2026 ICD-10-CM Diagnosis Code H90.5Unspecified sensorineural hearing loss

ICD-10-CM Codes›H60–H95›H90-H94›H90

ICD-10-CM H90.5
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H90.5 is a billable ICD-10-CM diagnosis code for unspecified sensorineural hearing loss. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 154 through 156. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Hearing loss.

Code Identity

ICD-10-CM Code
H90.5
Billable Status
Yes — Valid for Submission
Code Describes
Unspecified sensorineural hearing loss
Short Description
Unspecified sensorineural hearing loss
Same as the full description in the CMS dataset.
Parent Code
H90
Conductive and sensorineural hearing loss

Code Classification

ChapterH60–H95Diseases of the ear and mastoid process
SectionH90-H94Other disorders of ear
CategoryH90Conductive and sensorineural hearing loss
This CodeH90.5Unspecified sensorineural hearing loss

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 10p partial monosomy syndrome
  • 3-Methylglutaconic aciduria type 4
  • Achalasia of esophagus
  • Acquired sensorineural hearing loss
  • Adult-onset progressive leukoencephalopathy, early-onset deafness
  • Albinism with deafness syndrome
  • Anal atresia
  • Aphonia, deafness, retinal dystrophy, bifid halluces, intellectual disability syndrome
  • Arts syndrome
  • Asymmetrical hearing loss
  • Asymmetrical sensorineural hearing loss
  • Auditory synaptopathy
  • Autoimmune sensorineural hearing loss
  • Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
  • Autosomal dominant deafness with onychodystrophy syndrome
  • Autosomal dominant ichthyosis
  • Autosomal dominant myopia, midfacial retrusion, sensorineural hearing loss, rhizomelic dysplasia syndrome
  • Autosomal recessive keratitis-ichthyosis-deafness syndrome
  • Benign neoplasm of sacrococcygeal region
  • Bilateral optic atrophy of eyes
  • Björnstad syndrome
  • Black locks, oculocutaneous albinism, AND deafness of the sensorineural type
  • Body height below reference range
  • Cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome
  • Central hearing loss
  • Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
  • Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome
  • Chitty Hall Baraitser syndrome
  • Chronic deafness
  • Colobomatous microphthalmia
  • Combined perceptive hearing loss
  • COMMAD syndrome
  • Complete deafness
  • Congenital achalasia of esophagus
  • Congenital atrophy of optic nerve
  • Congenital calyceal diverticulum
  • Congenital cataract with ataxia and deafness syndrome
  • Congenital cataract with deafness and hypogonadism syndrome
  • Congenital cataract, hearing loss, severe developmental delay syndrome
  • Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome
  • Congenital conductive hearing loss
  • Congenital corneal dystrophy
  • Congenital deafness
  • Congenital dilatation of colon
  • Congenital hearing disorder
  • Congenital hereditary endothelial dystrophy
  • Congenital hereditary endothelial dystrophy and perceptive deafness syndrome
  • Congenital kyphoscoliosis
  • Congenital kyphosis
  • Congenital nephritis
  • Congenital osteodystrophy
  • Congenital prelingual deafness
  • Congenital sensorineural hearing loss
  • Craniofacial deafness hand syndrome
  • Cutaneous syndrome with ichthyosis
  • Deafness and hypogonadism syndrome
  • Deafness and oligodontia syndrome
  • Deafness craniofacial syndrome
  • Deafness with onychodystrophy syndrome
  • Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
  • Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome
  • Deafness, vitiligo, achalasia syndrome
  • Deafness-dystonia-optic neuronopathy syndrome
  • Deletion of part of chromosome 10
  • Deletion of part of chromosome 11
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
  • Developmental malformation, deafness, dystonia syndrome
  • Diabetes mellitus associated with genetic syndrome
  • DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome
  • Distal renal tubular acidosis
  • Distal renal tubular acidosis co-occurrent with sensorineural deafness
  • Diverticulum of renal calyx
  • Dominant sensorineural hearing loss
  • DOORS syndrome
  • Duane retraction syndrome with congenital deafness
  • Duane's syndrome
  • Duane's syndrome, type 3
  • Ectodermal dysplasia and sensorineural deafness syndrome
  • Ehlers-Danlos syndrome kyphoscoliotic and deafness type
