Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue (D76) ICD-10-CM
The D76 code range covers other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue with 4 ICD-10-CM diagnosis codes. 3 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- Abt- Letterer-Siwe disease C96.0
- eosinophilic granuloma C96.6
- Hand-Schüller-Christian disease C96.5
- histiocytic medullary reticulosis C96.9
- histiocytic sarcoma C96.A
- histiocytosis X, multifocal C96.5
- histiocytosis X, unifocal C96.6
- Langerhans-cell histiocytosis, multifocal C96.5
- Langerhans-cell histiocytosis NOS C96.6
- Langerhans-cell histiocytosis, unifocal C96.6
- leukemic reticuloendotheliosis C91.4
- lipomelanotic reticulosis I89.8
- malignant histiocytosis C96.A
- malignant reticulosis C86.0
- nonlipid reticuloendotheliosis C96.0
Codes in the D76 Range 4 codes · 3 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the D76 range.
Histiocytosis
General term for the abnormal appearance of histiocytes in the blood. Based on the pathological features of the cells involved rather than on clinical findings, the histiocytic diseases are subdivided into three groups: HISTIOCYTOSIS, LANGERHANS CELL; HISTIOCYTOSIS, NON-LANGERHANS-CELL; and HISTIOCYTIC DISORDERS, MALIGNANT.
Lymphohistiocytosis, Hemophagocytic
A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.
Reactive Hemophagocytic Syndrome
Proliferation of HISTIOCYTES in response to viral, bacterial, fungal, or parasitic infections.
About the D76 Code Range
These conditions involve lymphoreticular and reticulohistiocytic tissue and sit within the broader group of blood and blood-forming organ disorders.
Within D76, the subdivisions separate a named condition (D76.1), a related syndrome associated with infection (D76.2), and other histiocytosis syndromes (D76.3).
Questions About This Page
How many billable codes are in the D76 range?
Of the 4 codes in this range, 3 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the D76 range classify?
The range classifies other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
