Other localized connective tissue disorders (L94) ICD-10-CM
The L94 code range covers other localized connective tissue disorders with 10 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the L94 Range 10 codes · 9 billable
- L94 Other localized connective tissue disordersNon-billable
- L94.0 Localized scleroderma [morphea]
- L94.1 Linear scleroderma
- L94.2 Calcinosis cutis
- L94.3 Sclerodactyly
- L94.4 Gottron's papules
- L94.5 Poikiloderma vasculare atrophicans
- L94.6 Ainhum
- L94.8 Other specified localized connective tissue disorders
- L94.9 Localized connective tissue disorder, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the L94 range.
Ainhum
Spontaneous autoamputation of the fourth or fifth toe.
Calcinosis Cutis
Pathological deposition of calcium in the skin and subcutaneous tissue. Excessive calcification of the skin may be associated with underlying diseases that cause tissue damage (e.g., EHLERS-DANLOS SYNDROME; PSEUDOXANTHOMA ELASTICUM; ROTHMUND-THOMSON SYNDROME; and WERNER SYNDROME) or that cause abnormal calcium and phosphate metabolism (e.g., CALCIPHYLAXIS; CHRONIC KIDNEY FAILURE; HYPERPARATHYROIDISM; and SARCOIDOSIS).
Parapsoriasis
The term applied to a group of relatively uncommon inflammatory, maculopapular, scaly eruptions of unknown etiology and resistant to conventional treatment. Eruptions are both psoriatic and lichenoid in appearance, but the diseases are distinct from psoriasis, lichen planus, or other recognized dermatoses. Proposed nomenclature divides parapsoriasis into two distinct subgroups, PITYRIASIS LICHENOIDES and parapsoriasis en plaques (small- and large-plaque parapsoriasis).
Pityriasis Lichenoides
A subgroup of PARAPSORIASIS itself divided into acute and chronic forms. The acute form is characterized by the abrupt onset of a generalized, reddish-brown, maculopapular eruption. Lesions may be vesicular, hemorrhagic, crusted, or necrotic. Histologically the disease is characterized by epidermal necrolysis. The chronic form shows milder skin changes with necrosis.
About the L94 Code Range
The ICD-10 code section L94 covers various other localized connective tissue disorders, which include specific skin and tissue conditions such as localized scleroderma, calcinosis cutis, and sclerodactyly. These codes are used to classify disorders affecting connective tissue that are limited to certain areas rather than systemic involvement.
This section includes L94.0 for localized scleroderma (morphea), known by synonyms like plaque morphea and disabling pansclerotic morphea of children, capturing changes in skin thickening and hardening. L94.1 codes for linear scleroderma, also called coup de sabre scleroderma, characterized by lines of hardened skin. L94.2 represents calcinosis cutis, the abnormal skin calcification linked to terms such as dystrophic scrotal calcinosis and tumoral calcinosis. Other codes cover conditions like sclerodactyly (L94.3), Gottron's papules (L94.4), and ainhum (L94.6). Medical professionals and coders use these detailed ICD-10 codes to accurately identify and document localized connective tissue disorders, aligning clinical descriptions with proper coding for diagnosis and treatment.
Questions About This Page
How many billable codes are in the L94 range?
Of the 10 codes in this range, 9 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the L94 range classify?
The range classifies other localized connective tissue disorders. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
