2026 ICD-10-CM Diagnosis Code H57.01Argyll Robertson pupil, atypical

ICD-10-CM Codes›H00–H59›H55-H57›H57

ICD-10-CM H57.01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H57.01 is a billable ICD-10-CM diagnosis code for argyll Robertson pupil, atypical. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as abnormal pupil reaction. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified eye disorders.

Code Identity

ICD-10-CM Code
H57.01
Billable Status
Yes — Valid for Submission
Code Describes
Argyll Robertson pupil, atypical
Short Description
Argyll Robertson pupil, atypical
Same as the full description in the CMS dataset.
Parent Code
H57.0
Anomalies of pupillary function

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH55-H57Other disorders of eye and adnexa
CategoryH57Other disorders of eye and adnexa
This CodeH57.01Argyll Robertson pupil, atypical

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal pupil reaction
  • Argyll-Robertson pupil
  • Atypical Argyll-Robertson pupil
  • Light near dissociated pupil
  • Non-syphilitic Argyll Robertson pupil

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • syphilitic Argyll Robertson pupil A52.19

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • pupil
        • function
          • Argyll Robertson pupil

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE012
Other specified eye disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Eye Diseases

Even if your eyes feel healthy, you could have a problem and not know it. That's why regular eye exams are so important. Refractive errors are the most common type of vision problem that makes it hard to see clearly. But some eye conditions or diseases don't have any symptoms and can lead to a permanent loss of vision.

The full article covers:

  • What diseases can affect the eye?
  • What are the symptoms of eye diseases?
  • Who is more likely to develop eye diseases?
  • What are the treatments for eye diseases?
  • Can eye diseases be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H57.01 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
379.45 Argyll robertson pupil
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H57.01Overview

Is H57.01 (Anomalies of pupillary function) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report argyll Robertson pupil, atypical on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of H57.01?

Under the General Equivalence Mappings, argyll Robertson pupil, atypical converts to ICD-9-CM 379.45 (argyll robertson pupil). The mapping is a direct match.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.