2027 ICD-10-CM Diagnosis Code H47.033Optic nerve hypoplasia, bilateral
ICD-10-CM Codes›H00–H59›H46-H47›H47
- Billable — Valid for Submission
- Chronic Condition
H47.033 is a billable ICD-10-CM diagnosis code for optic nerve hypoplasia, bilateral. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 123. Coders also document this condition as bilateral congenital hypoplasia of optic nerves. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neuro-ophthalmology.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Bilateral congenital hypoplasia of optic nerves
- Congenital hypoplasia of left optic nerve
- Congenital hypoplasia of right optic nerve
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to H47.033: its own notes plus those printed at Chapter 7. A note printed at a category, block or chapter applies to every code under it.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Notes
General instructions on how these codes are used.
- Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name H47.033, its category, or a range that includes it.
Excludes1 1
These codes carry an Excludes1 note naming H47.033: they are not reported together with it, unless the two conditions are unrelated.
Excludes2 2
These codes carry an Excludes2 note naming H47.033: its condition is not part of those codes, and both may be reported when the patient has both.
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Optic Nerve Hypoplasia
a group of rare genetic disorders characterized by underdeveloped optic nerves, resulting in increased incidences of vision impairment, congenital nystagmus and strabismus. it may be syndromic, and is often associated with cns malformations.
Patient EducationClinical
Optic Nerve Disorders
The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert H47.033 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About H47.033Overview
What is the ICD-10 code for optic nerve hypoplasia, bilateral?
The ICD-10-CM code for optic nerve hypoplasia, bilateral is H47.033 (sometimes written as H47033). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is H47.033 (Optic nerve hypoplasia) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report optic nerve hypoplasia, bilateral on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does H47.033 group to?
When optic nerve hypoplasia, bilateral is the principal diagnosis on an inpatient stay, it groups to MS-DRG 123 (neurological Eye Disorders), which carries a relative weight of 0.8218. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of H47.033?
Under the General Equivalence Mappings, optic nerve hypoplasia, bilateral converts to ICD-9-CM 377.43 (optic nerve hypoplasia). The mapping is approximate, so confirm the match fits the documentation.
