2026 ICD-10-CM Diagnosis Code D18.1Lymphangioma, any site

ICD-10-CM Codes›C00–D49›D10-D36›D18

ICD-10-CM D18.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D18.1 is a billable ICD-10-CM diagnosis code for lymphangioma, any site. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 814 through 816. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.

Code Identity

ICD-10-CM Code
D18.1
Billable Status
Yes — Valid for Submission
Code Describes
Lymphangioma, any site
Short Description
Lymphangioma, any site
Same as the full description in the CMS dataset.
Parent Code
D18
Hemangioma and lymphangioma, any site

Code Classification

ChapterC00–D49Neoplasms
SectionD10-D36Benign neoplasms, except benign neuroendocrine tumors
CategoryD18Hemangioma and lymphangioma, any site
This CodeD18.1Lymphangioma, any site

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired lymphangioma
  • Acquired progressive lymphangioma
  • Benign extra-axial hygroma
  • Cavernous lymphangioma
  • Cavernous lymphangioma of skin
  • Chronic disease of lymphatic vessels
  • Congenital anomaly of lymphatic structure of trunk
  • Congenital lymphangioma
  • Cystic hygroma
  • Diffuse lymphangioma
  • Diffuse pulmonary lymphangiomatosis
  • Hemolymphangioma of conjunctiva
  • Kaposiform lymphangiomatosis
  • Lymphangioma
  • Lymphangioma circumscriptum
  • Lymphangioma of appendix
  • Lymphangioma of conjunctiva
  • Lymphangioma of large intestine
  • Lymphangioma of larynx
  • Lymphangioma of liver
  • Lymphangioma of orbit
  • Lymphangioma of skin
  • Lymphangioma of small intestine
  • Lymphangiomatosis
  • Multiple lymphangiomas of skin
  • Oral lymphangioma
  • Primary laryngeal lymphangioma
  • Segmental lymphangiomatosis
  • Simple lymphangioma
  • Subdural hygroma
  • Systemic lymphangiomatosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cyst(colloid) (mucous) (simple) (retention)
      • lymphangiomatous
    • Hemolymphangioma
    • Hygroma(congenital) (cystic)
    • Lymphangioendothelioma
    • Lymphangioma
    • Lymphangioma
      • capillary
    • Lymphangioma
      • cavernous
    • Lymphangioma
      • cystic
    • Lymphangiomyoma
    • Nevus
      • lymphatic

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO073
Benign neoplasms
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Lymphangioma

    a benign tumor resulting from a congenital malformation of the lymphatic system. lymphangioendothelioma is a type of lymphangioma in which endothelial cells are the dominant component.

  • Lymphangioma, Cystic

    a cystic growth originating from lymphatic tissue. it is usually found in the neck, axilla, or groin.

  • Diffuse Pulmonary Lymphangiomatosis

    lymphangiomatosis diffusely involving the lung parenchyma.

  • Lymphangioma Circumscriptum

    a localized lymphangioma characterized by microcystic changes.

  • Liver Lymphangiomatosis

    multiple lymphangiomas that affect the liver and other anatomic sites. although histologically benign, diffuse lymphangiomatosis that affects the liver and multiple organs has a poor prognosis.

  • Lymphangiomatosis

    a lymphangioma affecting several anatomic sites.

Patient EducationClinical

Benign Tumors

Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D18.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
228.1 Lymphangioma, any site
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D18.1Overview

Is D18.1 (Hemangioma and lymphangioma, any site) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lymphangioma, any site on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does D18.1 group to?

When lymphangioma, any site is the principal diagnosis on an inpatient stay, it groups to MS-DRG 814, 815, 816, with relative weights from 0.6320 to 2.1267 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of D18.1?

Under the General Equivalence Mappings, lymphangioma, any site converts to ICD-9-CM 228.1 (lymphangioma, any site). The mapping is a direct match.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.