2027 ICD-10-CM Diagnosis Code N90.61Childhood asymmetric labium majus enlargement

ICD-10-CM Codes›N00–N99›N80-N98›N90

ICD-10-CM N90.61
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

N90.61 is a billable ICD-10-CM diagnosis code for childhood asymmetric labium majus enlargement. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 742 through 743, 760 through 761. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified female genital disorders.

Code Identity

ICD-10-CM Code
N90.61
Billable Status
Yes — Valid for Submission
Code Describes
Childhood asymmetric labium majus enlargement
Short Description
Childhood asymmetric labium majus enlargement
Same as the full description in the CMS dataset.
Parent Code
N90.6
Hypertrophy of vulva

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN80-N98Noninflammatory disorders of female genital tract
CategoryN90Other noninflammatory disorders of vulva and perineum
This CodeN90.61Childhood asymmetric labium majus enlargement

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to N90.61: its own notes plus those printed at N90 and Chapter 14. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • CALME

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From N90 Other noninflammatory disorders of vulva and perineum applies to 16 codes
  • anogenital (venereal) warts (A63.0)
  • carcinoma in situ of vulva (D07.1)
  • condyloma acuminatum (A63.0)
  • current obstetric trauma (O70.-, O71.7-O71.8)
  • inflammation of vulva (N76.-)
  • severe dysplasia of vulva (D07.1)
  • vulvar intraepithelial neoplasm III [VIN III] (D07.1)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 14 (N00-N99) Diseases of the genitourinary system applies to 838 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR GEN025
Other specified female genital disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Vulvar Disorders

The vulva is the outer part of the female genitals. This includes the clitoris, vaginal lips, and the opening to the vagina. A vulvar disorder is a health problem that affects your vulva. These problems may cause pain, itching, or skin changes of the vulva. Treatment depends on the cause.

The full article covers:

  • What are vulvar disorders?
  • Who is more likely to develop vulvar disorders?
  • What are the symptoms of vulvar disorders?
  • How are vulvar disorders diagnosed?
  • What are the treatments for vulvar disorders?
  • Can vulvar disorders be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert N90.61 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
624.3 Hypertrophy of labia
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement N90.61 replaces the following previously assigned code(s):

  • N90.6 - Hypertrophy of vulva
FY 2019AddedAdded to the ICD-10-CM code setEffective October 1, 2018.
FY 2020–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About N90.61Overview

What is the ICD-10 code for childhood asymmetric labium majus enlargement?

The ICD-10-CM code for childhood asymmetric labium majus enlargement is N90.61 (sometimes written as N9061). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is N90.61 (Hypertrophy of vulva) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report childhood asymmetric labium majus enlargement on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does N90.61 group to?

When childhood asymmetric labium majus enlargement is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 743, 760, 761, with relative weights from 0.7039 to 1.8448 depending on complications. Higher weights mean higher Medicare reimbursement.

Can N90.61 be reported with A63.0?

Not as a rule. The Excludes1 note at N90, which applies to N90.61, lists "anogenital (venereal) warts (A63.0)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of N90.61?

Under the General Equivalence Mappings, childhood asymmetric labium majus enlargement converts to ICD-9-CM 624.3 (hypertrophy of labia). The mapping is approximate, so confirm the match fits the documentation.