ICD-10-CM Code H18.50

Unspecified hereditary corneal dystrophies

Version 2021 Replaced Code Non-Billable Code

Not Valid for Submission

H18.50 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of unspecified hereditary corneal dystrophies. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions.

ICD-10:H18.50
Short Description:Unspecified hereditary corneal dystrophies
Long Description:Unspecified hereditary corneal dystrophies

Consider the following ICD-10 codes with a higher level of specificity:

Replaced Code

This code was replaced in the 2021 ICD-10 code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2020. This code was replaced for the FY 2021 (October 1, 2020 - September 30, 2021).

  • H18.501 - Unspecified hereditary corneal dystrophies, right eye
  • H18.502 - Unspecified hereditary corneal dystrophies, left eye
  • H18.503 - Unspecified hereditary corneal dystrophies, bilateral
  • H18.509 - Unspecified hereditary corneal dystrophies, unspecified eye

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code H18.50 are found in the index:


Clinical Information

  • CORNEAL DYSTROPHIES HEREDITARY-. bilateral hereditary disorders of the cornea usually autosomal dominant which may be present at birth but more frequently develop during adolescence and progress slowly throughout life. central macular dystrophy is transmitted as an autosomal recessive defect.

Convert H18.50 to ICD-9

  • 371.50 - Corneal dystrophy NOS

Code Classification

  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of sclera, cornea, iris and ciliary body (H15-H22)
      • Other disorders of cornea (H18)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - Code Deleted, effective from 10/1/2020 through 9/30/2021

Information for Patients


Corneal Disorders

Your cornea is the outermost layer of your eye. It is clear and shaped like a dome. The cornea helps to shield the rest of the eye from germs, dust, and other harmful matter. It also helps your eye to focus. If you wear contact lenses, they float on top of your corneas.

Problems with the cornea include

  • Refractive errors
  • Allergies
  • Infections
  • Injuries
  • Dystrophies - conditions in which parts of the cornea lose clarity due to a buildup of cloudy material

Treatments of corneal disorders include medicines, corneal transplantation, and corneal laser surgery.

NIH: National Eye Institute

  • Cloudy cornea (Medical Encyclopedia)
  • Corneal injury (Medical Encyclopedia)
  • Corneal transplant (Medical Encyclopedia)
  • Corneal ulcers and infections (Medical Encyclopedia)
  • Fuchs dystrophy (Medical Encyclopedia)
  • Keratoconus (Medical Encyclopedia)

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