2026 ICD-10-CM Diagnosis Code P78.81Congenital cirrhosis (of liver)

ICD-10-CM Codes›P00–P96›P76-P78›P78

ICD-10-CM P78.81
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

P78.81 is a billable ICD-10-CM diagnosis code for congenital cirrhosis (of liver). It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neonatal digestive and feeding disorders.

Code Identity

ICD-10-CM Code
P78.81
Billable Status
Yes — Valid for Submission
Code Describes
Congenital cirrhosis (of liver)
Short Description
Congenital cirrhosis (of liver)
Same as the full description in the CMS dataset.
Parent Code
P78.8
Other specified perinatal digestive system disorders

Code Classification

ChapterP00–P96Certain conditions originating in the perinatal period
SectionP76-P78Digestive system disorders of newborn
CategoryP78Other perinatal digestive system disorders
This CodeP78.81Congenital cirrhosis (of liver)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cirrhosis, cirrhotic(hepatic) (liver)
      • liver
        • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL012
Neonatal digestive and feeding disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cirrhosis

Cirrhosis is scarring of the liver. Scar tissue forms because of injury or long-term disease. Scar tissue cannot do what healthy liver tissue does - make protein, help fight infections, clean the blood, help digest food and store energy. Cirrhosis can lead to :

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert P78.81 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
777.8 Perinat GI sys dis NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About P78.81Overview

Is P78.81 (Other specified perinatal digestive system disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital cirrhosis (of liver) on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of P78.81?

Under the General Equivalence Mappings, congenital cirrhosis (of liver) converts to ICD-9-CM 777.8 (perinat GI sys dis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.