2026 ICD-10-CM Diagnosis Code H30.90Unspecified chorioretinal inflammation, unspecified eye

AHRQ’s CCSR groups this code into broader clinical categories.

• Choroiditis

  inflammation of the choroid.

• Multifocal Choroiditis

  a multifocal uveitis syndrome involving the retinal pigment epithelium and capillary layer of the choroid. it is characterized by chronic uveitis and multiple choroid lesions referred to as white dots, blurry vision, floaters, sensitivity to light, blind spots, and eye discomfort.

• White Dot Syndromes

  a group of idiopathic multifocal posterior uveitis syndromes involving the choroid; retinal pigment epithelium; and retina. they are characterized by multiple lesions of hypoautofluorescent dots in the fundus oculi and reduced visual acuity. several entities including birdshot chorioretinopathy are hla-a antigens serotype a29 positive.

• Cytomegalovirus Retinitis

  infection of the retina by cytomegalovirus characterized by retinal necrosis, hemorrhage, vessel sheathing, and retinal edema. cytomegalovirus retinitis is a major opportunistic infection in aids patients and can cause blindness.

• Foveomacular Retinitis

  a photochemical injury to retina tissues, usually at the retinal pigment epithelium. it is commonly associated with sungazing, eclipse viewing, welding, or using a laser pointer without proper eye protection resulting in subjective visual disturbances (e.g., floaters) and reduced visual acuity.

• Retinitis

  inflammation of the retina. it is rarely limited to the retina, but is commonly associated with diseases of the choroid (chorioretinitis) and of the optic disk (neuroretinitis).

• Retinitis Pigmentosa

  hereditary, progressive degeneration of the retina due to death of rod photoreceptors initially and subsequent death of cone photoreceptors. it is characterized by deposition of pigment in the retina.

• Usher Syndromes

  autosomal recessive hereditary disorders characterized by congenital sensorineural hearing loss and retinitis pigmentosa. genetically and symptomatically heterogeneous, clinical classes include type i, type ii, and type iii. their severity, age of onset of retinitis pigmentosa and the degree of vestibular dysfunction are variable.

• Birdshot Chorioretinopathy

  a form of chorioretinitis characterized by multiple small, cream-colored lesions, symmetrically scattered mainly around the optic disk. these lesions are the most distinctive sign and often appear at the level of the retinal pigment epithelium but, on occasion, suggest an even deeper infiltration and may ultimately lead to visual loss. an association with hla-a29 antigen (see hla-a antigens) has been observed in nearly all patients.

• Chorioretinitis

  inflammation of the choroid in which the sensory retina becomes edematous and opaque. the inflammatory cells and exudate may burst through the sensory retina to cloud the vitreous body.

• Neurodegeneration with Brain Iron Accumulation 1|Brain Iron Accumulation Type I Syndrome|HARP Syndrome|Hallervorden-Spatz Disease|Hallervorden-Spatz Syndrome|Hallervorden-Spatz disease|Hypoprebetalipoproteinemia, Acanthocytosis, Retinitis Pigmentosa, and Pallidal Degeneration Syndrome|NBIA 1|NBIA1|Neuroaxonal Dystrophy, Late Infantile|PKAN Neuroaxonal Dystrophy, Juvenile-Onset|Pantothenate Kinase-Associated Neurodegeneration|Pigmentary pallidal degeneration

  a rare autosomal recessive inherited disorder caused by mutations in the pank2 gene. it is characterized by abnormal accumulation of iron in the basal ganglia. signs and symptoms include progressive motor disturbances, muscle spasm and rigidity, dysarthria, mental deterioration, and behavioral changes.

• Pantothenate Kinase-Associated Neurodegeneration|HARP Syndrome|Hallervorden-Spatz Disease|Hypoprebetalipoproteinemia, Acanthocytosis, Retinitis Pigmentosa, and Pallidal Degeneration Syndrome|NBIA1|Neuroaxonal Dystrophy, Late Infantile|PKAN Neuroaxonal Dystrophy, Juvenile-Onset|Pigmentary pallidal degeneration

  a rare autosomal recessive inherited disorder caused by mutations in the pank2 gene. it is characterized by abnormal accumulation of iron in the basal ganglia. signs and symptoms include progressive motor disturbances, muscle spasm and rigidity, dysarthria, mental deterioration, and behavioral changes.

• Solar Retinopathy|Photic Retinopathy|Solar Retinitis|Solar retinitis

  damage to the retina caused by bright light, commonly sunlight.

• Ceramide Kinase-like Protein|Retinitis Pigmentosa 26 (Autosomal Recessive)

  ceramide kinase-like protein (558 aa, ~63 kda) is encoded by the human cerkl gene. this protein plays a role in protecting cells from apoptosis in oxidative stress conditions.

• Chorioretinitis

  inflammation of the distal posterior uveal tract (choroid) and its structural and vascular attachments to the retina. it is usually caused by infection and though rare, it is clinically significant due to its most serious sequela: loss of vision.

• Cytomegaloviral Retinitis|Cytomegalovirus retinitis

  inflammation of the retina due to cytomegalovirus.

