2026 ICD-10-CM Diagnosis Code L94.1Linear scleroderma

ICD-10-CM Codes›L00–L99›L80-L99›L94

ICD-10-CM L94.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

L94.1 is a billable ICD-10-CM diagnosis code for linear scleroderma. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. Coders also document this condition as coup de sabre scleroderma. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified skin disorders.

Code Identity

ICD-10-CM Code
L94.1
Billable Status
Yes — Valid for Submission
Code Describes
Linear scleroderma
Short Description
Linear scleroderma
Same as the full description in the CMS dataset.
Parent Code
L94
Other localized connective tissue disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL80-L99Other disorders of the skin and subcutaneous tissue
CategoryL94Other localized connective tissue disorders
This CodeL94.1Linear scleroderma

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Coup de sabre scleroderma
  • Linear scleroderma
  • Localized scleroderma

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • En coup de sabre lesion

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • En coup de sabre lesion
    • Lesion(s) (nontraumatic)
      • en coup de sabre
    • Scleroderma, sclerodermia(acrosclerotic) (diffuse) (generalized) (progressive) (pulmonary)
      • linear

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN007
Other specified and unspecified skin disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Scleroderma

Scleroderma means "hard skin." It's the name of an autoimmune disease that causes inflammation and thickening in the skin and other areas of the body. This inflammation causes you to have areas of tight, hard skin. Scleroderma may affect just one area of your body, or it can affect many systems in your body.

The full article covers:

  • What is scleroderma?
  • What are the types of scleroderma?
  • What causes scleroderma?
  • Who is more likely to develop scleroderma?
  • What are the symptoms of scleroderma?
  • How is scleroderma diagnosed?
  • What are the treatments for scleroderma?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L94.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
701.0 Circumscribe scleroderma
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About L94.1Overview

Is L94.1 (Other localized connective tissue disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report linear scleroderma on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does L94.1 group to?

When linear scleroderma is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L94.1?

Under the General Equivalence Mappings, linear scleroderma converts to ICD-9-CM 701.0 (circumscribe scleroderma). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.