Other localized connective tissue disorders (L94) ICD-10-CM
The L94 code range covers other localized connective tissue disorders with 10 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the L94 Range 10 codes · 9 billable
- L94 Other localized connective tissue disordersNon-billable
- L94.0 Localized scleroderma [morphea]
- L94.1 Linear scleroderma
- L94.2 Calcinosis cutis
- L94.3 Sclerodactyly
- L94.4 Gottron's papules
- L94.5 Poikiloderma vasculare atrophicans
- L94.6 Ainhum
- L94.8 Other specified localized connective tissue disorders
- L94.9 Localized connective tissue disorder, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the L94 range.
Ainhum
Spontaneous autoamputation of the fourth or fifth toe.
Calcinosis Cutis
Pathological deposition of calcium in the skin and subcutaneous tissue. Excessive calcification of the skin may be associated with underlying diseases that cause tissue damage (e.g. EHLERS-DANLOS SYNDROME; PSEUDOXANTHOMA ELASTICUM; ROTHMUND-THOMSON SYNDROME; and WERNER SYNDROME) or that cause abnormal calcium and phosphate metabolism (e.g., CALCIPHYLAXIS; CHRONIC KIDNEY FAILURE; HYPERPARATHYROIDISM; and SARCOIDOSIS).
Linear Scleroderma
A type of localized scleroderma characterized by a long strip of indurated skin, which is typically found unilaterally on an arm or leg, and sometimes on the forehead or trunk. This disorder often affects the tissues beneath the skin, causing damage to bones, muscle or other organs. It can limit movement, alter growth, and disfigure the affected area.
Localized Scleroderma
A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. Localized scleroderma typically affects the skin, with formation of patches or lines of thick and unyielding tissue; there can be muscle and underlying tissue involvement as well as occasional joint complications. The affected areas of skin can be restrictive and disfiguring. The shape, depth and location of the affected area is used to classify one of the four types of local scleroderma. An individual can have a combination of localized scleroderma types.
Sclerodactyly
Thickening of the skin of the digits which leads to contractures.
About the L94 Code Range
These are localized connective tissue disorders of the skin or tissue beneath it.
The subdivisions distinguish localized scleroderma, also called morphea, from linear scleroderma. Other subdivisions name distinct disorders rather than separating them by site or severity. L94.8 identifies other specified localized connective tissue disorders, while L94.9 identifies an unspecified disorder.
Questions About This Page
How many billable codes are in the L94 range?
Of the 10 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the L94 range classify?
The range classifies other localized connective tissue disorders. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
