1. Home
  2. ICD-10-CM Codes List
  3. L00–L99
  4. L80-L99
  5. Other localized connective tissue disorders (L94)

Other localized connective tissue disorders (L94)

The ICD-10 code section L94 covers various other localized connective tissue disorders, which include specific skin and tissue conditions such as localized scleroderma, calcinosis cutis, and sclerodactyly. These codes are used to classify disorders affecting connective tissue that are limited to certain areas rather than systemic involvement.

This section includes L94.0 for localized scleroderma (morphea), known by synonyms like plaque morphea and disabling pansclerotic morphea of children, capturing changes in skin thickening and hardening. L94.1 codes for linear scleroderma, also called coup de sabre scleroderma, characterized by lines of hardened skin. L94.2 represents calcinosis cutis, the abnormal skin calcification linked to terms such as dystrophic scrotal calcinosis and tumoral calcinosis. Other codes cover conditions like sclerodactyly (L94.3), Gottron's papules (L94.4), and ainhum (L94.6). Medical professionals and coders use these detailed ICD-10 codes to accurately identify and document localized connective tissue disorders, aligning clinical descriptions with proper coding for diagnosis and treatment.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • systemic connective tissue disorders M30 M36

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Ainhum

Spontaneous autoamputation of the fourth or fifth toe.

Calcinosis Cutis

Pathological deposition of calcium in the skin and subcutaneous tissue. Excessive calcification of the skin may be associated with underlying diseases that cause tissue damage (e.g., EHLERS-DANLOS SYNDROME; PSEUDOXANTHOMA ELASTICUM; ROTHMUND-THOMSON SYNDROME; and WERNER SYNDROME) or that cause abnormal calcium and phosphate metabolism (e.g., CALCIPHYLAXIS; CHRONIC KIDNEY FAILURE; HYPERPARATHYROIDISM; and SARCOIDOSIS).

Parapsoriasis

The term applied to a group of relatively uncommon inflammatory, maculopapular, scaly eruptions of unknown etiology and resistant to conventional treatment. Eruptions are both psoriatic and lichenoid in appearance, but the diseases are distinct from psoriasis, lichen planus, or other recognized dermatoses. Proposed nomenclature divides parapsoriasis into two distinct subgroups, PITYRIASIS LICHENOIDES and parapsoriasis en plaques (small- and large-plaque parapsoriasis).

Pityriasis Lichenoides

A subgroup of PARAPSORIASIS itself divided into acute and chronic forms. The acute form is characterized by the abrupt onset of a generalized, reddish-brown, maculopapular eruption. Lesions may be vesicular, hemorrhagic, crusted, or necrotic. Histologically the disease is characterized by epidermal necrolysis. The chronic form shows milder skin changes with necrosis.