ICD-10 Diagnosis Code E71.318

Other disorders of fatty-acid oxidation

Diagnosis Code E71.318

ICD-10: E71.318
Short Description: Other disorders of fatty-acid oxidation
Long Description: Other disorders of fatty-acid oxidation
This is the 2017 version of the ICD-10-CM diagnosis code E71.318

Code Classification
  • Endocrine, nutritional and metabolic diseases
    • Metabolic disorders (E70-E88)
      • Disord of branched-chain amino-acid metab & fatty-acid metab (E71)

Information for Medical Professionals

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The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • 3-Ketoacyl-coenzyme A triolase deficiency
  • Combined deficiency of long chain 3-hydroxyacyl-coenzyme A dehydrogenase and enoyl-coenzyme A hydratase
  • Combined long chain hydroxyacyl-coenzyme A dehydrogenase deficiency
  • Deficiency of 2-methylbutyryl-coenzyme A dehydrogenase
  • Deficiency of 3-hydroxyacyl-CoA dehydrogenase
  • Deficiency of acetyl-coenzyme A acyltransferase
  • Deficiency of enoyl-coenzyme A hydratase
  • Isolated long chain hydroxyacyl-CoA dehydrogenase deficiency
  • Mitochondrial trifunctional protein deficiency
  • Succinyl-coenzyme A acetoacetate transferase deficiency

Information for Patients

Lipid Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Lipid metabolism disorders, such as Gaucher disease and Tay-Sachs disease, involve lipids. Lipids are fats or fat-like substances. They include oils, fatty acids, waxes, and cholesterol. If you have one of these disorders, you may not have enough enzymes to break down lipids. Or the enzymes may not work properly and your body can't convert the fats into energy. They cause a harmful amount of lipids to build up in your body. Over time, that can damage your cells and tissues, especially in the brain, peripheral nervous system, liver, spleen, and bone marrow. Many of these disorders can be very serious, or sometimes even fatal.

These disorders are inherited. Newborn babies get screened for some of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.

Enzyme replacement therapies can help with a few of these disorders. For others, there is no treatment. Medicines, blood transfusions, and other procedures may help with complications.

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