2021 ICD-10-CM Code H18.5

Hereditary corneal dystrophies

Version 2021

Not Valid for Submission

H18.5 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of hereditary corneal dystrophies. The code is not specific and is NOT valid for the year 2021 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

ICD-10:H18.5
Short Description:Hereditary corneal dystrophies
Long Description:Hereditary corneal dystrophies

Code Classification

Specific Coding for Hereditary corneal dystrophies

Non-specific codes like H18.5 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for hereditary corneal dystrophies:

  • NON-BILLABLE CODE - H18.50 for Unspecified hereditary corneal dystrophies
  • BILLABLE CODE - Use H18.501 for Unspecified hereditary corneal dystrophies, right eye
  • BILLABLE CODE - Use H18.502 for Unspecified hereditary corneal dystrophies, left eye
  • BILLABLE CODE - Use H18.503 for Unspecified hereditary corneal dystrophies, bilateral
  • BILLABLE CODE - Use H18.509 for Unspecified hereditary corneal dystrophies, unspecified eye
  • NON-BILLABLE CODE - H18.51 for Endothelial corneal dystrophy
  • BILLABLE CODE - Use H18.511 for Endothelial corneal dystrophy, right eye
  • BILLABLE CODE - Use H18.512 for Endothelial corneal dystrophy, left eye
  • BILLABLE CODE - Use H18.513 for Endothelial corneal dystrophy, bilateral
  • BILLABLE CODE - Use H18.519 for Endothelial corneal dystrophy, unspecified eye
  • NON-BILLABLE CODE - H18.52 for Epithelial (juvenile) corneal dystrophy
  • BILLABLE CODE - Use H18.521 for Epithelial (juvenile) corneal dystrophy, right eye
  • BILLABLE CODE - Use H18.522 for Epithelial (juvenile) corneal dystrophy, left eye
  • BILLABLE CODE - Use H18.523 for Epithelial (juvenile) corneal dystrophy, bilateral
  • BILLABLE CODE - Use H18.529 for Epithelial (juvenile) corneal dystrophy, unspecified eye
  • NON-BILLABLE CODE - H18.53 for Granular corneal dystrophy
  • BILLABLE CODE - Use H18.531 for Granular corneal dystrophy, right eye
  • BILLABLE CODE - Use H18.532 for Granular corneal dystrophy, left eye
  • BILLABLE CODE - Use H18.533 for Granular corneal dystrophy, bilateral
  • BILLABLE CODE - Use H18.539 for Granular corneal dystrophy, unspecified eye
  • NON-BILLABLE CODE - H18.54 for Lattice corneal dystrophy
  • BILLABLE CODE - Use H18.541 for Lattice corneal dystrophy, right eye
  • BILLABLE CODE - Use H18.542 for Lattice corneal dystrophy, left eye
  • BILLABLE CODE - Use H18.543 for Lattice corneal dystrophy, bilateral
  • BILLABLE CODE - Use H18.549 for Lattice corneal dystrophy, unspecified eye
  • NON-BILLABLE CODE - H18.55 for Macular corneal dystrophy
  • BILLABLE CODE - Use H18.551 for Macular corneal dystrophy, right eye
  • BILLABLE CODE - Use H18.552 for Macular corneal dystrophy, left eye
  • BILLABLE CODE - Use H18.553 for Macular corneal dystrophy, bilateral
  • BILLABLE CODE - Use H18.559 for Macular corneal dystrophy, unspecified eye
  • NON-BILLABLE CODE - H18.59 for Other hereditary corneal dystrophies
  • BILLABLE CODE - Use H18.591 for Other hereditary corneal dystrophies, right eye
  • BILLABLE CODE - Use H18.592 for Other hereditary corneal dystrophies, left eye
  • BILLABLE CODE - Use H18.593 for Other hereditary corneal dystrophies, bilateral
  • BILLABLE CODE - Use H18.599 for Other hereditary corneal dystrophies, unspecified eye

Clinical Information

Information for Patients


Corneal Disorders

Your cornea is the outermost layer of your eye. It is clear and shaped like a dome. The cornea helps to shield the rest of the eye from germs, dust, and other harmful matter. It also helps your eye to focus. If you wear contact lenses, they float on top of your corneas.

Problems with the cornea include

Treatments of corneal disorders include medicines, corneal transplantation, and corneal laser surgery.

NIH: National Eye Institute


[Learn More in MedlinePlus]

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)