2026 ICD-10-CM Diagnosis Code P94.0Transient neonatal myasthenia gravis

ICD-10-CM Codes›P00–P96›P90-P96›P94

ICD-10-CM P94.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

P94.0 is a billable ICD-10-CM diagnosis code for transient neonatal myasthenia gravis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 791, 793. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 44 closely related codes. Coders also document this condition as myasthenia gravis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified perinatal conditions.

Code Identity

ICD-10-CM Code
P94.0
Billable Status
Yes — Valid for Submission
Code Describes
Transient neonatal myasthenia gravis
Short Description
Transient neonatal myasthenia gravis
Same as the full description in the CMS dataset.
Parent Code
P94
Disorders of muscle tone of newborn

Code Classification

ChapterP00–P96Certain conditions originating in the perinatal period
SectionP90-P96Other disorders originating in the perinatal period
CategoryP94Disorders of muscle tone of newborn
This CodeP94.0Transient neonatal myasthenia gravis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Myasthenia gravis
  • Neonatal myasthenia gravis
  • Neonatal neuromuscular disorder
  • Transient neonatal myasthenia gravis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • myasthenia gravis G70.0

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL013
Other specified and unspecified perinatal conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Myasthenia Gravis

    a disorder of neuromuscular transmission characterized by fatigable weakness of cranial and skeletal muscles with elevated titers of acetylcholine receptors or muscle-specific receptor tyrosine kinase (musk) autoantibodies. clinical manifestations may include ocular muscle weakness (fluctuating, asymmetric, external ophthalmoplegia; diplopia; ptosis; and weakness of eye closure) and extraocular fatigable weakness of facial, bulbar, respiratory, and proximal limb muscles. the disease may remain limited to the ocular muscles (ocular myasthenia). thymoma is commonly associated with this condition.

  • Myasthenia Gravis, Autoimmune, Experimental

    any autoimmune animal disease model used in the study of myasthenia gravis. injection with purified neuromuscular junction acetylcholine receptor (achr) (see receptors, cholinergic) components results in a myasthenic syndrome that has acute and chronic phases. the motor endplate pathology, loss of acetylcholine receptors, presence of circulating anti-achr antibodies, and electrophysiologic changes make this condition virtually identical to human myasthenia gravis. passive transfer of achr antibodies or lymphocytes from afflicted animals to normals induces passive transfer experimental autoimmune myasthenia gravis. (from joynt, clinical neurology, 1997, ch 54, p3)

  • Myasthenia Gravis, Neonatal

    a disorder of neuromuscular transmission that occurs in a minority of newborns born to women with myasthenia gravis. clinical features are usually present at birth or develop in the first 3 days of life and consist of hypotonia and impaired respiratory, suck, and swallowing abilities. this condition is associated with the passive transfer of acetylcholine receptor antibodies through the placenta. in the majority of infants the myasthenic weakness resolves (i.e., transient neonatal myasthenia gravis) although this disorder may rarely continue beyond the neonatal period (i.e., persistent neonatal myasthenia gravis). (from menkes, textbook of child neurology, 5th ed, p823; neurology 1997 jan;48(1):50-4)

  • Myasthenic Syndromes, Congenital

    a heterogeneous group of disorders characterized by a congenital defect in neuromuscular transmission at the neuromuscular junction. this includes presynaptic, synaptic, and postsynaptic disorders (that are not of autoimmune origin). the majority of these diseases are caused by mutations of various subunits of the nicotinic acetylcholine receptor (receptors, nicotinic) on the postsynaptic surface of the junction. (from arch neurol 1999 feb;56(2):163-7)

  • Transient Neonatal Myasthenia Gravis

    a condition characterized as a temporary autoimmune neuromuscular disease leading to fluctuating muscle weakness and fatigue in a newborn infant.

Patient EducationClinical

Myasthenia Gravis

Myasthenia gravis, sometimes called MG, is a chronic (long-lasting) disease that causes weakness in your voluntary muscles. The voluntary muscles are the ones that you can control. They include the muscles you use for:

The full article covers:

  • What is myasthenia gravis?
  • What causes myasthenia gravis?
  • Who is more likely to develop myasthenia gravis?
  • What are the symptoms of myasthenia gravis?
  • How is myasthenia gravis diagnosed?
  • What are the treatments for myasthenia gravis?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert P94.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
775.2 Neonat myasthenia gravis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About P94.0Overview

What is the ICD-10 code for transient neonatal myasthenia gravis?

The ICD-10-CM code for transient neonatal myasthenia gravis is P94.0 (sometimes written as P940). It is billable on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Is P94.0 (Disorders of muscle tone of newborn) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report transient neonatal myasthenia gravis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does P94.0 group to?

When transient neonatal myasthenia gravis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 791, 793, with relative weights from 4.0590 to 4.1696 depending on complications. Higher weights mean higher Medicare reimbursement.

Is P94.0 a CC or MCC?

CMS lists P94.0 as a CC (complication or comorbidity) for FY 2026. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 44 closely related codes in its exclusion list.

What is the ICD-9 equivalent of P94.0?

Under the General Equivalence Mappings, transient neonatal myasthenia gravis converts to ICD-9-CM 775.2 (neonat myasthenia gravis). The mapping is approximate, so confirm the match fits the documentation.