2027 ICD-10-CM Diagnosis Code H31.20Hereditary choroidal dystrophy, unspecified

ICD-10-CM Codes›H00–H59›H30-H36›H31

ICD-10-CM H31.20
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

H31.20 is a billable ICD-10-CM diagnosis code for hereditary choroidal dystrophy, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. Coders also document this condition as autosomal dominant vitreoretinochoroidopathy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Retinal and vitreous conditions.

Code Identity

ICD-10-CM Code
H31.20
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary choroidal dystrophy, unspecified
Short Description
Hereditary choroidal dystrophy, unspecified
Same as the full description in the CMS dataset.
Parent Code
Hereditary choroidal dystrophy

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH30-H36Disorders of choroid and retina
CategoryH31Other disorders of choroid
This CodeH31.20Hereditary choroidal dystrophy, unspecified

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant vitreoretinochoroidopathy
  • Boucher Neuhäuser syndrome
  • Choroidal dystrophy
  • Congenital chorioretinal degeneration
  • Congenital ectopic lens
  • Ectopia lentis, chorioretinal dystrophy, myopia syndrome
  • Hereditary choroidal dystrophy

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to H31.20: its own notes plus those printed at H31.2 and Chapter 7. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From H31.2 Hereditary choroidal dystrophy applies to 5 codes
From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Notes

General instructions on how these codes are used.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name H31.20, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming H31.20: they are not reported together with it, unless the two conditions are unrelated.

  • E72.4 Disorders of ornithine metabolism
    hereditary choroidal dystrophy (H31.2-) names H31.2-, which includes this code

Use Additional Code 1

These codes say to use an additional code from the note, and H31.20 is one of the codes named.

  • H44.2A Degenerative myopia with choroidal neovascularization
    code for any associated choroid disorders (H31.-) names H31.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE005
Retinal and vitreous conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Eye Diseases

Even if your eyes feel healthy, you could have a problem and not know it. That's why regular eye exams are so important. Refractive errors are the most common type of vision problem that makes it hard to see clearly. But some eye conditions or diseases don't have any symptoms and can lead to a permanent loss of vision.

The full article covers:

  • What diseases can affect the eye?
  • What are the symptoms of eye diseases?
  • Who is more likely to develop eye diseases?
  • What are the treatments for eye diseases?
  • Can eye diseases be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H31.20 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
363.50 Hered choroid atroph NOS
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About H31.20Overview

What is the ICD-10 code for hereditary choroidal dystrophy, unspecified?

The ICD-10-CM code for hereditary choroidal dystrophy, unspecified is H31.20 (sometimes written as H3120). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is H31.20 (Hereditary choroidal dystrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary choroidal dystrophy, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does H31.20 group to?

When hereditary choroidal dystrophy, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H31.20?

Under the General Equivalence Mappings, hereditary choroidal dystrophy, unspecified converts to ICD-9-CM 363.50 (hered choroid atroph NOS). The mapping is a direct match.