2026 ICD-10-CM Diagnosis Code K83.01Primary sclerosing cholangitis

ICD-10-CM Codes›K00–K95›K80-K87›K83

ICD-10-CM K83.01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

K83.01 is a billable ICD-10-CM diagnosis code for primary sclerosing cholangitis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 444 through 446. Coders also document this condition as cirrhosis of liver with primary sclerosing cholangitis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Biliary tract disease.

Code Identity

ICD-10-CM Code
K83.01
Billable Status
Yes — Valid for Submission
Code Describes
Primary sclerosing cholangitis
Short Description
Primary sclerosing cholangitis
Same as the full description in the CMS dataset.
Parent Code
K83.0
Cholangitis

Code Classification

ChapterK00–K95Diseases of the digestive system
SectionK80-K87Disorders of gallbladder, biliary tract and pancreas
CategoryK83Other diseases of biliary tract
This CodeK83.01Primary sclerosing cholangitis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cirrhosis of liver with primary sclerosing cholangitis
  • Primary sclerosing cholangitis
  • Sclerosing cholangitis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cholangitis(ascending) (recurrent) (secondary) (stenosing) (suppurative)
      • primary
        • sclerosing

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR DIG017
Biliary tract disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cholangitis

    inflammation of the biliary ductal system (bile ducts); intrahepatic, extrahepatic, or both.

  • Cholangitis, Sclerosing

    chronic inflammatory disease of the biliary tract. it is characterized by fibrosis and hardening of the intrahepatic and extrahepatic biliary ductal systems leading to bile duct strictures, cholestasis, and eventual biliary cirrhosis.

  • Liver Cirrhosis, Biliary

    fibrosis of the hepatic parenchyma due to obstruction of bile flow (cholestasis) in the intrahepatic or extrahepatic bile ducts (bile ducts, intrahepatic; bile ducts, extrahepatic). primary biliary cholangitis involves the destruction of small intra-hepatic bile ducts and decreased bile secretion. secondary biliary cholangitis is produced by prolonged obstruction of large intrahepatic or extrahepatic bile ducts from a variety of causes.

Patient EducationClinical

Bile Duct Diseases

Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement K83.01 replaces the following previously assigned code(s):

  • K83.0 - Cholangitis
FY 2019AddedAdded to the ICD-10-CM code setEffective October 1, 2018.
FY 2020–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About K83.01Overview

Is K83.01 (Cholangitis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report primary sclerosing cholangitis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does K83.01 group to?

When primary sclerosing cholangitis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 444, 445, 446, with relative weights from 0.8273 to 1.6709 depending on complications. Higher weights mean higher Medicare reimbursement.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.