2027 ICD-10-CM Diagnosis Code H18.599Other hereditary corneal dystrophies, unspecified eye

ICD-10-CM Codes›H00–H59›H15-H22›H18

ICD-10-CM H18.599
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

H18.599 is a billable ICD-10-CM diagnosis code for other hereditary corneal dystrophies, unspecified eye. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cornea and external disease.

Code Identity

ICD-10-CM Code
H18.599
Billable Status
Yes — Valid for Submission
Code Describes
Other hereditary corneal dystrophies, unspecified eye
Short Description
Other hereditary corneal dystrophies, unspecified eye
Same as the full description in the CMS dataset.
Parent Code
H18.59
Other hereditary corneal dystrophies

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH15-H22Disorders of sclera, cornea, iris and ciliary body
CategoryH18Other disorders of cornea
This CodeH18.599Other hereditary corneal dystrophies, unspecified eye

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Central cloudy dystrophy of Francois
  • Combined corneal dystrophy
  • Congenital corneal dystrophy
  • Congenital osteodystrophy
  • Congenital stromal corneal dystrophy
  • Crocodile shagreen of cornea
  • Fleck corneal dystrophy
  • Francois syndrome
  • Gelatinous droplike corneal dystrophy
  • Grayson Wilbrandt corneal dystrophy
  • Polymorphous corneal dystrophy
  • Posterior amorphous corneal dystrophy
  • Posterior crocodile shagreen of cornea
  • Pre-descemet's corneal dystrophy
  • Reis-Bucklers' corneal dystrophy
  • Ring-like corneal dystrophy
  • Schnyder crystalline cornea dystrophy
  • Stromal corneal dystrophy
  • Subepithelial mucinous corneal dystrophy
  • Thiel-Behnke corneal dystrophy

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to H18.599: its own notes plus those printed at Chapter 7. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Notes

General instructions on how these codes are used.

From Chapter 7 (H00-H59) Diseases of the eye and adnexa applies to 2,677 codes
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE001
Cornea and external disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Corneal Dystrophies, Hereditary

    bilateral hereditary disorders of the cornea, usually autosomal dominant, which may be present at birth but more frequently develop during adolescence and progress slowly throughout life. central macular dystrophy is transmitted as an autosomal recessive defect.

Patient EducationClinical

Corneal Disorders

Your cornea is the outermost layer of your eye. It is clear and shaped like a dome. The cornea helps to shield the rest of the eye from germs, dust, and other harmful matter. It also helps your eye to focus. If you wear contact lenses, they float on top of your corneas.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement H18.599 replaces the following previously assigned code(s):

  • H18.59 - Other hereditary corneal dystrophies
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About H18.599Overview

What is the ICD-10 code for other hereditary corneal dystrophies, unspecified eye?

The ICD-10-CM code for other hereditary corneal dystrophies, unspecified eye is H18.599 (sometimes written as H18599). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is H18.599 (Other hereditary corneal dystrophies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other hereditary corneal dystrophies, unspecified eye on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does H18.599 group to?

When other hereditary corneal dystrophies, unspecified eye is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.