2027 ICD-10-CM Diagnosis Code L41.0Pityriasis lichenoides et varioliformis acuta

ICD-10-CM Codes›L00–L99›L40-L45›L41

ICD-10-CM L41.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

L41.0 is a billable ICD-10-CM diagnosis code for pityriasis lichenoides et varioliformis acuta. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 595 through 596. Coders also document this condition as acute lichenoid pityriasis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

L41.0 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 316 for payment year 2027.

Code Identity

ICD-10-CM Code
L41.0
Billable Status
Yes — Valid for Submission
Code Describes
Pityriasis lichenoides et varioliformis acuta
Short Description
Pityriasis lichenoides et varioliformis acuta
Same as the full description in the CMS dataset.
Parent Code
L41
Parapsoriasis

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL40-L45Papulosquamous disorders
CategoryL41Parapsoriasis
This CodeL41.0Pityriasis lichenoides et varioliformis acuta

Medicare Risk Adjustment (HCC)Billing

L41.0 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model, but it maps to payment categories in the other CMS models shown below.

CMS-HCC V28 (Medicare Advantage Payment Model)
Not mapped
no payment category in the model that pays 100% of MA risk scores
Prior Model (CMS-HCC V24)
Not mapped under V24
this diagnosis newly risk-adjusts under the V28 model
Part D (RxHCC)
RxHCC 316 — Psoriasis, Except with Arthropathy
also risk-adjusts in the Part D prescription drug model (V08)

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acute lichenoid pityriasis
  • Febrile ulceronecrotic pityriasis lichenoides acuta
  • Parapsoriasis
  • Parapsoriasis varioliformis
  • Pityriasis lichenoides

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to L41.0: its own notes plus those printed at L41 and Chapter 12. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Mucha-Habermann disease

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From L41 Parapsoriasis applies to 7 codes
  • poikiloderma vasculare atrophicans (L94.5)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue applies to 1,001 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • lipomelanotic reticulosis (I89.8)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • viral warts (B07.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Pityriasis Lichenoides et Varioliformis Acuta

    a rare skin disorder of unknown etiology that is considered to be a more severe form of pityriasis lichenoides. it is characterized by itchy, burning papular lesions which form open sores with red-brown crusts. low grade fever, headache, malaise, and arthralgias may occasionally precede or accompany the skin findings.

  • Parapsoriasis

    the term applied to a group of relatively uncommon inflammatory, maculopapular, scaly eruptions of unknown etiology and resistant to conventional treatment. eruptions are both psoriatic and lichenoid in appearance, but the diseases are distinct from psoriasis, lichen planus, or other recognized dermatoses. proposed nomenclature divides parapsoriasis into two distinct subgroups, pityriasis lichenoides and parapsoriasis en plaques (small- and large-plaque parapsoriasis).

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L41.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
696.2 Parapsoriasis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About L41.0Overview

What is the ICD-10 code for pityriasis lichenoides et varioliformis acuta?

The ICD-10-CM code for pityriasis lichenoides et varioliformis acuta is L41.0 (sometimes written as L410). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is L41.0 (Parapsoriasis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pityriasis lichenoides et varioliformis acuta on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does L41.0 group to?

When pityriasis lichenoides et varioliformis acuta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 596, 595, with relative weights from 1.1067 to 2.0230 depending on complications. Higher weights mean higher Medicare reimbursement.

Can L41.0 be reported with L94.5?

Not as a rule. The Excludes1 note at L41, which applies to L41.0, lists "poikiloderma vasculare atrophicans (L94.5)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of L41.0?

Under the General Equivalence Mappings, pityriasis lichenoides et varioliformis acuta converts to ICD-9-CM 696.2 (parapsoriasis). The mapping is approximate, so confirm the match fits the documentation.

Does L41.0 risk-adjust for Medicare Advantage payment?

Not for Medicare Advantage: L41.0 maps to no category in the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 316 (Psoriasis, Except with Arthropathy).