2026 ICD-10-CM Diagnosis Code D75.0Familial erythrocytosis

ICD-10-CM Codes›D50–D89›D70-D77›D75

ICD-10-CM D75.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D75.0 is a billable ICD-10-CM diagnosis code for familial erythrocytosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 814 through 816. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified hematologic conditions.

Code Identity

ICD-10-CM Code
D75.0
Billable Status
Yes — Valid for Submission
Code Describes
Familial erythrocytosis
Short Description
Familial erythrocytosis
Same as the full description in the CMS dataset.
Parent Code
D75
Other and unspecified diseases of blood and blood-forming organs

Code Classification

ChapterD50–D89Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
SectionD70-D77Other disorders of blood and blood-forming organs
CategoryD75Other and unspecified diseases of blood and blood-forming organs
This CodeD75.0Familial erythrocytosis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Chuvash erythrocytosis
  • Disorder of manganese metabolism
  • Familial erythrocytosis
  • Familial erythrocytosis due to diphosphoglycerate mutase deficiency
  • Familial polycythemia vera
  • Hypermanganesemia with dystonia
  • Hypermanganesemia with dystonia, polycythemia, and cirrhosis
  • Polycythemia vera
  • Primary familial polycythemia due to erythropoietin receptor mutation
  • Primary malignant neoplasm of bone marrow

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Benign polycythemia
  • Familial polycythemia

Type 1 Excludes

  • hereditary ovalocytosis D58.1

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Erythrocytosis(megalosplenic) (secondary)
      • familial
    • Polycythemia(secondary)
      • benign (familial)
    • Polycythemia(secondary)
      • familial (benign)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR BLD010
Other specified and unspecified hematologic conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Polycythemia Vera

    a myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. hematopoiesis is also reactive in extramedullary sites (liver and spleen). in time myelofibrosis occurs.

Patient EducationClinical

Blood Disorders

Your blood is living tissue made up of liquid and solids. The liquid part, called plasma, is made of water, salts and protein. Over half of your blood is plasma. The solid part of your blood contains red blood cells, white blood cells and platelets.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D75.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
289.6 Familial polycythemia
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D75.0Overview

Is D75.0 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report familial erythrocytosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does D75.0 group to?

When familial erythrocytosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 814, 815, 816, with relative weights from 0.6320 to 2.1267 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of D75.0?

Under the General Equivalence Mappings, familial erythrocytosis converts to ICD-9-CM 289.6 (familial polycythemia). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.