2026 ICD-10-CM Diagnosis Code I27.29Other secondary pulmonary hypertension

ICD-10-CM Codes›I00–I99›I26-I28›I27

ICD-10-CM I27.29
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I27.29 is a billable ICD-10-CM diagnosis code for other secondary pulmonary hypertension. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 314 through 316. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Pulmonary heart disease.

This medical diagnosis code is frequently used in Cardiology medical specialties to designate conditions such hypertension.

Code Identity

ICD-10-CM Code
I27.29
Billable Status
Yes — Valid for Submission
Code Describes
Other secondary pulmonary hypertension
Short Description
Other secondary pulmonary hypertension
Same as the full description in the CMS dataset.
Parent Code
I27.2
Other secondary pulmonary hypertension

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI26-I28Pulmonary heart disease and diseases of pulmonary circulation
CategoryI27Other pulmonary heart diseases
This CodeI27.29Other secondary pulmonary hypertension

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Associated pulmonary arterial hypertension
  • Effects of air pressure
  • Facultative pulmonary hypertension with shunt at atrial level
  • Large vessel pulmonary hypertension
  • Post-arteritic pulmonary hypertension
  • Postcapillary pulmonary hypertension
  • Pulmonary arterial hypertension associated with portal hypertension
  • Pulmonary hypertension associated with chronic underventilation
  • Pulmonary hypertension caused by low air pressure due to chronic exposure to high altitude
  • Pulmonary hypertension due to alveolar hypoventilation disorder
  • Pulmonary hypertension due to developmental abnormality
  • Pulmonary hypertension due to diastolic systemic ventricular dysfunction
  • Pulmonary hypertension due to hematological disorder
  • Pulmonary hypertension due to left heart disease
  • Pulmonary hypertension due to left-sided valvular heart disease
  • Pulmonary hypertension due to lung disease and/or hypoxia
  • Pulmonary hypertension due to myeloproliferative disorder
  • Pulmonary hypertension due to post-splenectomy hematological disorder
  • Pulmonary hypertension due to sleep-disordered breathing
  • Pulmonary hypertension due to vasculitis
  • Pulmonary hypertension in Langerhans cell histiocytosis
  • Pulmonary hypertension in neurofibromatosis
  • Pulmonary hypertension in sarcoidosis
  • Pulmonary hypertension in systemic disorder
  • Pulmonary hypertension secondary to raised pulmonary vascular resistance
  • Pulmonary hypertension with extreme obesity
  • Pulmonary hypertension with occult mitral stenosis
  • Pulmonary veno-occlusive disease
  • Pulmonary venous hypertension as complication of procedure
  • Pulmonary venous hypertension due to compression of pulmonary great vein
  • Pulmonary venous hypertension due to compression of pulmonary great vein by lymphadenopathy
  • Pulmonary venous hypertension due to compression of pulmonary great vein by neoplasm
  • Pulmonary venous hypertension due to compression of pulmonary great vein by sclerosing mediastinitis
  • Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
  • Small vessel pulmonary hypertension
  • Solitary pulmonary hypertension

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Group 5 pulmonary hypertension
  • Pulmonary hypertension with unclear multifactorial mechanisms
  • Pulmonary hypertension due to hematologic disorders
  • Pulmonary hypertension due to metabolic disorders
  • Pulmonary hypertension due to other systemic disorders

Code Also

  • other associated disorders, if known, such as:
  • chronic myeloid leukemia C92.10 C92.22
  • essential thrombocythemia D47.3
  • Gaucher disease E75.22
  • hypertensive chronic kidney disease with end stage renal disease I12.0 I13.11 I13.2
  • hyperthyroidism E05
  • hypothyroidism E00 E03
  • polycythemia vera D45
  • sarcoidosis D86

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • with
          • cor pulmonale (chronic)
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • with
          • right heart ventricular strain/failure
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • with
          • unclear multifactorial mechanisms
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • due to
          • hematologic disorders
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • due to
          • metabolic disorders
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • due to
          • specified systemic disorders NEC
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • group 5
    • Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)
      • pulmonary
        • secondary
          • specified NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR014
Pulmonary heart disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Pulmonary Hypertension

Pulmonary hypertension, sometimes called PH, is a serious condition that affects the blood vessels in the lungs. It develops when the blood pressure in your lungs is higher than normal.

The full article covers:

  • What is pulmonary hypertension?
  • What causes pulmonary hypertension?
  • Who is more likely to develop pulmonary hypertension?
  • What are the symptoms of pulmonary hypertension?
  • What other problems can pulmonary hypertension cause?
  • How is pulmonary hypertension diagnosed?
  • What are the treatments for pulmonary hypertension?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I27.29 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
416.8 Chr pulmon heart dis NEC
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement I27.29 replaces the following previously assigned code(s):

  • I27.2 - Other secondary pulmonary hypertension
FY 2018AddedAdded to the ICD-10-CM code setEffective October 1, 2017.
FY 2019–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I27.29Overview

Is I27.29 (Other secondary pulmonary hypertension) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other secondary pulmonary hypertension on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does I27.29 group to?

When other secondary pulmonary hypertension is the principal diagnosis on an inpatient stay, it groups to MS-DRG 314, 315, 316, with relative weights from 0.6821 to 2.0852 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I27.29?

Under the General Equivalence Mappings, other secondary pulmonary hypertension converts to ICD-9-CM 416.8 (chr pulmon heart dis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.