2026 ICD-10-CM Diagnosis Code L41.0Pityriasis lichenoides et varioliformis acuta

ICD-10-CM Codes›L00–L99›L40-L45›L41

ICD-10-CM L41.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

L41.0 is a billable ICD-10-CM diagnosis code for pityriasis lichenoides et varioliformis acuta. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 595 through 596. Coders also document this condition as acute lichenoid pityriasis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

Code Identity

ICD-10-CM Code
L41.0
Billable Status
Yes — Valid for Submission
Code Describes
Pityriasis lichenoides et varioliformis acuta
Short Description
Pityriasis lichenoides et varioliformis acuta
Same as the full description in the CMS dataset.
Parent Code
L41
Parapsoriasis

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL40-L45Papulosquamous disorders
CategoryL41Parapsoriasis
This CodeL41.0Pityriasis lichenoides et varioliformis acuta

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acute lichenoid pityriasis
  • Febrile ulceronecrotic pityriasis lichenoides acuta
  • Parapsoriasis
  • Parapsoriasis varioliformis
  • Pityriasis lichenoides

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Mucha-Habermann disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Mucha-Habermann disease
    • Parakeratosis
      • variegata
    • Parapsoriasis
      • varioliformis (acuta)
    • Pityriasis(capitis)
      • lichenoides
    • Pityriasis(capitis)
      • lichenoides
        • et varioliformis (acuta)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Pityriasis Lichenoides

    a subgroup of parapsoriasis itself divided into acute and chronic forms. the acute form is characterized by the abrupt onset of a generalized, reddish-brown, maculopapular eruption. lesions may be vesicular, hemorrhagic, crusted, or necrotic. histologically the disease is characterized by epidermal necrolysis. the chronic form shows milder skin changes with necrosis.

  • Parapsoriasis

    the term applied to a group of relatively uncommon inflammatory, maculopapular, scaly eruptions of unknown etiology and resistant to conventional treatment. eruptions are both psoriatic and lichenoid in appearance, but the diseases are distinct from psoriasis, lichen planus, or other recognized dermatoses. proposed nomenclature divides parapsoriasis into two distinct subgroups, pityriasis lichenoides and parapsoriasis en plaques (small- and large-plaque parapsoriasis).

  • Pityriasis Lichenoides

    a rare cutaneous disorder of unknown etiology that can present either as an acute condition, with multiple papular lesions which become vesicular and necrotic (pityriasis lichenoides et varioliformis acuta) or chronic, with small, scaling papules (pityriasis lichenoides chronica).

  • Pityriasis Lichenoides et Varioliformis Acuta|PLEVA

    a rare skin disorder of unknown etiology that is considered to be a more severe form of pityriasis lichenoides. it is characterized by itchy, burning papular lesions which form open sores with red-brown crusts. low grade fever, headache, malaise, and arthralgias may occasionally precede or accompany the skin findings.

  • Large Plaque Parapsoriasis|Parapsoriasis en Plaques

    a variant of parapsoriasis in which the plaques are large.

  • Parapsoriasis

    an inflammatory skin disorder of unknown etiology characterized by papules and plaques or scaly patches resembling psoriasis.

  • Parapsoriasis Lichenoides|Parapsoriasis Variegata|Poikiloderma Atrophicans Vasculare|Poikilodermic Parapsoriasis|Retiform Parapsoriasis

    a rare condition that stimulated chronic radiodermatitis. it is considered a variant of mycosis fungoides.

  • Small Plaque Parapsoriasis

    a variant of parapsoriasis in which the plaques are small.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L41.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
696.2 Parapsoriasis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About L41.0Overview

Is L41.0 (Parapsoriasis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pityriasis lichenoides et varioliformis acuta on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does L41.0 group to?

When pityriasis lichenoides et varioliformis acuta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 595, 596, with relative weights from 1.0825 to 2.1207 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L41.0?

Under the General Equivalence Mappings, pityriasis lichenoides et varioliformis acuta converts to ICD-9-CM 696.2 (parapsoriasis). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.