2026 ICD-10-CM Diagnosis Code C83.89Other non-follicular lymphoma, extranodal and solid organ sites

ICD-10-CM Codes›C00–D49›C81-C96›C83

ICD-10-CM C83.89
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

C83.89 is a billable ICD-10-CM diagnosis code for other non-follicular lymphoma, extranodal and solid organ sites. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 820 through 825, 840 through 842, 974 through 976. Coders also document this condition as lymphomatoid granulomatosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Non-Hodgkin lymphoma.

Code Identity

ICD-10-CM Code
C83.89
Billable Status
Yes — Valid for Submission
Code Describes
Other non-follicular lymphoma, extranodal and solid organ sites
Short Description
Oth non-follic lymphoma, extranodal and solid organ sites
Parent Code
C83.8
Other non-follicular lymphoma

Code Classification

ChapterC00–D49Neoplasms
SectionC81-C96Malignant neoplasms of lymphoid, hematopoietic and related tissue
CategoryC83Non-follicular lymphoma
This CodeC83.89Other non-follicular lymphoma, extranodal and solid organ sites

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Lymphomatoid granulomatosis
  • Lymphomatoid granulomatosis of lung
  • Malignant lymphomatoid granulomatosis
  • Malignant lymphomatoid granulomatosis grade 3
  • Malignant lymphomatoid granulomatosis grade 3 of lung
  • Malignant lymphomatoid granulomatosis of lung

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO058
Non-Hodgkin lymphoma
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Lymphomatoid Granulomatosis

    an angiocentric and angiodestructive lymphoproliferative disorder primarily involving the lungs. it is caused by an epstein-barr virus-induced transformation of the b-cells, in a t-cell rich environment. clinically and pathologically it resembles extranodal nk-t-cell lymphoma.

  • Lymphoma, Extranodal NK-T-Cell

    an extranodal neoplasm, usually possessing an nk-cell phenotype and associated with epstein-barr virus. these lymphomas exhibit a broad morphologic spectrum, frequent necrosis, angioinvasion, and most commonly present in the midfacial region, but also in other extranodal sites.

Patient EducationClinical

Lymphoma

Lymphoma is a cancer of a part of the immune system called the lymph system. There are many types of lymphoma. One type is Hodgkin disease. The rest are called non-Hodgkin lymphomas.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert C83.89 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
200.30 Margnl zone lym xtrndl
Approximate The match is approximate rather than exact.
ICD-9-CM
200.50 Primary CNS lymph xtrndl
Approximate The match is approximate rather than exact.
ICD-9-CM
200.80 Oth varn unsp xtrndl org
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About C83.89Overview

Is C83.89 (Other non-follicular lymphoma) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other non-follicular lymphoma, extranodal and solid organ sites on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does C83.89 group to?

When other non-follicular lymphoma, extranodal and solid organ sites is the principal diagnosis on an inpatient stay, it groups to MS-DRG 820, 821, 822, 823, 824, 825, 840, 841, 842, 974, 975, 976, with relative weights from 0.8945 to 5.8648 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of C83.89?

Under the General Equivalence Mappings, other non-follicular lymphoma, extranodal and solid organ sites converts to ICD-9-CM 200.30 (margnl zone lym xtrndl), 200.50 (primary CNS lymph xtrndl), and 200.80 (oth varn unsp xtrndl org). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.