2027 ICD-10-CM Diagnosis Code H90.5Unspecified sensorineural hearing loss

Alternate terms and clinical phrases that map to this code.

• 10p partial monosomy syndrome
• 3-Methylglutaconic aciduria type 4
• Achalasia of esophagus
• Acquired sensorineural hearing loss
• Adult onset sensorineural hearing loss
• Adult-onset progressive leukoencephalopathy, early-onset deafness
• Albinism with deafness syndrome
• Anal atresia
• Aphonia, deafness, retinal dystrophy, bifid halluces, intellectual disability syndrome
• Arts syndrome
• Asymmetrical hearing loss
• Asymmetrical sensorineural hearing loss
• Auditory synaptopathy
• Autoimmune sensorineural hearing loss
• Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
• Autosomal dominant deafness with onychodystrophy syndrome
• Autosomal dominant ichthyosis
• Autosomal dominant myopia, midfacial retrusion, sensorineural hearing loss, rhizomelic dysplasia syndrome
• Autosomal recessive keratitis-ichthyosis-deafness syndrome
• Benign neoplasm of sacrococcygeal region
• Bilateral optic atrophy of eyes
• Björnstad syndrome
• Black locks, oculocutaneous albinism, AND deafness of the sensorineural type
• Cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome
• Central hearing loss
• Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
• Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome
• Childhood onset sensorineural hearing loss
• Chitty Hall Baraitser syndrome
• Cochlear nerve disorder
• Colobomatous microphthalmia
• Combined perceptive hearing loss
• COMMAD syndrome
• Complete deafness
• Congenital achalasia of esophagus
• Congenital atrophy of optic nerve
• Congenital calyceal diverticulum
• Congenital cataract with ataxia and deafness syndrome
• Congenital cataract with deafness and hypogonadism syndrome
• Congenital cataract, hearing loss, severe developmental delay syndrome
• Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome
• Congenital conductive hearing loss
• Congenital corneal dystrophy
• Congenital deafness
• Congenital dilatation of colon
• Congenital hearing disorder
• Congenital hereditary endothelial dystrophy
• Congenital hereditary endothelial dystrophy and perceptive deafness syndrome
• Congenital kyphoscoliosis
• Congenital kyphosis
• Congenital nephritis
• Congenital osteodystrophy
• Congenital prelingual deafness
• Congenital scoliosis deformity of spine
• Congenital sensorineural hearing loss
• Craniofacial deafness hand syndrome
• Cutaneous syndrome with ichthyosis
• Deafness and hypogonadism syndrome
• Deafness and oligodontia syndrome
• Deafness craniofacial syndrome
• Deafness with onychodystrophy syndrome
• Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
• Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome
• Deafness, vitiligo, achalasia syndrome
• Deafness-dystonia-optic neuronopathy syndrome
• Deletion of part of chromosome 10
• Deletion of part of chromosome 11
• Dentinogenesis imperfecta
• Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
• Developmental malformation, deafness, dystonia syndrome
• DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome
• Distal renal tubular acidosis
• Distal renal tubular acidosis co-occurrent with sensorineural deafness
• Diverticulum of renal calyx
• Dominant sensorineural hearing loss
• DOORS syndrome
• Duane retraction syndrome with congenital deafness
• Duane's syndrome
• Duane's syndrome, type 3
• Ectodermal dysplasia and sensorineural deafness syndrome
• Ehlers-Danlos syndrome kyphoscoliotic and deafness type
• Ehlers-Danlos syndrome kyphoscoliotic type
• Epiphyseal dysplasia, hearing loss, dysmorphism syndrome
• Essential tremor
• Familial steroid-resistant nephrotic syndrome with sensorineural deafness
• Gemignani syndrome
• Generalized dystonia
• Gingival fibromatosis
• Gingival fibromatosis with progressive deafness syndrome
• Globodontia
• Gonadal dysgenesis with auditory dysfunction, autosomal recessive inheritance
• Hereditary essential tremor
• Hereditary gingival fibromatosis
• Hereditary growth hormone deficiency
• Hereditary sensory neuropathy
• Heritable disorder of neutrophil function
• High frequency sensorineural hearing loss
• High frequency sensorineural hearing loss in right ear
• Hirschsprung disease with deafness and polydactyly syndrome
• Hypertelorism
• Hypertelorism, preauricular sinus, punctual pits, deafness syndrome
• Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome
• Hypoparathyroidism, deafness, renal disease syndrome
• Hypotrichosis and deafness syndrome
• Kawashima Tsuji syndrome
• Keipert syndrome
• KID syndrome
• Leber's amaurosis
• Lipoma of lower back
• Low frequency sensorineural hearing loss
• Lowe Kohn Cohen syndrome
• Lowry Yong syndrome
