2026 ICD-10-CM Diagnosis Code L44.0Pityriasis rubra pilaris

ICD-10-CM Codes›L00–L99›L40-L45›L44

ICD-10-CM L44.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

L44.0 is a billable ICD-10-CM diagnosis code for pityriasis rubra pilaris. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

Code Identity

ICD-10-CM Code
L44.0
Billable Status
Yes — Valid for Submission
Code Describes
Pityriasis rubra pilaris
Short Description
Pityriasis rubra pilaris
Same as the full description in the CMS dataset.
Parent Code
L44
Other papulosquamous disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL40-L45Papulosquamous disorders
CategoryL44Other papulosquamous disorders
This CodeL44.0Pityriasis rubra pilaris

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adult pityriasis rubra pilaris
  • Atypical adult pityriasis rubra pilaris
  • Atypical juvenile pityriasis rubra pilaris
  • Circumscribed juvenile pityriasis rubra pilaris
  • Classical adult pityriasis rubra pilaris
  • Classical juvenile pityriasis rubra pilaris
  • Disorder of skin due to human immunodeficiency virus infection
  • Juvenile pityriasis rubra pilaris
  • Nail dystrophy due to pityriasis rubra pilaris
  • Pityriasis rubra pilaris
  • Pityriasis rubra pilaris due to human immunodeficiency virus infection

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Devergie's disease(pityriasis rubra pilaris)
    • Disease, diseased
      • Devergie's (pityriasis rubra pilaris)
    • Disease, diseased
      • Hebra's
        • pityriasis
          • rubra pilaris
    • Disease, diseased
      • Tarral-Besnier (pityriasis rubra pilaris)
    • Kaposi's
      • lichen ruber
    • Kaposi's
      • lichen ruber
        • acuminatus
    • Lichen
      • ruber
        • acuminatus
    • Pityriasis(capitis)
      • pilaris, Hebra's
    • Pityriasis(capitis)
      • rubra (Hebra) pilaris
    • Tarral-Besnier disease

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Pityriasis Rubra Pilaris

    a chronic skin disease characterized by small follicular papules, disseminated reddish-brown scaly patches, and often, palmoplantar hyperkeratosis. the papules are about the size of a pin and topped by a horny plug.

  • Pityriasis Rubra Pilaris

    a rare cutaneous disorder of unknown etiology characterized by the presence of reddish-orange scaly plaques, palmoplantar keratoderma, keratotic follicular papules, and confluent erythematous areas with areas of normal skin between the lesions.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L44.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
696.4 Pityriasis rubra pilaris
Approximate The match is approximate rather than exact.
ICD-9-CM
696.8 Psorias related dis NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About L44.0Overview

Is L44.0 (Other papulosquamous disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pityriasis rubra pilaris on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does L44.0 group to?

When pityriasis rubra pilaris is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L44.0?

Under the General Equivalence Mappings, pityriasis rubra pilaris converts to ICD-9-CM 696.4 (pityriasis rubra pilaris) and 696.8 (psorias related dis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.