2027 ICD-10-CM Diagnosis Code H47.219Primary optic atrophy, unspecified eye

ICD-10-CM Codes›H00–H59›H46-H47›H47

ICD-10-CM H47.219
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

H47.219 is a billable ICD-10-CM diagnosis code for primary optic atrophy, unspecified eye. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 123. Coders also document this condition as congenital atrophy of optic nerve. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neuro-ophthalmology.

Code Identity

ICD-10-CM Code
H47.219
Billable Status
Yes — Valid for Submission
Code Describes
Primary optic atrophy, unspecified eye
Short Description
Primary optic atrophy, unspecified eye
Same as the full description in the CMS dataset.
Parent Code
H47.21
Primary optic atrophy

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH46-H47Disorders of optic nerve and visual pathways
CategoryH47Other disorders of optic [2nd] nerve and visual pathways
This CodeH47.219Primary optic atrophy, unspecified eye

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital atrophy of optic nerve
  • Primary optic atrophy

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to H47.219: its own notes plus those printed at Chapter 7. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Notes

General instructions on how these codes are used.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name H47.219, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming H47.219: they are not reported together with it, unless the two conditions are unrelated.

  • G71.3 Mitochondrial myopathy, not elsewhere classified
    Leber's disease (H47.21) names H47.21, which includes this code

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE006
Neuro-ophthalmology
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Optic Atrophy

    atrophy of the optic disk which may be congenital or acquired. this condition indicates a deficiency in the number of nerve fibers which arise in the retina and converge to form the optic disk; optic nerve; optic chiasm; and optic tracts. glaucoma; ischemia; inflammation, a chronic elevation of intracranial pressure, toxins, optic nerve compression, and inherited conditions (see optic atrophies, hereditary) are relatively common causes of this condition.

Patient EducationClinical

Optic Nerve Disorders

The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H47.219 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
377.11 Primary optic atrophy
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About H47.219Overview

What is the ICD-10 code for primary optic atrophy, unspecified eye?

The ICD-10-CM code for primary optic atrophy, unspecified eye is H47.219 (sometimes written as H47219). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is H47.219 (Primary optic atrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report primary optic atrophy, unspecified eye on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does H47.219 group to?

When primary optic atrophy, unspecified eye is the principal diagnosis on an inpatient stay, it groups to MS-DRG 123 (neurological Eye Disorders), which carries a relative weight of 0.8218. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H47.219?

Under the General Equivalence Mappings, primary optic atrophy, unspecified eye converts to ICD-9-CM 377.11 (primary optic atrophy). The mapping is approximate, so confirm the match fits the documentation.