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  6. 2026 ICD-10-CM Code I27.841

2026 ICD-10-CM Diagnosis Code I27.841

Fontan-associated lymphatic dysfunction

ICD-10-CM Code:
I27.841
ICD-10 Code for:
Fontan-associated lymphatic dysfunction
Is Billable?
Yes - Valid for Submission
Code Navigator:

I27.841 is a billable diagnosis code used to specify a medical diagnosis of fontan-associated lymphatic dysfunction. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2025 through September 30, 2026.

Code Classification

  • Diseases of the circulatory system
    I00–I99
    • Pulmonary heart disease and diseases of pulmonary circulation
      I26-I28
      • Other pulmonary heart diseases
        I27

New 2026 ICD-10-CM Code

I27.841 is new to ICD-10-CM code set for the FY 2026, effective October 1, 2025. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2025. This is a new and revised code for the FY 2026 (October 1, 2025 - September 30, 2026).

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Code Also

Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • associated conditions such as:
  • chylothorax J94.0
  • Fontan associated protein-losing enteropathy K90.89
  • plastic obstructive bronchitis J44.89

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Index of External Cause of Injuries

References found for this diagnosis code in the External Cause of Injuries Index:

    • Circulation
      • Fontan related
        • with
          • Fontan-associated lymphatic dysfunction
    • Dysfunction
      • lymphatic
        • Fontan-associated

Replacement Code

I27841 replaces the following previously assigned ICD-10-CM code(s):

  • I27.89 - Other specified pulmonary heart diseases

Code History

  • FY 2026 - Code Added, effective from 10/1/2025 through 9/30/2026