2026 ICD-10-CM Diagnosis Code H40.1390Pigmentary glaucoma, unspecified eye, stage unspecified

ICD-10-CM Codes›H00–H59›H40-H42›H40

ICD-10-CM H40.1390
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H40.1390 is a billable ICD-10-CM diagnosis code for pigmentary glaucoma, unspecified eye, stage unspecified. The 7th character 0 reports glaucoma with the stage unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. The code is not accepted as a principal diagnosis by the Medicare Code Editor. Coders also document this condition as glaucoma due to iris anomaly. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Glaucoma.

Code Identity

ICD-10-CM Code
H40.1390
Billable Status
Yes — Valid for Submission
Code Describes
Pigmentary glaucoma, unspecified eye, stage unspecified
Short Description
Pigmentary glaucoma, unspecified eye, stage unspecified
Same as the full description in the CMS dataset.
Parent Code
H40.139
Pigmentary glaucoma, unspecified eye

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH40-H42Glaucoma
CategoryH40Glaucoma
This CodeH40.1390Pigmentary glaucoma, unspecified eye, stage unspecified

Code EditsBilling

Medicare Code Editor checks that affect claim validity for H40.1390.

Unacceptable principal diagnosis
There are selected codes that describe a circumstance which influences an individual's health status but not a current illness or injury, or codes that are not specific manifestations but may be due to an underlying cause. These codes are considered unacceptable as a principal diagnosis.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Glaucoma due to iris anomaly
  • Pigmentary glaucoma

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE003
Glaucoma
Default principal diagnosis: inpatient No · outpatient Yes

Patient EducationClinical

Glaucoma

Glaucoma is a group of diseases that can damage the optic nerve of one, or both, of your eyes. This can result in vision loss. There are different types of glaucoma, but the most common type is open-angle glaucoma. Other less common types include angle-closure glaucoma, and congenital glaucoma.

The full article covers:

  • What is glaucoma?
  • What causes glaucoma?
  • What are the symptoms of glaucoma?
  • How is glaucoma diagnosed?
  • What are the treatments for glaucoma?
  • Can glaucoma be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H40.1390 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
365.13 Pigmentary glaucoma
ApproximateCombination The match is approximate, and more than one code can be needed to describe the source diagnosis. Confirm with contextual judgment.
ICD-9-CM
365.70 Glaucoma stage NOS
ApproximateCombination The match is approximate, and more than one code can be needed to describe the source diagnosis. Confirm with contextual judgment.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H40.1390Overview

Is H40.1390 (Pigmentary glaucoma, unspecified eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pigmentary glaucoma, unspecified eye, stage unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What does the 7th character 0 in H40.1390 mean?

The final character 0 reports glaucoma with the stage unspecified, in this case involving the pigmentary glaucoma.

What MS-DRG does H40.1390 group to?

On inpatient claims, pigmentary glaucoma, unspecified eye, stage unspecified maps to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Can H40.1390 be a principal diagnosis?

No. The Medicare Code Editor rejects this code as a principal diagnosis because pigmentary glaucoma, unspecified eye, stage unspecified describes a circumstance that influences health status rather than a current illness. Report it as a secondary diagnosis.

What is the ICD-9 equivalent of H40.1390?

Under the General Equivalence Mappings, pigmentary glaucoma, unspecified eye, stage unspecified converts to ICD-9-CM 365.13 (pigmentary glaucoma) and 365.70 (glaucoma stage NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.