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  2. ICD-10-CM Codes List
  3. D50–D89
  4. D70-D77
  5. Methemoglobinemia (D74)

Methemoglobinemia (D74)

ICD-10 code D74 and its subcodes classify different forms of methemoglobinemia, a blood condition where hemoglobin is unable to effectively carry oxygen. These codes are used to specify whether the condition is inherited, acquired, or unspecified.

D74.0 refers to congenital methemoglobinemia, which includes inherited types like Familial methemoglobinemia or Hemoglobin M disease, caused by defective enzymes or abnormal hemoglobin. This is important for coding genetic or long-standing cases. D74.8 covers other methemoglobinemias, often acquired through exposure to toxins, drugs, or nitrate poisoning, sometimes called drug-induced or toxic methemoglobinemia. This lets coders distinguish environmentally or chemically caused cases. Finally, D74.9 is for unspecified methemoglobinemia when the origin is not clearly documented. Using these codes precisely helps in identifying whether a patient's methemoglobinemia is inherited or acquired, which is essential for accurate diagnosis and treatment documentation.

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Methemoglobinemia

The presence of methemoglobin in the blood, resulting in cyanosis. A small amount of methemoglobin is present in the blood normally, but injury or toxic agents convert a larger proportion of hemoglobin into methemoglobin, which does not function reversibly as an oxygen carrier. Methemoglobinemia may be due to a defect in the enzyme NADH methemoglobin reductase (an autosomal recessive trait) or to an abnormality in hemoglobin M (an autosomal dominant trait). (Dorland, 27th ed)

Sulfhemoglobinemia

A morbid condition due to the presence of sulfmethemoglobin in the blood. It is marked by persistent cyanosis, but the blood count does not reveal any special abnormality in the blood. It is thought to be caused by the action of hydrogen sulfide absorbed from the intestine. (Stedman, 25th ed)