2027 ICD-10-CM Diagnosis Code K83.01Primary sclerosing cholangitis
ICD-10-CM Codes›K00–K95›K80-K87›K83
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- Risk Adjusts — HCC 68
- Chronic Condition
K83.01 is a billable ICD-10-CM diagnosis code for primary sclerosing cholangitis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 444 through 446, 791, 793. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 5 closely related codes. Coders also document this condition as cirrhosis of liver due to primary sclerosing cholangitis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Biliary tract disease.
For Medicare Advantage risk adjustment, K83.01 maps to CMS-HCC Category 68 (Cholangitis and Obstruction of Bile Duct Without Gallstones) under the V28 model, adding a risk factor of about 0.388 for a community, non-dual, aged beneficiary in payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
K83.01 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Cirrhosis of liver due to primary sclerosing cholangitis
- Primary sclerosing cholangitis
- Sclerosing cholangitis
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to K83.01: its own notes plus those printed at K83.0, K83, and Chapter 11. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name K83.01, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Primary Sclerosing Cholangitis
a chronic, autoimmune inflammatory liver disorder characterized by narrowing and scarring of the lumen of the bile ducts. it is often seen in patients with ulcerative colitis. signs and symptoms include jaundice, fatigue, and malabsorption. it may lead to cirrhosis and liver failure.Cholangitis
inflammation of the biliary ductal system (bile ducts); intrahepatic, extrahepatic, or both.
Patient EducationClinical
Bile Duct Diseases
Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Code History & ChangesHistory
Replacement K83.01 replaces the following previously assigned code(s):
- K83.0 - Cholangitis
Questions About K83.01Overview
What is the ICD-10 code for primary sclerosing cholangitis?
The ICD-10-CM code for primary sclerosing cholangitis is K83.01 (sometimes written as K8301). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is K83.01 (Cholangitis) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report primary sclerosing cholangitis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does K83.01 group to?
When primary sclerosing cholangitis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 793, 791, 444, 445, 446, with relative weights from 0.8121 to 4.2192 depending on complications. Higher weights mean higher Medicare reimbursement.
Is K83.01 a CC or MCC?
CMS lists K83.01 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 5 closely related codes in its exclusion list.
Can K83.01 be reported with K75.0?
Not as a rule. The Excludes1 note at K83.0, which applies to K83.01, lists "cholangitic liver abscess (K75.0)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What HCC is K83.01?
K83.01 (primary sclerosing cholangitis) maps to CMS-HCC Category 68 (Cholangitis and Obstruction of Bile Duct Without Gallstones), commonly written as HCC 68, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It does not map to any RxHCC in the Part D prescription drug model.
Does K83.01 risk-adjust for Medicare Advantage payment?
Yes. When documented and reported on a Medicare Advantage encounter, K83.01 adds a risk adjustment factor of about 0.388 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.085 to 0.391 depending on the payment segment). A more severe related category (HCC 62, HCC 63, and HCC 64) supersedes it when both are reported. See the full factor table on the HCC 68 category page.
