Methemoglobinemia (D74) ICD-10-CM
The D74 code range covers methemoglobinemia with 4 ICD-10-CM diagnosis codes. 3 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the D74 Range 4 codes · 3 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the D74 range.
Congenital Methemoglobinemia
Methemoglobinemia inherited in an autosomal recessive pattern. It is caused by deficiency of the enzyme NADH methemoglobin reductase or the presence of abnormal hemoglobin M. It presents with cyanosis early in life. There is no evidence of cardiopulmonary disease present.
Methemoglobinemia
The presence of methemoglobin in the blood, resulting in cyanosis. A small amount of methemoglobin is present in the blood normally, but injury or toxic agents convert a larger proportion of hemoglobin into methemoglobin, which does not function reversibly as an oxygen carrier. Methemoglobinemia may be due to a defect in the enzyme NADH methemoglobin reductase (an autosomal recessive trait) or to an abnormality in hemoglobin M (an autosomal dominant trait). (Dorland, 27th ed)
Sulfhemoglobinemia
A morbid condition due to the presence of sulfmethemoglobin in the blood. It is marked by persistent cyanosis, but the blood count does not reveal any special abnormality in the blood. It is thought to be caused by the action of hydrogen sulfide absorbed from the intestine. (Stedman, 25th ed)
About the D74 Code Range
Methemoglobinemia occurs when too much of the blood’s oxygen-carrying hemoglobin changes into methemoglobin, which cannot carry oxygen normally and causes a bluish discoloration.
Within other blood disorders, D74 separates congenital methemoglobinemia from other and unspecified forms. D74.0 is congenital, meaning present at birth; D74.8 covers other forms; and D74.9 is unspecified.
Questions About This Page
How many billable codes are in the D74 range?
Of the 4 codes in this range, 3 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the D74 range classify?
The range classifies methemoglobinemia. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
