Methemoglobinemia (D74) ICD-10-CM
The D74 code range covers methemoglobinemia with 4 ICD-10-CM diagnosis codes. 3 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the D74 Range 4 codes · 3 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the D74 range.
Methemoglobinemia
The presence of methemoglobin in the blood, resulting in cyanosis. A small amount of methemoglobin is present in the blood normally, but injury or toxic agents convert a larger proportion of hemoglobin into methemoglobin, which does not function reversibly as an oxygen carrier. Methemoglobinemia may be due to a defect in the enzyme NADH methemoglobin reductase (an autosomal recessive trait) or to an abnormality in hemoglobin M (an autosomal dominant trait). (Dorland, 27th ed)
Sulfhemoglobinemia
A morbid condition due to the presence of sulfmethemoglobin in the blood. It is marked by persistent cyanosis, but the blood count does not reveal any special abnormality in the blood. It is thought to be caused by the action of hydrogen sulfide absorbed from the intestine. (Stedman, 25th ed)
About the D74 Code Range
ICD-10 code D74 and its subcodes classify different forms of methemoglobinemia, a blood condition where hemoglobin is unable to effectively carry oxygen. These codes are used to specify whether the condition is inherited, acquired, or unspecified.
D74.0 refers to congenital methemoglobinemia, which includes inherited types like Familial methemoglobinemia or Hemoglobin M disease, caused by defective enzymes or abnormal hemoglobin. This is important for coding genetic or long-standing cases. D74.8 covers other methemoglobinemias, often acquired through exposure to toxins, drugs, or nitrate poisoning, sometimes called drug-induced or toxic methemoglobinemia. This lets coders distinguish environmentally or chemically caused cases. Finally, D74.9 is for unspecified methemoglobinemia when the origin is not clearly documented. Using these codes precisely helps in identifying whether a patient's methemoglobinemia is inherited or acquired, which is essential for accurate diagnosis and treatment documentation.
Questions About This Page
How many billable codes are in the D74 range?
Of the 4 codes in this range, 3 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the D74 range classify?
The range classifies methemoglobinemia. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