• EYS wt Allele|C6orf178|C6orf179|C6orf180|Chromosome 6 Open Reading Frame 178 Gene|Chromosome 6 Open Reading Frame 179 Gene|Chromosome 6 Open Reading Frame 180 Gene|EGF-Like-Domain, Multiple 10 Gene|EGF-Like-Domain, Multiple 11 Gene|EGFL10|EGFL11|Eyes Shut Homolog (Drosophila) Gene|Eyes Shut Homolog wt Allele|Eyes Shut, Drosophila, Homolog of Gene|RP25|Retinitis Pigmentosa 25 (Autosomal Recessive) Gene|SPAM|Spacemaker Gene|UNQ9424/PRO34591|bA166P24.2|bA307F22.3|bA74E24.1|dJ1018A4.2|dJ22I17.2|dJ303F19.1

  human eys wild-type allele is located in the vicinity of 6q12 and is approximately 1987 kb in length. this allele, which encodes protein eyes shut homolog, is involved in retinal function. mutation of the gene is associated with autosomal recessive retinitis pigmentosa 25.

• OFD1 wt Allele|71-7A|CXorf5|Chromosome X Open Reading Frame 5 Gene|JBTS10|MGC117039|MGC117040|Oral-Facial-Digital Syndrome 1 wt Allele|Retinitis Pigmentosa 23 (X-Linked Recessive) Gene|SGBS2

  human ofd1 wild-type allele is located in the vicinity of xp22 and is approximately 35 kb in length. this allele, which encodes oral-facial-digital syndrome 1, may be involved in the mediation of embryonic development. mutations in the gene are associated with both oral-facial-digital syndrome type i and simpson-golabi-behmel syndrome type 2.

• POLR1D wt Allele|AC19|MGC9850|POLR1C|Polymerase (RNA) I Polypeptide D, 16kDa Gene|Polymerase (RNA) I Subunit D Gene|Polymerase I, RNA, Subunit D Gene|RNA Polymerase A, 16-kD, Mouse, Homolog of Gene|RNA Polymerase I and III Subunit D wt Allele|RPA16|RPA9|RPAC2|RPC16|RPO1-3|Retinitis Pigmentosa 25 (Autosomal Recessive) Gene|TCS2

  human polr1d wild-type allele is located in the vicinity of 13q12.2 and is approximately 123 kb in length. this allele, which encodes dna-directed rna polymerases i and iii subunit rpac2 protein, is involved in rna polymerase i- and iii-dependent transcription of rrna and other small rnas. mutation of the gene is associated with treacher collins syndrome 2.

• Retinitis

  inflammation of the retina.

• Retinitis Pigmentosa

  a rare inherited retinal dystrophy disorder characterized by spots of black bone-spicule pigmentation of the retinal pigment epithelium. it is manifested with decreased vision in low light or in the night, followed by decreased peripheral vision, and, eventual decreased central vision. it may lead to blindness.

• RHO wt Allele|CSNBAD1|OPN2|Opsin 2, Rod Pigment Gene|RP4|Retinitis Pigmentosa 4, Autosomal Dominant Gene|Rhodopsin wt Allele

  human rho wild-type allele is located in the vicinity of 3q22.1 and is approximately 7 kb in length. this allele, which encodes rhodopsin protein, is involved in photoreceptor cell activity and maintenance. mutation of the gene is associated with congenital stationary night blindness, retinitis pigmentosa 4, and retinitis punctata albescens.

• RP2 Gene|RP2|RP2|Retinitis Pigmentosa 2 (X-Linked Recessive) Gene

  this gene plays a role in development.

• RP2 wt Allele|DELXp11.3|NME10|Retinitis Pigmentosa 2 (X-Linked Recessive) wt Allele|TBCCD2|XRP2

  human rp2 wild-type allele is located within xp11.4-xp11.21 and is approximately 45 kb in length. this allele, which encodes protein xrp2, plays a role in photoreceptor development. mutations in this gene are associated with x-linked mental retardation with retinitis pigmentosa.

• CERKL wt Allele|Ceramide Kinase Like wt Allele|Ceramide Kinase-like Gene|RP26|Retinitis Pigmentosa 26 (Autosomal Recessive) Gene|Retinitis Pigmentosa 26 Gene

  human cerkl wild-type allele is located in the vicinity of 2q31.3 and is approximately 144 kb in length. this allele, which encodes ceramide kinase-like protein, is involved in protecting cells from apoptosis in oxidative stress conditions.

• MT-ATP6 wt Allele|ATP Synthase 6 Gene|ATP6|ATPASE-6|ATPase-6|ATPase6|Complex V, ATP Synthase, Subunit ATPase6 Gene|MTATP6|Mitochondrially Encoded ATP Synthase Gene|Mitochondrially Encoded ATP Synthase Membrane Subunit 6 wt Allele|Mitochondrially Encoded ATP Synthase Membrane Subunit A Gene|Spicular Retinitis Pigmentosa with Dementia, Seizures, Ataxia, Proximal Muscle Weakness and Sensory Deficit Gene|Su6m

  human mt-atp6 wild-type allele is located within the circular mitochondrial (mt) chromosome and is approximately 681 bases in length. this allele, which encodes atp synthase subunit a protein, plays a role in proton-transport and atp synthesis. mutation of the gene is associated with neuropathy, ataxia, and retinitis pigmentosa (narp); leber hereditary optic neuropathy (lhon); leigh syndrome (ls); mitochondrial infantile bilateral striatal necrosis (mibsn); myopathy, lactic acidosis, and sideroblastic anemia 3 (mlasa3); adult-onset ataxia and polyneuropathy (apao); infantile hypertrophic cardiomyopathy (cmhi); and mitochondrial complex v (atp synthase) deficiency mitochondrial type 1 (mc5dm1).

• Polyneuropathy, Hearing Loss, Ataxia, Retinitis Pigmentosa, and Cataract|PHARC

  an autosomal recessive condition caused by mutation(s) in the abhd12 gene, encoding lysophosphatidylserine lipase abhd12. it is characterized by polyneuropathy, hearing loss, ataxia, retinitis pigmentosa and cataract.

Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

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