2026 ICD-10-CM Diagnosis Code H47.033Optic nerve hypoplasia, bilateral

ICD-10-CM Codes›H00–H59›H46-H47›H47

ICD-10-CM H47.033
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H47.033 is a billable ICD-10-CM diagnosis code for optic nerve hypoplasia, bilateral. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as bilateral congenital hypoplasia of optic nerves. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neuro-ophthalmology.

Code Identity

ICD-10-CM Code
H47.033
Billable Status
Yes — Valid for Submission
Code Describes
Optic nerve hypoplasia, bilateral
Short Description
Optic nerve hypoplasia, bilateral
Same as the full description in the CMS dataset.
Parent Code
H47.03
Optic nerve hypoplasia

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH46-H47Disorders of optic nerve and visual pathways
CategoryH47Other disorders of optic [2nd] nerve and visual pathways
This CodeH47.033Optic nerve hypoplasia, bilateral

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral congenital hypoplasia of optic nerves
  • Congenital hypoplasia of left optic nerve
  • Congenital hypoplasia of right optic nerve

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE006
Neuro-ophthalmology
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Optic Nerve Hypoplasia

    a group of rare genetic disorders characterized by underdeveloped optic nerves, resulting in increased incidences of vision impairment, congenital nystagmus and strabismus. it may be syndromic, and is often associated with cns malformations.

Patient EducationClinical

Optic Nerve Disorders

The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H47.033 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
377.43 Optic nerve hypoplasia
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H47.033Overview

Is H47.033 (Optic nerve hypoplasia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report optic nerve hypoplasia, bilateral on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of H47.033?

Under the General Equivalence Mappings, optic nerve hypoplasia, bilateral converts to ICD-9-CM 377.43 (optic nerve hypoplasia). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.