2026 ICD-10-CM Diagnosis Code H31.22Choroidal dystrophy (central areolar) (generalized) (peripapillary)

ICD-10-CM CodesH00–H59H30-H36H31

ICD-10-CM H31.22
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H31.22 is a billable ICD-10-CM diagnosis code for choroidal dystrophy (central areolar) (generalized) (peripapillary). It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Retinal and vitreous conditions.

Code Identity

ICD-10-CM Code
H31.22
Billable Status
Yes — Valid for Submission
Code Describes
Choroidal dystrophy (central areolar) (generalized) (peripapillary)
Short Description
Choroidal dystrophy (central areolar) (peripapillary)
Parent Code
Hereditary choroidal dystrophy

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH30-H36Disorders of choroid and retina
CategoryH31Other disorders of choroid
This CodeH31.22Choroidal dystrophy (central areolar) (generalized) (peripapillary)

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Central areolar choroidal sclerosis
  • Hereditary choroidal dystrophy
  • Partial central choroid dystrophy
  • Partial generalized choroidal dystrophy
  • Peripapillary atrophy
  • Peripapillary choroidal dystrophy
  • Peripapillary choroidal sclerosis
  • Total generalized choroidal dystrophy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dystrophy, dystrophia
      • choroid (hereditary)
        • central areolar

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE005
Retinal and vitreous conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Eye Diseases

Even if your eyes feel healthy, you could have a problem and not know it. That's why regular eye exams are so important. Refractive errors are the most common type of vision problem that makes it hard to see clearly. But some eye conditions or diseases don't have any symptoms and can lead to a permanent loss of vision.

The full article covers:

  • What diseases can affect the eye?
  • What are the symptoms of eye diseases?
  • Who is more likely to develop eye diseases?
  • What are the treatments for eye diseases?
  • Can eye diseases be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H31.22 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
363.53 Part cent choroid dystr
Approximate The match is approximate rather than exact.
ICD-9-CM
363.54 Tot cent choroid atrophy
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H31.22Overview

Is H31.22 (Hereditary choroidal dystrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report choroidal dystrophy (central areolar) (generalized) (peripapillary) on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does H31.22 group to?

When choroidal dystrophy (central areolar) (generalized) (peripapillary) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H31.22?

Under the General Equivalence Mappings, choroidal dystrophy (central areolar) (generalized) (peripapillary) converts to ICD-9-CM 363.53 (part cent choroid dystr) and 363.54 (tot cent choroid atrophy). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.