2027 ICD-10-CM Diagnosis Code P00.1Newborn affected by maternal renal and urinary tract diseases

ICD-10-CM Codes›P00–P96›P00-P04›P00

ICD-10-CM P00.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

P00.1 is a billable ICD-10-CM diagnosis code for newborn affected by maternal renal and urinary tract diseases. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 794. The code is exempt from POA reporting. Coders also document this condition as neonatal disorder due to maternal disorder of urinary tract. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Newborn affected by maternal conditions or complications of labor/delivery.

Code Identity

ICD-10-CM Code
P00.1
Billable Status
Yes — Valid for Submission
Code Describes
Newborn affected by maternal renal and urinary tract diseases
Short Description
Newborn aff by maternal renal and urinary tract diseases
Parent Code
P00
Newborn affected by maternal conditions that may be unrelated to present pregnancy

Code Classification

ChapterP00–P96Certain conditions originating in the perinatal period
SectionP00-P04Newborn affected by maternal factors and by complications of pregnancy, labor, and delivery
CategoryP00Newborn affected by maternal conditions that may be unrelated to present pregnancy
This CodeP00.1Newborn affected by maternal renal and urinary tract diseases

Present on Admission (POA)Billing

P00.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Newborn affected by maternal factors and by complications of pregnancy, labor, and delivery (P00-P04).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Neonatal disorder due to maternal disorder of urinary tract
  • Neonatal disorder due to maternal renal disease

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to P00.1: its own notes plus those printed at P00, block P00-P04, and Chapter 16. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • conditions that have their origin in the fetal or perinatal period (before birth through the first 28 days after birth) even if morbidity occurs later

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Newborn affected by maternal conditions classifiable to N00-N39

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From P00 Newborn affected by maternal conditions that may be unrelated to present pregnancy applies to 12 codes
  • encounter for observation of newborn for suspected diseases and conditions ruled out (Z05.-)
  • newborn affected by maternal complications of pregnancy (P01.-)
  • newborn affected by maternal endocrine and metabolic disorders (P70-P74)
  • newborn affected by noxious substances transmitted via placenta or breast milk (P04.-)
From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • tetanus neonatorum (A33)

Code First

The underlying condition named in the note is sequenced before this code.

From P00 Newborn affected by maternal conditions that may be unrelated to present pregnancy applies to 12 codes
  • any current condition in newborn

Notes

General instructions on how these codes are used.

From Block P00-P04 Newborn affected by maternal factors and by complications of pregnancy, labor, and delivery applies to 70 codes
  • These codes are for use when the listed maternal conditions are specified as the cause of confirmed morbidity or potential morbidity which have their origin in the perinatal period (before birth through the first 28 days after birth).
From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • Codes from this chapter are for use on newborn records only, never on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL010
Newborn affected by maternal conditions or complications of labor/delivery
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Infant and Newborn Care

Going home with a new baby is exciting, but it can be scary, too. Newborns have many needs, like frequent feedings and diaper changes. Babies can have health issues that are different from older children and adults, like diaper rash and cradle cap.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert P00.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
760.1 Matern urine dis aff NB
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About P00.1Overview

What is the ICD-10 code for newborn affected by maternal renal and urinary tract diseases?

The ICD-10-CM code for newborn affected by maternal renal and urinary tract diseases is P00.1 (sometimes written as P001). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is P00.1 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report newborn affected by maternal renal and urinary tract diseases on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does P00.1 group to?

When newborn affected by maternal renal and urinary tract diseases is the principal diagnosis on an inpatient stay, it groups to MS-DRG 794 (neonate with Other Significant Problems), which carries a relative weight of 1.4934. Higher weights mean higher Medicare reimbursement.

Is P00.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for newborn affected by maternal renal and urinary tract diseases on inpatient claims. The code appears in the Newborn affected by maternal factors and by complications of pregnancy, labor, and delivery (P00-P04) range of the CMS exempt list.

What is coded first with P00.1?

The Code First note at P00, which applies to P00.1, reads: any current condition in newborn. When one of these applies, it is sequenced before P00.1.