2026 ICD-10-CM Diagnosis Code N90.4Leukoplakia of vulva

ICD-10-CM Codes›N00–N99›N80-N98›N90

ICD-10-CM N90.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N90.4 is a billable ICD-10-CM diagnosis code for leukoplakia of vulva. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 742 through 743, 760 through 761. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified female genital disorders.

Code Identity

ICD-10-CM Code
N90.4
Billable Status
Yes — Valid for Submission
Code Describes
Leukoplakia of vulva
Short Description
Leukoplakia of vulva
Same as the full description in the CMS dataset.
Parent Code
N90
Other noninflammatory disorders of vulva and perineum

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN80-N98Noninflammatory disorders of female genital tract
CategoryN90Other noninflammatory disorders of vulva and perineum
This CodeN90.4Leukoplakia of vulva

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Anogenital lichen sclerosus
  • Carcinoma of vulva
  • Childhood lichen sclerosus
  • Chronic vulvitis
  • Dystrophy of vulva
  • Genital lichen sclerosus
  • Hyperkeratosis of female perineum
  • Hyperkeratosis of vulva
  • Leukoplakia of vulva
  • Lichen sclerosus of vulva
  • Lichenification of female perineum
  • Lichenification of vulva
  • Prepubertal lichen sclerosus of vulva
  • Squamous cell carcinoma of anogenital area
  • Squamous cell carcinoma of vulva
  • Squamous cell carcinoma of vulva due to lichen sclerosus
  • Squamous cell hyperplasia of vulva
  • Vulval hyperplasia
  • Vulval intraepithelial neoplasia
  • Vulval intraepithelial neoplasia with lichen sclerosus
  • Vulval lichen sclerosus, childhood form

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Dystrophy of vulva
  • Kraurosis of vulva
  • Lichen sclerosus of external female genital organs

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Breisky's disease
    • Disease, diseased
      • white-spot, meaning lichen sclerosus et atrophicus
        • vulva
    • Dystrophy, dystrophia
      • vulva
    • Hyperkeratosis
      • vulva
    • Kraurosis
      • vulva
    • Leukokraurosis vulva(e)
    • Leukoplakia
      • vulva
    • Lichen
      • albus
        • vulva
    • Lichen
      • atrophicus
        • vulva
    • Lichen
      • sclerosus (et atrophicus)
        • vulva
    • Vulvitis(acute) (allergic) (atrophic) (hypertrophic) (intertriginous) (senile)
      • leukoplakic

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR GEN025
Other specified female genital disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Vulvar Disorders

The vulva is the external part of a woman's genitals. Some problems you can have with the vulvar area include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert N90.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
624.09 Dystrophy of vulva NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About N90.4Overview

Is N90.4 (Other noninflammatory disorders of vulva and perineum) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report leukoplakia of vulva on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does N90.4 group to?

When leukoplakia of vulva is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 743, 760, 761, with relative weights from 0.5696 to 1.8348 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of N90.4?

Under the General Equivalence Mappings, leukoplakia of vulva converts to ICD-9-CM 624.09 (dystrophy of vulva NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.