2026 ICD-10-CM Diagnosis Code L95.0Livedoid vasculitis

ICD-10-CM Codes›L00–L99›L80-L99›L95

ICD-10-CM L95.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

L95.0 is a billable ICD-10-CM diagnosis code for livedoid vasculitis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. Coders also document this condition as congenital livedo reticularis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin and Vasculitis.

Code Identity

ICD-10-CM Code
L95.0
Billable Status
Yes — Valid for Submission
Code Describes
Livedoid vasculitis
Short Description
Livedoid vasculitis
Same as the full description in the CMS dataset.
Parent Code
L95
Vasculitis limited to skin, not elsewhere classified

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL80-L99Other disorders of the skin and subcutaneous tissue
CategoryL95Vasculitis limited to skin, not elsewhere classified
This CodeL95.0Livedoid vasculitis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital livedo reticularis
  • Idiopathic livedo reticularis
  • Idiopathic livedo reticularis with summer ulceration
  • Livedo reticularis
  • Livedoid vasculopathy of lower limb due to varicose veins of lower limb

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Atrophie blanche (en plaque)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Atrophie blanche(en plaque) (de Milian)
    • Atrophy, atrophic(of)
      • blanche (en plaque) (of Milian)
    • Vasculitis
      • livedoid

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR CIR037
Vasculitis
Default principal diagnosis: inpatient No · outpatient No

Clinical InformationClinical

  • Livedo Reticularis

    a condition characterized by a reticular or fishnet pattern on the skin of lower extremities and other parts of the body. this red and blue pattern is due to deoxygenated blood in unstable dermal blood vessels. the condition is intensified by cold exposure and relieved by rewarming.

  • Livedoid Vasculopathy

    a rare cutaneous thrombotic disease due to occlusion of dermal vessels. it is characterized by purpuric maculae and ulcerations especially during summer which form scars called atrophie blanche. it is more associated with other syndromes (e.g., protein c deficiency; hyperhomocysteinemia). livedo reticularis with systemic involvement and stroke is sneddon syndrome.

  • Sneddon Syndrome

    a systemic non-inflammatory arteriopathy primarily of middle-aged females characterized by the association of livedo reticularis, multiple thrombotic cerebral infarction; coronary disease, and hypertension. elevation of antiphospholipid antibody titers (see also antiphospholipid syndrome), cardiac valvulopathy, ischemic attack, transient; seizures; dementia; and chronic ischemia of the extremities may also occur. pathologic examination of affected arteries reveals non-inflammatory adventitial fibrosis, thrombosis, and changes in the media (from jablonski, dictionary of syndromes & eponymic diseases, 2d ed; adams et al., principles of neurology, 6th ed, p861; arch neurol 1997 jan;54(1):53-60). mutations in the cecr1 gene (ada2 protein, human) are associated with sneddon syndrome.

  • Livedo Reticularis

    a recurrent purple discoloration of the skin that does not blanche and is found in a lacy, network pattern, most often in the lower extremities. it may be aggravated by exposure to cold and is classified as idiopathic or secondary. secondary livedo reticularis may be a cutaneous manifestation of immune system disorders (e.g., lupus erythematosus, rheumatoid arthritis, cryoglobulinemia, lymphoma, etc), and hematologic disorders (polycythemia vera).

Patient EducationClinical

Vasculitis

Vasculitis is an inflammation of the blood vessels. It happens when the body's immune system attacks the blood vessel by mistake. It can happen because of an infection, a medicine, or another disease. The cause is often unknown.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L95.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
709.1 Vascular disord of skin
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About L95.0Overview

Is L95.0 (Vasculitis limited to skin, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report livedoid vasculitis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does L95.0 group to?

When livedoid vasculitis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L95.0?

Under the General Equivalence Mappings, livedoid vasculitis converts to ICD-9-CM 709.1 (vascular disord of skin). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.