Other diseases of biliary tract (K83) ICD-10-CM
The K83 code range covers other diseases of biliary tract with 11 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- postcholecystectomy syndrome K91.5
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the K83 Range 11 codes · 9 billable
- K83 Other diseases of biliary tractNon-billable
- K83.0 CholangitisNon-billable
- K83.01 Primary sclerosing cholangitis
- K83.09 Other cholangitis
- K83.1 Obstruction of bile duct
- K83.2 Perforation of bile duct
- K83.3 Fistula of bile duct
- K83.4 Spasm of sphincter of Oddi
- K83.5 Biliary cyst
- K83.8 Other specified diseases of biliary tract
- K83.9 Disease of biliary tract, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the K83 range.
Alagille Syndrome
A multisystem disorder that is characterized by aplasia of intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC), and malformations in the cardiovascular system, the eyes, the vertebral column, and the facies. Major clinical features include JAUNDICE, and congenital heart disease with peripheral PULMONARY STENOSIS. Alagille syndrome may result from heterogeneous gene mutations, including mutations in JAG1 on CHROMOSOME 20 (Type 1) and NOTCH2 on CHROMOSOME 1 (Type 2).
Bile Ducts
The channels that collect and transport the bile secretion from the BILE CANALICULI, the smallest branch of the BILIARY TRACT in the LIVER, through the bile ductules, the bile ducts out the liver, and to the GALLBLADDER for storage.
Cholangitis
Inflammation of the biliary ductal system (BILE DUCTS); intrahepatic, extrahepatic, or both.
Cholangitis, Sclerosing
Chronic inflammatory disease of the BILIARY TRACT. It is characterized by fibrosis and hardening of the intrahepatic and extrahepatic biliary ductal systems leading to bile duct strictures, CHOLESTASIS, and eventual BILIARY CIRRHOSIS.
Choledochal Cyst
A congenital anatomic malformation of a bile duct, including cystic dilatation of the extrahepatic bile duct or the large intrahepatic bile duct. Classification is based on the site and type of dilatation. Type I is most common.
Cholestasis
Impairment of bile flow due to obstruction in small bile ducts (INTRAHEPATIC CHOLESTASIS) or obstruction in large bile ducts (EXTRAHEPATIC CHOLESTASIS).
Cholestasis, Extrahepatic
Impairment of bile flow in the large BILE DUCTS by mechanical obstruction or stricture due to benign or malignant processes.
Cholestasis, Intrahepatic
Impairment of bile flow due to injury to the HEPATOCYTES; BILE CANALICULI; or the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC).
Hemobilia
Hemorrhage in or through the BILIARY TRACT due to trauma, inflammation, CHOLELITHIASIS, vascular disease, or neoplasms.
Liver Cirrhosis, Biliary
FIBROSIS of the hepatic parenchyma due to obstruction of BILE flow (CHOLESTASIS) in the intrahepatic or extrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC; BILE DUCTS, EXTRAHEPATIC). Primary biliary cholangitis involves the destruction of small intra-hepatic bile ducts and decreased bile secretion. Secondary biliary cholangitis is produced by prolonged obstruction of large intrahepatic or extrahepatic bile ducts from a variety of causes.
About the K83 Code Range
The ICD-10 code section K83 covers other diseases of the biliary tract, including inflammation, obstruction, perforation, fistulas, spasms, cysts, and various specified or unspecified disorders affecting bile ducts. These codes help specify conditions related to the bile ducts beyond the most common biliary diseases.
This section is used to code rare or complex biliary tract problems. For example, K83.0 codes cholangitis, an inflammation of the bile ducts. K83.01 specifically identifies primary sclerosing cholangitis, a chronic liver disease characterized by bile duct scarring. Other cholangitis types with various causes are detailed under K83.09. K83.1 covers obstruction of the bile duct, which includes conditions like biliary strictures and cholestasis often seen in pregnancy or post-surgical states. Codes like K83.2 and K83.3 reflect mechanical complications such as bile duct perforation and fistulas, while K83.4 addresses spasms of the sphincter of Oddi, a muscle controlling bile flow. Biliary cysts are coded as K83.5. The K83.8 group includes other specified biliary tract diseases like biliary sludge, infections, and anatomical abnormalities. When the specific diagnosis is unclear, K83.9 is used for unspecified biliary tract diseases. Using this ICD-10 code section ensures precise documentation and aids appropriate treatment for diverse biliary conditions.
Questions About This Page
How many billable codes are in the K83 range?
Of the 11 codes in this range, 9 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the K83 range classify?
The range classifies other diseases of biliary tract. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
