2027 ICD-10-CM Diagnosis Code H47.031Optic nerve hypoplasia, right eye

ICD-10-CM Codes›H00–H59›H46-H47›H47

ICD-10-CM H47.031
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

H47.031 is a billable ICD-10-CM diagnosis code for optic nerve hypoplasia, right eye. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 123. Coders also document this condition as congenital hypoplasia of right optic nerve. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neuro-ophthalmology.

Code Identity

ICD-10-CM Code
H47.031
Billable Status
Yes — Valid for Submission
Code Describes
Optic nerve hypoplasia, right eye
Short Description
Optic nerve hypoplasia, right eye
Same as the full description in the CMS dataset.
Parent Code
H47.03
Optic nerve hypoplasia

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH46-H47Disorders of optic nerve and visual pathways
CategoryH47Other disorders of optic [2nd] nerve and visual pathways
This CodeH47.031Optic nerve hypoplasia, right eye

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital hypoplasia of right optic nerve

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to H47.031: its own notes plus those printed at Chapter 7. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Notes

General instructions on how these codes are used.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name H47.031, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming H47.031: they are not reported together with it, unless the two conditions are unrelated.

  • Q15 Other congenital malformations of eye
    optic nerve hypoplasia (H47.03-) names H47.03-, which includes this code

Excludes2 2

These codes carry an Excludes2 note naming H47.031: its condition is not part of those codes, and both may be reported when the patient has both.

  • G52 Disorders of other cranial nerves
    disorders of optic [2nd] nerve (H46, H47.0) names H47.0, which includes this code
  • Q14 Congenital malformations of posterior segment of eye
    optic nerve hypoplasia (H47.03-) names H47.03-, which includes this code

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE006
Neuro-ophthalmology
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Optic Nerve Hypoplasia

    a group of rare genetic disorders characterized by underdeveloped optic nerves, resulting in increased incidences of vision impairment, congenital nystagmus and strabismus. it may be syndromic, and is often associated with cns malformations.

Patient EducationClinical

Optic Nerve Disorders

The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H47.031 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
377.43 Optic nerve hypoplasia
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About H47.031Overview

What is the ICD-10 code for optic nerve hypoplasia, right eye?

The ICD-10-CM code for optic nerve hypoplasia, right eye is H47.031 (sometimes written as H47031). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is H47.031 (Optic nerve hypoplasia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report optic nerve hypoplasia, right eye on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does H47.031 group to?

When optic nerve hypoplasia, right eye is the principal diagnosis on an inpatient stay, it groups to MS-DRG 123 (neurological Eye Disorders), which carries a relative weight of 0.8218. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H47.031?

Under the General Equivalence Mappings, optic nerve hypoplasia, right eye converts to ICD-9-CM 377.43 (optic nerve hypoplasia). The mapping is approximate, so confirm the match fits the documentation.