2027 ICD-10-CM Diagnosis Code L94.1Linear scleroderma

ICD-10-CM Codes›L00–L99›L80-L99›L94

ICD-10-CM L94.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

L94.1 is a billable ICD-10-CM diagnosis code for linear scleroderma. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. Coders also document this condition as coup de sabre scleroderma. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified skin disorders.

Code Identity

ICD-10-CM Code
L94.1
Billable Status
Yes — Valid for Submission
Code Describes
Linear scleroderma
Short Description
Linear scleroderma
Same as the full description in the CMS dataset.
Parent Code
L94
Other localized connective tissue disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL80-L99Other disorders of the skin and subcutaneous tissue
CategoryL94Other localized connective tissue disorders
This CodeL94.1Linear scleroderma

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Coup de sabre scleroderma
  • Linear scleroderma
  • Localized scleroderma

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to L94.1: its own notes plus those printed at L94 and Chapter 12. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • En coup de sabre lesion

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From L94 Other localized connective tissue disorders applies to 9 codes
  • systemic connective tissue disorders (M30-M36)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue applies to 1,001 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • lipomelanotic reticulosis (I89.8)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • viral warts (B07.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN007
Other specified and unspecified skin disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Linear Scleroderma

    a type of localized scleroderma characterized by a long strip of indurated skin, which is typically found unilaterally on an arm or leg, and sometimes on the forehead or trunk. this disorder often affects the tissues beneath the skin, causing damage to bones, muscle or other organs. it can limit movement, alter growth, and disfigure the affected area.

Patient EducationClinical

Scleroderma

Scleroderma means "hard skin." It's the name of an autoimmune disease that causes inflammation and thickening in the skin and other areas of the body. This inflammation causes you to have areas of tight, hard skin. Scleroderma may affect just one area of your body, or it can affect many systems in your body.

The full article covers:

  • What is scleroderma?
  • What are the types of scleroderma?
  • What causes scleroderma?
  • Who is more likely to develop scleroderma?
  • What are the symptoms of scleroderma?
  • How is scleroderma diagnosed?
  • What are the treatments for scleroderma?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L94.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
701.0 Circumscribe scleroderma
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About L94.1Overview

What is the ICD-10 code for linear scleroderma?

The ICD-10-CM code for linear scleroderma is L94.1 (sometimes written as L941). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is L94.1 (Other localized connective tissue disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report linear scleroderma on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does L94.1 group to?

When linear scleroderma is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L94.1?

Under the General Equivalence Mappings, linear scleroderma converts to ICD-9-CM 701.0 (circumscribe scleroderma). The mapping is approximate, so confirm the match fits the documentation.