ICD-10 Diagnosis Code Q42.2

Congenital absence, atresia and stenosis of anus w fistula

Diagnosis Code Q42.2

ICD-10: Q42.2
Short Description: Congenital absence, atresia and stenosis of anus w fistula
Long Description: Congenital absence, atresia and stenosis of anus with fistula
This is the 2017 version of the ICD-10-CM diagnosis code Q42.2

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Other congenital malformations of the digestive system (Q38-Q45)
      • Congenital absence, atresia and stenosis of large intestine (Q42)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q42.2 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q42.2 is exempt from POA reporting.

  • Anal atresia
  • Anorectal agenesis
  • Atresia of anus with fistula
  • Congenital absence of anus
  • Congenital absence of anus with fistula
  • Congenital occlusion of anus with fistula
  • Congenital stricture of anus
  • Congenital stricture of anus with fistula
  • Low anorectal malformation

Information for Patients

Anal Disorders

Also called: Anorectal diseases

The anus is the opening of the rectum through which stool passes out of your body. Problems with the anus are common. They include hemorrhoids, abscesses, fissures (cracks), and cancer.

You may be embarrassed to talk about your anal troubles. But it is important to let your doctor know, especially if you have pain or bleeding. The more details you can give about your problem, the better your doctor will be able to help you. Treatments vary depending on the particular problem.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

  • Anal fissure
  • Anal itching -- self-care
  • Anorectal abscess
  • Anoscopy
  • Digital rectal exam
  • Imperforate anus
  • Lower GI Series - NIH (National Institute of Diabetes and Digestive and Kidney Diseases)
  • Perianal streptococcal cellulitis

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Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can vary from mild to severe. Some result from exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome. Infections during pregnancy can also result in birth defects. For most birth defects, the cause is unknown.

Some birth defects can be prevented. Taking folic acid can help prevent some birth defects. Talk to your doctor about any medicines you take. Some medicines can cause serious birth defects.

Babies with birth defects may need surgery or other medical treatments. Today, doctors can diagnose many birth defects in the womb. This enables them to treat or even correct some problems before the baby is born.

Centers for Disease Control and Prevention

  • Intersex

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A fistula is an abnormal connection between two parts inside of the body. Fistulas may develop between different organs, such as between the esophagus and the windpipe or the bowel and the vagina. They can also develop between two blood vessels, such as between an artery and a vein or between two arteries.

Some people are born with a fistula. Other common causes of fistulas include

  • Complications from surgery
  • Injury
  • Infection
  • Diseases, such as Crohn's disease or ulcerative colitis

Treatment depends on the cause of the fistula, where it is, and how bad it is. Some fistulas will close on their own. In some cases, you may need antibiotics and/or surgery.

  • Fistula
  • Gastrointestinal fistula

[Read More]
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