2027 ICD-10-CM Diagnosis Code P78.81Congenital cirrhosis (of liver)

ICD-10-CM Codes›P00–P96›P76-P78›P78

ICD-10-CM P78.81
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

P78.81 is a billable ICD-10-CM diagnosis code for congenital cirrhosis (of liver). It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 794. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neonatal digestive and feeding disorders.

Code Identity

ICD-10-CM Code
P78.81
Billable Status
Yes — Valid for Submission
Code Describes
Congenital cirrhosis (of liver)
Short Description
Congenital cirrhosis (of liver)
Same as the full description in the CMS dataset.
Parent Code
P78.8
Other specified perinatal digestive system disorders

Code Classification

ChapterP00–P96Certain conditions originating in the perinatal period
SectionP76-P78Digestive system disorders of newborn
CategoryP78Other perinatal digestive system disorders
This CodeP78.81Congenital cirrhosis (of liver)

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to P78.81: its own notes plus those printed at P78 and Chapter 16. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • conditions that have their origin in the fetal or perinatal period (before birth through the first 28 days after birth) even if morbidity occurs later

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From P78 Other perinatal digestive system disorders applies to 10 codes

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • tetanus neonatorum (A33)

Notes

General instructions on how these codes are used.

From Chapter 16 (P00-P96) Certain conditions originating in the perinatal period applies to 463 codes
  • Codes from this chapter are for use on newborn records only, never on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name P78.81, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming P78.81: they are not reported together with it, unless the two conditions are unrelated.

  • K74 Fibrosis and cirrhosis of liver
    congenital cirrhosis (of liver) (P78.81)

Code First 1

These codes say to code first a condition named in the note, and P78.81 is one of the conditions named.

  • P91.811 Neonatal encephalopathy in diseases classified elsewhere
    congenital cirrhosis (of liver) (P78.81)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL012
Neonatal digestive and feeding disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cirrhosis

Cirrhosis is scarring of the liver. Scar tissue forms because of injury or long-term disease. Scar tissue cannot do what healthy liver tissue does - make protein, help fight infections, clean the blood, help digest food and store energy. Cirrhosis can lead to :

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert P78.81 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
777.8 Perinat GI sys dis NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About P78.81Overview

What is the ICD-10 code for congenital cirrhosis (of liver)?

The ICD-10-CM code for congenital cirrhosis (of liver) is P78.81 (sometimes written as P7881). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is P78.81 (Other specified perinatal digestive system disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital cirrhosis (of liver) on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does P78.81 group to?

When congenital cirrhosis (of liver) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 794 (neonate with Other Significant Problems), which carries a relative weight of 1.4934. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of P78.81?

Under the General Equivalence Mappings, congenital cirrhosis (of liver) converts to ICD-9-CM 777.8 (perinat GI sys dis NEC). The mapping is approximate, so confirm the match fits the documentation.