ICD-10 Diagnosis Code Q13.81

Rieger's anomaly

Diagnosis Code Q13.81

ICD-10: Q13.81
Short Description: Rieger's anomaly
Long Description: Rieger's anomaly
This is the 2018 version of the ICD-10-CM diagnosis code Q13.81

Valid for Submission
The code Q13.81 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of eye, ear, face and neck (Q10-Q18)
      • Congenital malformations of anterior segment of eye (Q13)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q13.81 is grouped in the following Diagnostic Related Group(s) (MS-DRG V34.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q13.81 is exempt from POA reporting.

  • Acquired partial lipodystrophy
  • Axenfeld-Rieger syndrome
  • Irido-corneal dysgenesis
  • Irido-trabecular dysgenesis
  • Lipodystrophy, partial, with Rieger anomaly, short stature, and insulinopenic diabetes mellitus
  • Rieger eye malformation sequence
  • Rieger syndrome

Index of Diseases and Injuries
References found for the code Q13.81 in the Index of Diseases and Injuries:

    Information for Patients

    Birth Defects

    A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

    A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can vary from mild to severe. Some result from exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome. Infections during pregnancy can also result in birth defects. For most birth defects, the cause is unknown.

    Some birth defects can be prevented. Taking folic acid can help prevent some birth defects. Talk to your doctor about any medicines you take. Some medicines can cause serious birth defects.

    Babies with birth defects may need surgery or other medical treatments. Today, doctors can diagnose many birth defects in the womb. This enables them to treat or even correct some problems before the baby is born.

    Centers for Disease Control and Prevention

    • Intersex (Medical Encyclopedia)

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    Eye Diseases

    Some eye problems are minor and don't last long. But some can lead to a permanent loss of vision.

    Common eye problems include

    • Refractive errors
    • Cataracts - clouded lenses
    • Optic nerve disorders, including glaucoma
    • Retinal disorders - problems with the nerve layer at the back of the eye
    • Macular degeneration - a disease that destroys sharp, central vision
    • Diabetic eye problems
    • Conjunctivitis - an infection also known as pinkeye

    Your best defense is to have regular checkups, because eye diseases do not always have symptoms. Early detection and treatment could prevent vision loss. See an eye care professional right away if you have a sudden change in vision, if everything looks dim, or if you see flashes of light. Other symptoms that need quick attention are pain, double vision, fluid coming from the eye, and inflammation.

    NIH: National Eye Institute

    • Anisocoria (Medical Encyclopedia)
    • Choroidal dystrophies (Medical Encyclopedia)
    • Coloboma of the iris (Medical Encyclopedia)
    • Episcleritis (Medical Encyclopedia)
    • Eye and orbit ultrasound (Medical Encyclopedia)
    • Eye burning - itching and discharge (Medical Encyclopedia)
    • Eye pain (Medical Encyclopedia)
    • Eye redness (Medical Encyclopedia)
    • Fluorescein angiography (Medical Encyclopedia)
    • Fluorescein eye stain (Medical Encyclopedia)
    • Heterochromia (Medical Encyclopedia)
    • Ophthalmoscopy (Medical Encyclopedia)
    • Orbit CT scan (Medical Encyclopedia)
    • Orbital pseudotumor (Medical Encyclopedia)
    • Photophobia (Medical Encyclopedia)
    • Pinguecula (Medical Encyclopedia)
    • Pterygium (Medical Encyclopedia)
    • Pupil - white spots (Medical Encyclopedia)
    • Scleritis (Medical Encyclopedia)
    • Slit-lamp exam (Medical Encyclopedia)
    • Standard ophthalmic exam (Medical Encyclopedia)
    • Subconjunctival hemorrhage (Medical Encyclopedia)
    • Uveitis (Medical Encyclopedia)

    [Read More]

    Axenfeld-Rieger syndrome Axenfeld-Rieger syndrome is primarily an eye disorder, although it can also affect other parts of the body. This condition is characterized by abnormalities of the front part of the eye, an area known as the anterior segment. For example, the colored part of the eye (the iris), may be thin or poorly developed. The iris normally has a single central hole, called the pupil, through which light enters the eye. People with Axenfeld-Rieger syndrome often have a pupil that is off-center (corectopia) or extra holes in the iris that can look like multiple pupils (polycoria). This condition can also cause abnormalities of the cornea, which is the clear front covering of the eye.About half of affected individuals develop glaucoma, a serious condition that increases pressure inside the eye. When glaucoma occurs with Axenfeld-Rieger syndrome, it most often develops in late childhood or adolescence, although it can occur as early as infancy. Glaucoma can cause vision loss or blindness.The signs and symptoms of Axenfeld-Rieger syndrome can also affect other parts of the body. Many affected individuals have distinctive facial features such as widely spaced eyes (hypertelorism); a flattened mid-face with a broad, flat nasal bridge; and a prominent forehead. The condition is also associated with dental abnormalities including unusually small teeth (microdontia) or fewer than normal teeth (oligodontia). Some people with Axenfeld-Rieger syndrome have extra folds of skin around their belly button (redundant periumbilical skin). Other, less common features can include heart defects, the opening of the urethra on the underside of the penis (hypospadias), narrowing of the anus (anal stenosis), and abnormalities of the pituitary gland that can result in slow growth.Researchers have described at least three types of Axenfeld-Rieger syndrome. The types, which are numbered 1 through 3, are distinguished by their genetic cause.
    [Read More]
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