2026 ICD-10-CM Diagnosis Code P94.2Congenital hypotonia

ICD-10-CM Codes›P00–P96›P90-P96›P94

ICD-10-CM P94.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

P94.2 is a billable ICD-10-CM diagnosis code for congenital hypotonia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified perinatal conditions.

Code Identity

ICD-10-CM Code
P94.2
Billable Status
Yes — Valid for Submission
Code Describes
Congenital hypotonia
Short Description
Congenital hypotonia
Same as the full description in the CMS dataset.
Parent Code
P94
Disorders of muscle tone of newborn

Code Classification

ChapterP00–P96Certain conditions originating in the perinatal period
SectionP90-P96Other disorders originating in the perinatal period
CategoryP94Disorders of muscle tone of newborn
This CodeP94.2Congenital hypotonia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Atypical hypotonia cystinuria syndrome
  • Benign congenital hypotonia
  • Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome
  • Congenital contracture of limbs and face, hypotonia, developmental delay syndrome
  • Congenital hypoplasia of bone of radius and/or ulna
  • Congenital hypoplasia of ulna
  • Cystinuria
  • Cystinuria, type 1
  • Flaccid newborn
  • Growth and developmental delay, hypotonia, vision impairment, lactic acidosis syndrome
  • Hypertrophic cardiomyopathy with hypotonia and lactic acidosis syndrome
  • Hypertrophic mitochondrial cardiomyopathy
  • Hypotonia, speech impairment, severe cognitive delay syndrome
  • Infantile hypotonia, oculomotor anomalies, hyperkinetic movements, developmental delay syndrome
  • Intellectual disability, hypotonia, brachycephaly, pyloric stenosis, cryptorchidism syndrome
  • Intellectual disability, seizures, hypotonia, ophthalmologic, skeletal anomalies syndrome
  • Left ventricular myocardial noncompaction cardiomyopathy
  • Lethal left ventricular non-compaction, seizures, hypotonia, cataract, developmental delay syndrome
  • Lethal pontocerebellar hypoplasia, hypotonia, respiratory insufficiency syndrome
  • Multiple congenital anomalies, hypotonia, seizures syndrome
  • Multiple congenital anomalies, hypotonia, seizures syndrome type 2
  • Neonatal hypotonia
  • Neonatal neuromuscular disorder
  • Postnatal microcephaly, infantile hypotonia, spastic diplegia, dysarthria, intellectual disability syndrome
  • Puerto Rican infant hypotonia syndrome
  • Respiratory insufficiency syndrome of newborn
  • Severe hypotonia, psychomotor developmental delay, strabismus, cardiac septal defect syndrome
  • Severe intellectual disability, hypotonia, strabismus, coarse face, planovalgus syndrome
  • Short ulna, dysmorphism, hypotonia, intellectual disability syndrome
  • Ventricular myocardial noncompaction cardiomyopathy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Floppy baby syndrome, unspecified

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Atonia, atony, atonic
      • congenital
    • Baby
      • floppy (syndrome)
    • Floppy
      • baby syndrome (nonspecific)
    • Hypotonia, hypotonicity, hypotony
      • congenital (benign)
    • Pseudoparalysis
      • atonic, congenital
    • Syndrome
      • floppy
        • baby

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL013
Other specified and unspecified perinatal conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cystinuria

    an inherited disorder due to defective reabsorption of cystine and other basic amino acids by the proximal renal tubules. this form of aminoaciduria is characterized by the abnormally high urinary levels of cystine; lysine; arginine; and ornithine. mutations involve the amino acid transport protein gene slc3a1.

  • Combined Methylmalonic Aciduria and Homocystinuria|Combined methylmalonic acidemia and homocystinuria due to defects in adenosylcobalamin and methylcobalamin synthesis

    a genetically heterogeneous disorder of cobalamin (cbl; vitamin b12) metabolism due to loss of function mutations in the enzymes that synthesize the coenzymes adenosylcobalamin (adocbl) and methylcobalamin (mecbl). this is a subtype of methylmalonic acidemia that includes complementation groups cblc, cbld, cblf, cblj, cbll and cblx.

  • Benign Congenital Hypotonia

    mild hypotonia that usually appears early in infancy and has a favorable outcome. it is not a manifestation of another disorder that may cause hypotonia (e.g., cerebral palsy or muscular dystrophy).

  • Arakawa Syndrome II|Arakawa's Syndrome 2|Arakawa's Syndrome II|Homocystinuria-Megaloblastic Anemia, cblG Complementation Type|Methionine Synthase Deficiency|Methylcobalamin Deficiency, cblG Type|Tetrahydrofolate Methyltransferase Deficiency|Tetrahydrofolate Methyltransferase Deficiency

    a rare autosomal dominant inherited metabolic disorder characterized by deficiency of the enzyme tetrahydrofolate-methyltransferase. it results in the abnormal metabolism of methylcobalamin. signs and symptoms include mental retardation, megaloblastic anemia, hypotonia, epilepsy, and hepatosplenomegaly.

  • Cystinuria

    an autosomal recessive inherited metabolic disorder caused by mutations in the slc3a1 and slc7a9 genes. it is characterized by deficient re-absorption of cystine in the proximal tubules of the kidney. it results in the formation of stones in the kidney, ureter, and urinary bladder.

