2026 ICD-10-CM Diagnosis Code H18.513Endothelial corneal dystrophy, bilateral

ICD-10-CM Codes›H00–H59›H15-H22›H18

ICD-10-CM H18.513
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H18.513 is a billable ICD-10-CM diagnosis code for endothelial corneal dystrophy, bilateral. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cornea and external disease.

Code Identity

ICD-10-CM Code
H18.513
Billable Status
Yes — Valid for Submission
Code Describes
Endothelial corneal dystrophy, bilateral
Short Description
Endothelial corneal dystrophy, bilateral
Same as the full description in the CMS dataset.
Parent Code
H18.51
Endothelial corneal dystrophy

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH15-H22Disorders of sclera, cornea, iris and ciliary body
CategoryH18Other disorders of cornea
This CodeH18.513Endothelial corneal dystrophy, bilateral

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Angle closure of left eye due to iridocorneal endothelial syndrome
  • Angle closure of right eye due to iridocorneal endothelial syndrome
  • Bilateral angle closure due to iridocorneal endothelial syndrome
  • Bilateral dystrophy of posterior surface of cornea of eyes
  • Bilateral iridocorneal endothelial syndrome of eyes
  • Bilateral secondary angle closure glaucoma
  • Bilateral secondary angle-closure glaucoma due to iridocorneal endothelial syndrome
  • Chandler syndrome
  • Iridocorneal endothelial syndrome
  • Iridocorneal endothelial syndrome of left eye
  • Iridocorneal endothelial syndrome of right eye
  • Secondary angle-closure due to iridocorneal endothelial syndrome
  • Secondary angle-closure glaucoma due to iridocorneal endothelial syndrome
  • Secondary angle-closure glaucoma of left eye due to iridocorneal endothelial syndrome
  • Secondary angle-closure glaucoma of right eye due to iridocorneal endothelial syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE001
Cornea and external disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Iridocorneal Endothelial Syndrome

    a grouping of three closely linked conditions: iris nevus (or cogan-reese) syndrome, chandler syndrome, and essential (progressive) iris atrophy. the most common features of this syndrome are the movement of endothelial cells off the cornea onto the iris leading to corneal swelling, distortion of the iris, and variable degrees of distortion of the pupil. the abnormal cell movement plugs fluid outflow channels of the eye causing glaucoma.

  • Glaucoma

    an ocular disease, occurring in many forms, having as its primary characteristics an unstable or a sustained increase in the intraocular pressure which the eye cannot withstand without damage to its structure or impairment of its function. the consequences of the increased pressure may be manifested in a variety of symptoms, depending upon type and severity, such as excavation of the optic disk, hardness of the eyeball, corneal anesthesia, reduced visual acuity, seeing of colored halos around lights, disturbed dark adaptation, visual field defects, and headaches. (dictionary of visual science, 4th ed)

  • Iridocorneal Endothelial Syndrome

    a group of disorders characterized by the presence of an abnormal inner layer of the cornea. this abnormality results in iris distortion, corneal swelling, pupil distortion, and glaucoma. it usually affects only one eye.

Patient EducationClinical

Corneal Disorders

Your cornea is the outermost layer of your eye. It is clear and shaped like a dome. The cornea helps to shield the rest of the eye from germs, dust, and other harmful matter. It also helps your eye to focus. If you wear contact lenses, they float on top of your corneas.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement H18.513 replaces the following previously assigned code(s):

  • H18.51 - Endothelial corneal dystrophy
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H18.513Overview

Is H18.513 (Endothelial corneal dystrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report endothelial corneal dystrophy, bilateral on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does H18.513 group to?

When endothelial corneal dystrophy, bilateral is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.