Disorders of tooth development and eruption (K00) ICD-10-CM
The K00 code range covers disorders of tooth development and eruption with 11 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- embedded and impacted teeth K01
Codes in the K00 Range 11 codes · 10 billable
- K00 Disorders of tooth development and eruptionNon-billable
- K00.0 Anodontia
- K00.1 Supernumerary teeth
- K00.2 Abnormalities of size and form of teeth
- K00.3 Mottled teeth
- K00.4 Disturbances in tooth formation
- K00.5 Hereditary disturbances in tooth structure, not elsewhere classified
- K00.6 Disturbances in tooth eruption
- K00.7 Teething syndrome
- K00.8 Other disorders of tooth development
- K00.9 Disorder of tooth development, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the K00 range.
Amelogenesis Imperfecta
A clinically and genetically heterogeneous group of hereditary conditions characterized by malformed DENTAL ENAMEL, usually involving DENTAL ENAMEL HYPOPLASIA and/or TOOTH HYPOMINERALIZATION.
Anodontia
Congenital absence of the teeth. It may involve all (total anodontia) or only some of the teeth (partial anodontia, hypodontia), or six or more of the teeth (oligodontia) and both the deciduous and the permanent dentition, or only teeth of the permanent dentition.
Dens in Dente
Anomaly of the tooth, found chiefly in upper lateral incisors. It is characterized by invagination of the enamel at the incisal edge.
Dental Pulp Calcification
CALCINOSIS of the DENTAL PULP or ROOT CANAL.
Dentin Dysplasia
An apparently hereditary disorder of dentin formation, marked by a normal appearance of coronal dentin associated with pulpal obliteration, faulty root formation, and a tendency for peripheral lesions without obvious cause. (From Dorland, 27th ed)
Dentinogenesis Imperfecta
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Hypohidrosis
Abnormally diminished or absent perspiration. Both generalized and segmented (reduced or absent sweating in circumscribed locations) forms of the disease are usually associated with other underlying conditions.
Natal Teeth
Predeciduous teeth present at birth. They may be well formed and normal or may represent hornified epithelial structures without roots. They are found on the gingivae over the crest of the ridge and arise from accessory buds of the dental lamina ahead of the deciduous buds or from buds of the accessory dental lamina. (From Jablonski, Dictionary of Dentistry, 1992)
Osteopetrosis
Excessive formation of dense trabecular bone leading to pathological fractures; OSTEITIS; SPLENOMEGALY with infarct; ANEMIA; and extramedullary hemopoiesis (HEMATOPOIESIS, EXTRAMEDULLARY).
Osteosclerosis
An abnormal hardening or increased density of bone tissue.
Steatocystoma Multiplex
A disorder characterized by multiple, wide spread cutaneous cysts that often become inflamed and rupture. It is caused by the same mutations in the gene coding for KRT-17 that are causative mutations for Pachyonychia congenita, Type 2. Natal teeth involvement is sometimes associated with steatocystoma multiplex.
Tooth Loss
The failure to retain teeth as a result of disease or injury.
Toothache
Pain in the adjacent areas of the teeth.
About the K00 Code Range
The ICD-10 code section K00 covers disorders related to tooth development and eruption, specifically used to identify conditions affecting the formation, number, shape, and eruption timing of teeth. It includes detailed codes for varied abnormalities such as missing teeth, extra teeth, and structural defects.
This section helps medical coders distinguish among specific tooth development issues like K00.0 Anodontia (complete congenital absence of teeth, also known as hypodontia), and K00.1 Supernumerary teeth, which covers extra teeth like mesiodens or supplemental teeth. It also addresses abnormalities in size and form under K00.2, including conditions like microdontia, macrodontia, and taurodontism. Other codes include K00.3 Mottled teeth for dental fluorosis, K00.4 Disturbances in tooth formation for enamel hypoplasia and related defects, and K00.5 Hereditary disturbances in tooth structure covering inherited disorders like amelogenesis imperfecta and dentinogenesis imperfecta. Conditions involving tooth eruption delays or failures are classified under K00.6, while teething issues fall under K00.7 Teething syndrome. Additional or unspecified tooth development abnormalities are found in K00.8 and K00.9. Using these codes ensures precise identification of developmental and eruption tooth disorders in clinical documentation.
Questions About This Page
How many billable codes are in the K00 range?
Of the 11 codes in this range, 10 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the K00 range classify?
The range classifies disorders of tooth development and eruption. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