  • Homocystinuria

    an autosomal recessive inherited metabolic disorder caused by mutations in the cbs, mthfr, mtr, and mtrr genes. it is characterized by abnormalities in the methionine metabolism and is associated with deficiency of cystathionine synthase. it results in the accumulation of homocysteine in the serum. it may affect the cardiovascular, musculoskeletal and the central nervous systems.

  • Homocystinuria-Megaloblastic Anemia, cblE Complementation Type|HMAE|Methylcobalamin Deficiency, cblE Type

    an autosomal recessive condition caused by mutation(s) in the mtrr gene, encoding methionine synthase reductase. it is characterized by homocystinuria and megaloblastic anemia.

  • Methylmalonic Aciduria and Homocystinuria Type D Protein, Mitochondrial|C2orf25 Protein|MMADHC|Methylmalonic Aciduria, cblD Type, And Homocystinuria Protein|Uncharacterized Protein C2orf25, Mitochondrial

    methylmalonic aciduria and homocystinuria type d protein, mitochondrial (296 aa, ~33 kda) is encoded by the human mmadhc gene. this protein plays a role in vitamin metabolism.

  • Methylmalonic Aciduria and Homocystinuria, cblC Type

    an autosomal recessive form of combined methylmalonic aciduria and homocystinuria, caused by mutation(s) in the mmachc gene, encoding methylmalonic aciduria and homocystinuria type c protein.

  • Methylmalonic Aciduria and Homocystinuria, cblD Type|MAHCD

    an autosomal recessive form of combined methylmalonic aciduria and homocystinuria, caused by mutation(s) in the mmadhc gene, encoding cobalamin trafficking protein cbld.

  • Methylmalonic Aciduria and Homocystinuria, cblF Type|MAHCF

    an autosomal recessive form of combined methylmalonic aciduria and homocystinuria, caused by mutation(s) in the lmbrd1 gene, encoding lysosomal cobalamin transport escort protein lmbd1.

  • Methylmalonic Aciduria and Homocystinuria, cblJ Type|MAHCJ

    an autosomal recessive form of combined methylmalonic aciduria and homocystinuria, caused by mutation(s) in the abcd4 gene, encoding lysosomal cobalamin transporter abcd4.

  • MMADHC Gene|MMADHC|MMADHC|Methylmalonic Aciduria (Cobalamin Deficiency) cblD Type, with Homocystinuria Gene

    this gene is involved in vitamin metabolism.

  • MMADHC wt Allele|C2orf25|CL25022|Chromosome 2 Open Reading Frame 25 Gene|HSPC161|Methylmalonic Aciduria (Cobalamin Deficiency) cblD Type, with Homocystinuria wt Allele|Methylmalonic Aciduria, cblD Type, and Homocystinuria Gene|My011|cblD

    human mmadhc wild-type allele is located in the vicinity of 2q23.2 and is approximately 18 kb in length. this allele, which encodes methylmalonic aciduria and homocystinuria type d protein, mitochondrial, plays a role in the mediation of vitamin b12 metabolism. mutation of the gene is associated with some cases of homocystinuria, and methylmalonic aciduria.

  • Cyanocobalamin Reductase / Alkylcobalamin Dealkylase|Alkylcobalamin:Glutathione S-Alkyltransferase|CblC|Cyanocobalamin Reductase (Cyanide-Eliminating)|EC 1.16.1.6|EC 2.5.1.15|MMACHC|Methylmalonic Aciduria and Homocystinuria Type C Protein

    cyanocobalamin reductase / alkylcobalamin dealkylase (282 aa, ~32 kda) is encoded by the human mmachc gene. this protein is involved in cobalamin transport and the decyanation of cyanocob(iii)alamin (cyanocobalamin, cncbl) to yield cob(ii)alamin and cyanide and the dealkylation of alkylcob(iii)alamins using a thiolate of glutathione to generate cob(i)alamin and the corresponding glutathione thioether.

  • MMACHC wt Allele|DKFZP564I122|Metabolism of Cobalamin Associated C wt Allele|Methylmalonic Aciduria (Cobalamin Deficiency) cblC Type, with Homocystinuria Gene|cblC

    human mmachc wild-type allele is located in the vicinity of 1p34.1 and is approximately 13 kb in length. this allele, which encodes cyanocobalamin reductase / alkylcobalamin dealkylase protein, plays a role in cobalamin transport and the conversion of cyanocobalamin and alkylcobalamin to cobalamin. mutation of the gene is associated with methylmalonic aciduria and homocystinuria cblc type.

Patient EducationClinical

Muscle Disorders

Your muscles help you move and help your body work. Different types of muscles have different jobs. There are many problems that can affect muscles. Muscle disorders can cause weakness, pain or even paralysis.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert P94.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
779.89 Perinatal condition NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About P94.2Overview

Is P94.2 (Disorders of muscle tone of newborn) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital hypotonia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of P94.2?

Under the General Equivalence Mappings, congenital hypotonia converts to ICD-9-CM 779.89 (perinatal condition NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.