• Macrodontia
• Male infertility of chromosomal origin
• Mandibular hypoplasia, deafness, progeroid syndrome
• Maternal perinatal sensorineural hearing loss
• Maternally inherited cardiomyopathy and hearing loss syndrome
• Maternally inherited diabetes and deafness
• Megaloblastic anemia due to inborn errors of metabolism
• Megaloblastic anemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness
• MEGDEL syndrome
• Microcephaly, intellectual disability, sensorineural hearing loss, epilepsy, abnormal muscle tone syndrome
• Micromelia
• Mid frequency sensorineural hearing loss
• Mild sensorineural hearing loss
• Moderate sensorineural hearing loss
• Multiple malformation syndrome, moderate short stature, facial
• Narcolepsy
• Nathalie syndrome
• Neonatal sensorineural hearing loss
• Nephrosis, deafness, urinary tract, digital malformation syndrome
• Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
• Neural hearing loss
• Neural hearing loss of left ear
• Neural hearing loss of right ear
• Neutropenia, monocytopenia, deafness syndrome
• Non-acquired combined pituitary hormone deficiency, sensorineural hearing loss, spine abnormalities syndrome
• Non-syndromic mitochondrial sensorineural deafness
• Ocular albinism
• Ocular albinism with late-onset sensorineural deafness
• Oculootodental syndrome
• Oligodontia
• Olivopontocerebellar atrophy and deafness
• Olivopontocerebellar degeneration
• Panhypopituitarism
• PCNA-related progressive neurodegenerative photosensitivity syndrome
• Peripheral neuropathy with sensorineural hearing impairment syndrome
• Phocomelia
• Phocomelia, ectrodactyly, deafness and sinus arrhythmia syndrome
• Pili torti
• Postlingual sensorineural hearing loss
• Postnatal acquired sensorineural hearing loss
• Postoperative profound sensorineural hearing loss
• Preauricular fistula
• Premature canities
• Profound acquired hearing loss
• Profound hearing loss
• Profound sensorineural hearing loss
• Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
• Progressive macrocephaly
• Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome
• Recessive sensorineural hearing loss
• Renal caliceal diverticuli and deafness syndrome
• Renal tubular acidosis with progressive nerve deafness
• Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
• Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
• Retinitis pigmentosa-deafness syndrome
• Retinitis pigmentosa-deafness syndrome type 3
• Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
• Sellars Beighton syndrome
• Sensorineural deafness and male infertility
• Sensorineural deafness due to late congenital syphilis
• Sensorineural deafness with dilated cardiomyopathy syndrome
• Sensorineural hearing loss
• Sensorineural hearing loss of combined sites
• Sensorineural hearing loss of left ear
• Sensorineural hearing loss of right ear
• Sensorineural hearing loss, early graying, essential tremor syndrome
• Sensory hearing loss
• Senter syndrome
• Severe hearing loss
• Severe motor and intellectual disabilities, sensorineural deafness, dystonia syndrome
• Severe sensorineural hearing loss
• Severe X-linked intellectual disability Gustavson type
• Short stature, skeletal dysplasia, retinal degeneration, intellectual disability, sensorineural hearing loss syndrome
• Sinoatrial node dysfunction and deafness
• SLC12A2-related developmental delay, intellectual disability, sensorineural deafness syndrome
• Spondyloepiphyseal dysplasia MacDermot type
• Spondyloepiphyseal dysplasia, sensorineural hearing loss, intellectual disability, Leber congenital amaurosis syndrome
• Steroid-resistant nephrotic syndrome
• Sudden hearing loss
• Sudden sensorineural hearing loss
• Syndromic sensorineural deafness due to combined oxidative phosphorylation defect
• Thiamine-responsive megaloblastic anemia
• Thong Douglas Ferrante syndrome
• Tungland Bellman syndrome
• Wolfram syndrome
• Wolfram syndrome type 1
• Wolfram syndrome type 2
• Woodhouse Sakati syndrome
• X-linked sensorineural hearing loss

Instructions from the official ICD-10-CM Tabular List that apply to H90.5: its own notes plus those printed at H90 and Chapter 8. A note printed at a category, block or chapter applies to every code under it.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Instructional notes printed at other codes that name H90.5, its category, or a range that includes it.

Alphabetical index entries that point to this code.

• Deafness (acquired) (complete) (hereditary) (partial) H91.9

  • congenital H90.5

  • sensorineural H90.5

• Loss (of)

  • hearing See Also: Deafness;

    • central NOS H90.5

    • neural NOS H90.5

    • perceptive NOS H90.5

    • sensorineural NOS H90.5

    • sensory NOS H90.5