2027 ICD-10-CM Diagnosis Code D13.91Familial adenomatous polyposis

ICD-10-CM Codes›C00–D49›D10-D36›D13

ICD-10-CM D13.91
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

D13.91 is a billable ICD-10-CM diagnosis code for familial adenomatous polyposis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 393 through 395. Coders also document this condition as AXIN2-related attenuated familial adenomatous polyposis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.

Code Identity

ICD-10-CM Code
D13.91
Billable Status
Yes — Valid for Submission
Code Describes
Familial adenomatous polyposis
Short Description
Familial adenomatous polyposis
Same as the full description in the CMS dataset.
Parent Code
D13.9
Benign neoplasm of ill-defined sites within the digestive system

Code Classification

ChapterC00–D49Neoplasms
SectionD10-D36Benign neoplasms, except benign neuroendocrine tumors
CategoryD13Benign neoplasm of other and ill-defined parts of digestive system
This CodeD13.91Familial adenomatous polyposis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • AXIN2-related attenuated familial adenomatous polyposis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to D13.91: its own notes plus those printed at D13 and Chapter 2. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From D13 Benign neoplasm of other and ill-defined parts of digestive system applies to 11 codes
  • benign stromal tumors of digestive system (D21.4)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

  • associated conditions, such as:
  • benign neoplasm of colon (D12.6)
  • malignant neoplasm of colon (C18.-)

Notes

General instructions on how these codes are used.

From Chapter 2 (C00-D49) Neoplasms applies to 1,730 codes
  • Functional activity
  • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Morphology [Histology]
  • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Primary malignant neoplasms overlapping site boundaries
  • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Malignant neoplasm of ectopic tissue
  • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO073
Benign neoplasms
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Adenomatous Polyposis Coli

    a polyposis syndrome due to an autosomal dominant mutation of the apc genes (genes, apc) on chromosome 5. the syndrome is characterized by the development of hundreds of adenomatous polyps in the colon and rectum of affected individuals by early adulthood.

Patient EducationClinical

Colonic Polyps

A polyp is an extra piece of tissue that grows inside your body. Colonic polyps grow in the large intestine, or colon. Most polyps are not dangerous. However, some polyps may turn into cancer or already be cancer. To be safe, doctors remove polyps and test them.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement D13.91 replaces the following previously assigned code(s):

  • D13.9 - Benign neoplasm of ill-defined sites within the dgstv sys
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About D13.91Overview

What is the ICD-10 code for familial adenomatous polyposis?

The ICD-10-CM code for familial adenomatous polyposis is D13.91 (sometimes written as D1391). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is D13.91 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report familial adenomatous polyposis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does D13.91 group to?

When familial adenomatous polyposis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 394, 395, 393, with relative weights from 0.6379 to 1.5877 depending on complications. Higher weights mean higher Medicare reimbursement.

Can D13.91 be reported with D21.4?

Not as a rule. The Excludes1 note at D13, which applies to D13.91, lists "benign stromal tumors of digestive system (D21.4)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).