2027 ICD-10-CM Diagnosis Code N90.4Leukoplakia of vulva
ICD-10-CM Codes›N00–N99›N80-N98›N90
- Billable — Valid for Submission
- Chronic Condition
N90.4 is a billable ICD-10-CM diagnosis code for leukoplakia of vulva. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 742 through 743, 760 through 761. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified female genital disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Anogenital lichen sclerosus
- Carcinoma of vulva
- Childhood lichen sclerosus
- Chronic vulvitis
- Dystrophy of vulva
- Genital lichen sclerosus
- Hyperkeratosis of vulva
- Leukoplakia of vulva
- Lichen sclerosus of vulva
- Lichenification of female perineum
- Lichenification of vulva
- Prepubertal lichen sclerosus of vulva
- Squamous cell carcinoma of anogenital area
- Squamous cell carcinoma of vulva
- Squamous cell carcinoma of vulva due to lichen sclerosus
- Squamous cell hyperplasia of vulva
- Vulval intraepithelial neoplasia
- Vulval intraepithelial neoplasia with lichen sclerosus
- Vulval lichen sclerosus, childhood form
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to N90.4: its own notes plus those printed at N90 and Chapter 14. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Dystrophy of vulva
- Kraurosis of vulva
- Lichen sclerosus of external female genital organs
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name N90.4, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Breisky's disease N90.4
Disease, diseased See Also: Syndrome;
vulva N90.4
Hyperkeratosis See Also: Keratosis; L85.9
vulva N90.4
Leukokraurosis vulva (e) N90.4
vulva N90.4
vulva N90.4
vulva N90.4
sclerosus (et atrophicus) L90.0
vulva N90.4
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Vulvar Disorders
The vulva is the outer part of the female genitals. This includes the clitoris, vaginal lips, and the opening to the vagina. A vulvar disorder is a health problem that affects your vulva. These problems may cause pain, itching, or skin changes of the vulva. Treatment depends on the cause.
The full article covers:
- What are vulvar disorders?
- Who is more likely to develop vulvar disorders?
- What are the symptoms of vulvar disorders?
- How are vulvar disorders diagnosed?
- What are the treatments for vulvar disorders?
- Can vulvar disorders be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert N90.4 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About N90.4Overview
What is the ICD-10 code for leukoplakia of vulva?
The ICD-10-CM code for leukoplakia of vulva is N90.4 (sometimes written as N904). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is N90.4 (Other noninflammatory disorders of vulva and perineum) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report leukoplakia of vulva on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does N90.4 group to?
When leukoplakia of vulva is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 743, 760, 761, with relative weights from 0.7039 to 1.8448 depending on complications. Higher weights mean higher Medicare reimbursement.
Can N90.4 be reported with A63.0?
Not as a rule. The Excludes1 note at N90, which applies to N90.4, lists "anogenital (venereal) warts (A63.0)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of N90.4?
Under the General Equivalence Mappings, leukoplakia of vulva converts to ICD-9-CM 624.09 (dystrophy of vulva NEC). The mapping is approximate, so confirm the match fits the documentation.
