2027 ICD-10-CM Diagnosis Code QA1.71Lynch syndrome

ICD-10-CM Codes›Q00-Q99›QA0-QA1›QA1

ICD-10-CM QA1.71
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

QA1.71 is a billable ICD-10-CM diagnosis code for lynch syndrome. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 951. The code is exempt from POA reporting.

Code Identity

ICD-10-CM Code
QA1.71
Billable Status
Yes — Valid for Submission
Code Describes
Lynch syndrome
Short Description
Lynch syndrome
Same as the full description in the CMS dataset.
Parent Code
QA1.7
Inherited neoplasm predisposition syndromes involving multiple systems, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQA0-QA1Genetic disorders, not elsewhere classified
CategoryQA1Genetic disorders associated with neoplasms, not elsewhere classified
This CodeQA1.71Lynch syndrome

Present on Admission (POA)Billing

QA1.71 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Genetic disorders, not elsewhere classified (QA0-QA1).

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to QA1.71: its own notes plus those printed at QA1 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Hereditary nonpolyposis colorectal cancer susceptibility
  • Lynch syndrome due to EPCAM
  • Lynch syndrome due to MLH1
  • Lynch syndrome due to MSH2
  • Lynch syndrome due to MSH6
  • Lynch syndrome due to PMS2

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From QA1 Genetic disorders associated with neoplasms, not elsewhere classified applies to 5 codes
  • multiple endocrine neoplasia [MEN] syndromes (E31.2-)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

From QA1 Genetic disorders associated with neoplasms, not elsewhere classified applies to 5 codes
  • if applicable, any associated conditions, such as:
  • genetic susceptibility to malignant neoplasm by site (Z15.0-)
  • malignant neoplasms (C00.0-C96.9)
  • personal history of malignant neoplasm (Z85.-)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical InformationClinical

  • Lynch Syndrome

    an autosomal dominant hereditary neoplastic syndrome characterized by the development of colorectal carcinoma and a high risk of developing endometrial carcinoma, gastric carcinoma, ovarian carcinoma, renal pelvis carcinoma, and small intestinal carcinoma. patients often develop colorectal carcinomas at an early age (mean, 45 years). in the majority of the cases the lesions arise from the proximal colon. at the molecular level, high-frequency microsatellite instability is present.

Code History & ChangesHistory

New Code QA1.71 was added to the ICD-10-CM code set for FY 2027, effective October 1, 2026.

FY 2027AddedAdded to the ICD-10-CM code setEffective October 1, 2026.
FY 2027CurrentRevised in the current code setEffective October 1, 2026 through September 30, 2027.

Questions About QA1.71Overview

What is the ICD-10 code for lynch syndrome?

The ICD-10-CM code for lynch syndrome is QA1.71 (sometimes written as QA171). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is QA1.71 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lynch syndrome on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does QA1.71 group to?

When lynch syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 951 (other Factors Influencing Health Status), which carries a relative weight of 0.5574. Higher weights mean higher Medicare reimbursement.

Is QA1.71 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for lynch syndrome on inpatient claims. The code appears in the Genetic disorders, not elsewhere classified (QA0-QA1) range of the CMS exempt list.