2026 ICD-10-CM Diagnosis Code K00.2Abnormalities of size and form of teeth

ICD-10-CM CodesK00–K95K00-K14K00

ICD-10-CM K00.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

K00.2 is a billable ICD-10-CM diagnosis code for abnormalities of size and form of teeth. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 157 through 159. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Any dental condition including traumatic injury, Disorders of teeth and gingiva, and Nontraumatic dental conditions.

Code Identity

ICD-10-CM Code
K00.2
Billable Status
Yes — Valid for Submission
Code Describes
Abnormalities of size and form of teeth
Short Description
Abnormalities of size and form of teeth
Same as the full description in the CMS dataset.
Parent Code
Disorders of tooth development and eruption

Code Classification

ChapterK00–K95Diseases of the digestive system
SectionK00-K14Diseases of oral cavity and salivary glands
CategoryK00Disorders of tooth development and eruption
This CodeK00.2Abnormalities of size and form of teeth

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal crown of tooth
  • Abnormal form of root of tooth
  • Abnormal form of tooth
  • Abnormal size of tooth
  • Amelogenesis imperfecta, hypomaturation hypoplasia type with taurodontism
  • Amelogenesis imperfecta, hypomaturation type
  • Amelogenesis imperfecta, hypoplastic type
  • Amelogenesis imperfecta, hypoplastic type with microdontia
  • Complete deafness
  • Concrescence of teeth
  • Congenital anomaly in number of teeth
  • Congenital deafness
  • Congenital deafness with labyrinthine aplasia, microtia and microdontia
  • Conical form of root of tooth
  • Curved form of root of tooth
  • Deletion of part of chromosome 11
  • Dens evaginatus
  • Dens in dente
  • Developmental abnormality of cusp of tooth
  • Dilated odontoma
  • Enamel pearls
  • Exaggerated cingulum of tooth
  • Exaggerated cusp of tooth
  • Fusion of crown of teeth
  • Fusion of mandibular incisor teeth
  • Fusion of teeth
  • Gemination of teeth
  • Gemination of tooth
  • Generalized macrodontia
  • Globodontia
  • High frequency sensorineural hearing loss
  • High frequency sensorineural hearing loss in left ear
  • High frequency sensorineural hearing loss in right ear
  • High frequency sensorineural hearing loss of bilateral ears
  • Hypertaurodontism
  • Hypotaurodontism
  • Incomplete form of root of tooth
  • KBG syndrome
  • Lateral accessory root canals
  • Localized macrodontia
  • Localized microdontia
  • Macrodontia
  • Mesotaurodontism
  • Microdontia
  • Microtia
  • Multirooted tooth with convergent roots
  • Multirooted tooth with divergent roots
  • Oculootodental syndrome
  • Otodental syndrome
  • Paired teeth microdontia
  • Peg-shaped teeth
  • Peg-shaped tooth
  • Protrusion of tooth
  • Radicular dens invaginatus
  • Relative generalized macrodontia
  • Relative generalized microdontia
  • Sensorineural hearing loss in left ear
  • Sensorineural hearing loss in right ear
  • Sensorineural hearing loss of bilateral ears
  • Sharp tooth
  • Shovel-shaped incisor
  • Single tooth macrodontia
  • Single tooth microdontia
  • Supernumerary cusp of tooth
  • Supernumerary root of tooth
  • Talon cusp
  • Tapered teeth
  • Taurodontia with absent teeth and sparse hair syndrome
  • Taurodontism
  • Tooth size discrepancy
  • True generalized microdontia
  • Tuberculum paramolare

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Concrescence of teeth
  • Fusion of teeth
  • Gemination of teeth
  • Dens evaginatus
  • Dens in dente
  • Dens invaginatus
  • Enamel pearls
  • Macrodontia
  • Microdontia
  • Peg-shaped conical teeth
  • Supernumerary roots
  • Taurodontism
  • Tuberculum paramolare

Type 1 Excludes

  • abnormalities of teeth due to congenital syphilis A50.5
  • tuberculum Carabelli, which is regarded as a normal variation and should not be coded

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Abnormal, abnormality, abnormalities
      • form
        • teeth
    • Abnormal, abnormality, abnormalities
      • size, tooth, teeth
    • Abnormal, abnormality, abnormalities
      • tooth, teeth (form) (size)
    • Accessory(congenital)
      • roots (teeth)
    • Anomaly, anomalous(congenital) (unspecified type)
      • form, teeth
    • Concrescence(teeth)
    • Conical
      • teeth
    • Deformity
      • tooth, teeth
    • Dens evaginatus, in dente or invaginatus
    • Dichotomy, teeth
    • Elongated, elongation(congenital)
      • tooth, teeth
    • Enamel pearls
    • Enameloma
    • Fusion, fused(congenital)
      • tooth, teeth
    • Gemination, tooth, teeth
    • Macrodontia
    • Microdontia
    • Molarization of premolars
    • Pearl(s)
      • enamel
    • Peg-shaped teeth
    • Predeciduous teeth
    • Premolarization, cuspids
    • Schizodontia
    • Shovel-shaped incisors
    • Spicule tooth
    • Supernumerary(congenital)
      • roots (of teeth)
    • Synodontia
    • Taurodontism
    • T-shaped incisors
    • Tuberculum
      • Carabelli
    • Tuberculum
      • occlusal
    • Tuberculum
      • paramolare
    • Twinning, teeth

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR DEN001
Any dental condition including traumatic injury
Default principal diagnosis: inpatient No · outpatient No
CCSR DIG002
Disorders of teeth and gingiva
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR DEN002
Nontraumatic dental conditions
Default principal diagnosis: inpatient No · outpatient No

Clinical InformationClinical

  • Dens in Dente

    anomaly of the tooth, found chiefly in upper lateral incisors. it is characterized by invagination of the enamel at the incisal edge.

Patient EducationClinical

Tooth Disorders

Your teeth are made of a hard, bonelike material. There are four parts:

The full article covers:

  • What are teeth?
  • What are tooth disorders?
  • What causes tooth disorders?
  • What are the symptoms of tooth disorders?
  • How are tooth disorders diagnosed?
  • What are the treatments for tooth disorders?
  • Can tooth disorders be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert K00.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
520.2 Abnormal tooth size/form
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About K00.2Overview

Is K00.2 (Disorders of tooth development and eruption) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report abnormalities of size and form of teeth on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does K00.2 group to?

When abnormalities of size and form of teeth is the principal diagnosis on an inpatient stay, it groups to MS-DRG 157, 158, 159, with relative weights from 0.7085 to 1.7168 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of K00.2?

Under the General Equivalence Mappings, abnormalities of size and form of teeth converts to ICD-9-CM 520.2 (abnormal tooth size/form). The mapping is a direct match.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.