Disorders of tooth development and eruption (K00) ICD-10-CM
The K00 code range covers disorders of tooth development and eruption with 11 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- embedded and impacted teeth K01
Codes in the K00 Range 11 codes · 10 billable
- K00 Disorders of tooth development and eruptionNon-billable
- K00.0 Anodontia
- K00.1 Supernumerary teeth
- K00.2 Abnormalities of size and form of teeth
- K00.3 Mottled teeth
- K00.4 Disturbances in tooth formation
- K00.5 Hereditary disturbances in tooth structure, not elsewhere classified
- K00.6 Disturbances in tooth eruption
- K00.7 Teething syndrome
- K00.8 Other disorders of tooth development
- K00.9 Disorder of tooth development, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the K00 range.
Amelogenesis Imperfecta
A clinically and genetically heterogeneous group of hereditary conditions characterized by malformed DENTAL ENAMEL, usually involving DENTAL ENAMEL HYPOPLASIA and/or TOOTH HYPOMINERALIZATION.
Anodontia
Congenital absence of the teeth. It may involve all (total anodontia) or only some of the teeth (partial anodontia, hypodontia), or six or more of the teeth (oligodontia) and both the deciduous and the permanent dentition, or only teeth of the permanent dentition.
Dentinogenesis Imperfecta
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Odontodysplasia
A localized arrested tooth development which appears to involve most commonly the anterior teeth, usually on one side of the midline, most often the maxillary central and lateral incisors. Roentgenographically, the teeth have a ghostlike appearance. Calcification and bits of prismatic enamel may be found in the pulp and the enamel is thin and absent in part. (Jablonski, Illustrated Dictionary of Dentistry, 1982)
Teething Syndrome
An expected condition experienced by children during the emergence of deciduous teeth. Though a full set of 20 primary teeth takes more than two years to emerge, teething syndrome may be variably noted from the first paired eruption (usually at the sixth month) until the last. Characteristically, irritability, inflamed gingivae, drooling and chewing on solid objects may be seen several days prior to the eruption with rapid resolution. Typically, the lower central incisors appear first followed by the upper central incisors. Molars and canine teeth are the last to erupt. Anecdotal associations with fever and diarrhea are misattributed.
Tooth, Supernumerary
An extra tooth, erupted or unerupted, resembling or unlike the other teeth in the group to which it belongs. Its presence may cause malposition of adjacent teeth or prevent their eruption.
About the K00 Code Range
These conditions affect how teeth develop or come in. The subdivisions distinguish differences in tooth number, size, shape, formation, and structure.
K00.0 describes absent teeth, while K00.1 describes extra teeth. K00.2 separates differences in size and shape from mottled teeth under K00.3. Other subdivisions identify disturbances in tooth formation (K00.4), inherited tooth structure (K00.5), and teeth coming in (K00.6). K00.7 identifies teething syndrome; K00.8 and K00.9 distinguish other from unspecified tooth development disorders.
Questions About This Page
How many billable codes are in the K00 range?
Of the 11 codes in this range, 10 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the K00 range classify?
The range classifies disorders of tooth development and eruption. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
