioma
- Diffuse pulmonary lymphangiomatosis
- Hemolymphangioma of conjunctiva
- Kaposiform lymphangiomatosis
- Lymphangioma
- Lymphangioma circumscriptum
- Lymphangioma of appendix
- Lymphangioma of conjunctiva
- Lymphangioma of large intestine
- Lymphangioma of larynx
- Lymphangioma of liver
- Lymphangioma of orbit
- Lymphangioma of skin
- Lymphangioma of small intestine
- Lymphangiomatosis
- Multiple lymphangiomas of skin
- Oral lymphangioma
- Primary laryngeal lymphangioma
- Segmental lymphangiomatosis
- Simple lymphangioma
- Subdural hygroma
- Systemic lymphangiomatosis
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to D18.1: its own notes plus those printed at D18 and Chapter 2. A note printed at a category, block or chapter applies to every code under it.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Functional activity
- All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
- Morphology [Histology]
- Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
- Primary malignant neoplasms overlapping site boundaries
- A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
- Malignant neoplasm of ectopic tissue
- Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name D18.1, its category, or a range that includes it.
Excludes1 3
These codes carry an Excludes1 note naming D18.1: they are not reported together with it, unless the two conditions are unrelated.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Hemolymphangioma D18.1
Lymphangioendothelioma D18.1
Lymphangioma D18.1
Lymphangiomyoma D18.1
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Lymphangioma
a benign tumor resulting from a congenital malformation of the lymphatic system. lymphangioendothelioma is a type of lymphangioma in which endothelial cells are the dominant component.
Patient EducationClinical
Benign Tumors
Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert D18.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About D18.1Overview
What is the ICD-10 code for lymphangioma, any site?
The ICD-10-CM code for lymphangioma, any site is D18.1 (sometimes written as D181). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is D18.1 (Hemangioma and lymphangioma, any site) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report lymphangioma, any site on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does D18.1 group to?
When lymphangioma, any site is the principal diagnosis on an inpatient stay, it groups to MS-DRG 816, 814, 815, with relative weights from 0.7378 to 2.0727 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of D18.1?
Under the General Equivalence Mappings, lymphangioma, any site converts to ICD-9-CM 228.1 (lymphangioma, any site). The mapping is a direct match.
