2027 ICD-10-CM Diagnosis Code L44.0Pityriasis rubra pilaris

ICD-10-CM Codes›L00–L99›L40-L45›L44

ICD-10-CM L44.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

L44.0 is a billable ICD-10-CM diagnosis code for pityriasis rubra pilaris. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

Code Identity

ICD-10-CM Code
L44.0
Billable Status
Yes — Valid for Submission
Code Describes
Pityriasis rubra pilaris
Short Description
Pityriasis rubra pilaris
Same as the full description in the CMS dataset.
Parent Code
L44
Other papulosquamous disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL40-L45Papulosquamous disorders
CategoryL44Other papulosquamous disorders
This CodeL44.0Pityriasis rubra pilaris

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adult pityriasis rubra pilaris
  • Atypical adult pityriasis rubra pilaris
  • Atypical juvenile pityriasis rubra pilaris
  • Circumscribed juvenile pityriasis rubra pilaris
  • Classical adult pityriasis rubra pilaris
  • Classical juvenile pityriasis rubra pilaris
  • Disorder of skin due to human immunodeficiency virus infection
  • Juvenile pityriasis rubra pilaris
  • Nail dystrophy due to pityriasis rubra pilaris
  • Pityriasis rubra pilaris
  • Pityriasis rubra pilaris due to human immunodeficiency virus infection

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to L44.0: its own notes plus those printed at Chapter 12. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue applies to 1,001 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • lipomelanotic reticulosis (I89.8)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • viral warts (B07.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Pityriasis Rubra Pilaris

    a chronic skin disease characterized by small follicular papules, disseminated reddish-brown scaly patches, and often, palmoplantar hyperkeratosis. the papules are about the size of a pin and topped by a horny plug.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L44.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
696.4 Pityriasis rubra pilaris
Approximate The match is approximate rather than exact.
ICD-9-CM
696.8 Psorias related dis NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About L44.0Overview

What is the ICD-10 code for pityriasis rubra pilaris?

The ICD-10-CM code for pityriasis rubra pilaris is L44.0 (sometimes written as L440). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is L44.0 (Other papulosquamous disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pityriasis rubra pilaris on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does L44.0 group to?

When pityriasis rubra pilaris is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L44.0?

Under the General Equivalence Mappings, pityriasis rubra pilaris converts to ICD-9-CM 696.4 (pityriasis rubra pilaris) and 696.8 (psorias related dis NEC). The mapping is approximate, so confirm the match fits the documentation.