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  3. K00–K95
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  5. Other diseases of biliary tract (K83)

Other diseases of biliary tract (K83)

The ICD-10 code section K83 covers other diseases of the biliary tract, including inflammation, obstruction, perforation, fistulas, spasms, cysts, and various specified or unspecified disorders affecting bile ducts. These codes help specify conditions related to the bile ducts beyond the most common biliary diseases.

This section is used to code rare or complex biliary tract problems. For example, K83.0 codes cholangitis, an inflammation of the bile ducts. K83.01 specifically identifies primary sclerosing cholangitis, a chronic liver disease characterized by bile duct scarring. Other cholangitis types with various causes are detailed under K83.09. K83.1 covers obstruction of the bile duct, which includes conditions like biliary strictures and cholestasis often seen in pregnancy or post-surgical states. Codes like K83.2 and K83.3 reflect mechanical complications such as bile duct perforation and fistulas, while K83.4 addresses spasms of the sphincter of Oddi, a muscle controlling bile flow. Biliary cysts are coded as K83.5. The K83.8 group includes other specified biliary tract diseases like biliary sludge, infections, and anatomical abnormalities. When the specific diagnosis is unclear, K83.9 is used for unspecified biliary tract diseases. Using this ICD-10 code section ensures precise documentation and aids appropriate treatment for diverse biliary conditions.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • postcholecystectomy syndrome K91.5

Type 2 Excludes

A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  • conditions involving the gallbladder K81 K82
  • conditions involving the cystic duct K81 K82

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Alagille Syndrome

A multisystem disorder that is characterized by aplasia of intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC), and malformations in the cardiovascular system, the eyes, the vertebral column, and the facies. Major clinical features include JAUNDICE, and congenital heart disease with peripheral PULMONARY STENOSIS. Alagille syndrome may result from heterogeneous gene mutations, including mutations in JAG1 on CHROMOSOME 20 (Type 1) and NOTCH2 on CHROMOSOME 1 (Type 2).

Bile Ducts

The channels that collect and transport the bile secretion from the BILE CANALICULI, the smallest branch of the BILIARY TRACT in the LIVER, through the bile ductules, the bile ducts out the liver, and to the GALLBLADDER for storage.

Cholangitis

Inflammation of the biliary ductal system (BILE DUCTS); intrahepatic, extrahepatic, or both.

Cholangitis, Sclerosing

Chronic inflammatory disease of the BILIARY TRACT. It is characterized by fibrosis and hardening of the intrahepatic and extrahepatic biliary ductal systems leading to bile duct strictures, CHOLESTASIS, and eventual BILIARY CIRRHOSIS.

Choledochal Cyst

A congenital anatomic malformation of a bile duct, including cystic dilatation of the extrahepatic bile duct or the large intrahepatic bile duct. Classification is based on the site and type of dilatation. Type I is most common.

Cholestasis

Impairment of bile flow due to obstruction in small bile ducts (INTRAHEPATIC CHOLESTASIS) or obstruction in large bile ducts (EXTRAHEPATIC CHOLESTASIS).

Cholestasis, Extrahepatic

Impairment of bile flow in the large BILE DUCTS by mechanical obstruction or stricture due to benign or malignant processes.

Cholestasis, Intrahepatic

Impairment of bile flow due to injury to the HEPATOCYTES; BILE CANALICULI; or the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC).

Hemobilia

Hemorrhage in or through the BILIARY TRACT due to trauma, inflammation, CHOLELITHIASIS, vascular disease, or neoplasms.

Liver Cirrhosis, Biliary

FIBROSIS of the hepatic parenchyma due to obstruction of BILE flow (CHOLESTASIS) in the intrahepatic or extrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC; BILE DUCTS, EXTRAHEPATIC). Primary biliary cholangitis involves the destruction of small intra-hepatic bile ducts and decreased bile secretion. Secondary biliary cholangitis is produced by prolonged obstruction of large intrahepatic or extrahepatic bile ducts from a variety of causes.