  • Ehlers-Danlos syndrome kyphoscoliotic type
  • End organ deafness
  • Epiphyseal dysplasia, hearing loss, dysmorphism syndrome
  • Essential tremor
  • Familial steroid-resistant nephrotic syndrome with sensorineural deafness
  • Gemignani syndrome
  • Generalized dystonia
  • Gingival fibromatosis
  • Gingival fibromatosis with progressive deafness syndrome
  • Globodontia
  • Gonadal dysgenesis with auditory dysfunction, autosomal recessive inheritance
  • Hereditary essential tremor
  • Hereditary gingival fibromatosis
  • Hereditary growth hormone deficiency
  • Hereditary sensory neuropathy
  • Heritable disorder of neutrophil function
  • High frequency sensorineural hearing loss
  • High frequency sensorineural hearing loss in right ear
  • Hirschsprung disease with deafness and polydactyly syndrome
  • Hypertelorism
  • Hypertelorism, preauricular sinus, punctual pits, deafness syndrome
  • Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome
  • Hypoparathyroidism, deafness, renal disease syndrome
  • Hypotrichosis and deafness syndrome
  • Kawashima Tsuji syndrome
  • Keipert syndrome
  • KID syndrome
  • Leber's amaurosis
  • Lipoma of lower back
  • Low frequency sensorineural hearing loss
  • Lowe Kohn Cohen syndrome
  • Lowry Yong syndrome
  • Macrodontia
  • Male infertility of chromosomal origin
  • Mandibular hypoplasia, deafness, progeroid syndrome
  • Maternal perinatal sensorineural hearing loss
  • Maternally inherited cardiomyopathy and hearing loss syndrome
  • Maternally inherited diabetes and deafness
  • Megaloblastic anemia due to inborn errors of metabolism
  • Megaloblastic anemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness
  • MEGDEL syndrome
  • Microcephaly, intellectual disability, sensorineural hearing loss, epilepsy, abnormal muscle tone syndrome
  • Micromelia
  • Multiple malformation syndrome, moderate short stature, facial
  • Narcolepsy
  • Nathalie syndrome
  • Neonatal sensorineural hearing loss
  • Nephrosis, deafness, urinary tract, digital malformation syndrome
  • Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
  • Neural hearing loss
  • Neural hearing loss of left ear
  • Neural hearing loss of right ear
  • Neutropenia, monocytopenia, deafness syndrome
  • Non-acquired combined pituitary hormone deficiency, sensorineural hearing loss, spine abnormalities syndrome
  • Non-syndromic mitochondrial sensorineural deafness
  • Ocular albinism
  • Ocular albinism with late-onset sensorineural deafness
  • Oculootodental syndrome
  • Oligodontia
  • Olivopontocerebellar atrophy and deafness
  • Olivopontocerebellar degeneration
  • Panhypopituitarism
  • PCNA-related progressive neurodegenerative photosensitivity syndrome
  • Peripheral neuropathy with sensorineural hearing impairment syndrome
  • Phocomelia
  • Phocomelia, ectrodactyly, deafness and sinus arrhythmia syndrome
  • Pili torti
  • Postnatal acquired sensorineural hearing loss
  • Postoperative profound sensorineural hearing loss
  • Preauricular fistula
  • Premature canities
  • Primary hypersomnia
  • Profound acquired hearing loss
  • Profound hearing loss
  • Profound sensorineural hearing loss
  • Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
  • Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome
  • Recessive sensorineural hearing loss
  • Renal caliceal diverticuli and deafness syndrome
  • Renal tubular acidosis with progressive nerve deafness
  • Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
  • Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
  • Retinitis pigmentosa-deafness syndrome
  • Retinitis pigmentosa-deafness syndrome type 3
  • Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
  • Sellars Beighton syndrome
  • Sensorineural deafness and male infertility
  • Sensorineural deafness due to late congenital syphilis
  • Sensorineural deafness with dilated cardiomyopathy syndrome
  • Sensorineural hearing loss
  • Sensorineural hearing loss in left ear
  • Sensorineural hearing loss in right ear
  • Sensorineural hearing loss of combined sites
  • Sensorineural hearing loss of left ear
  • Sensorineural hearing loss of right ear
  • Sensorineural hearing loss, early graying, essential tremor syndrome
  • Sensory hearing loss
  • Sensory neuropathy
  • Senter syndrome
  • Severe motor and intellectual disabilities, sensorineural deafness, dystonia syndrome
  • Severe X-linked intellectual disability Gustavson type
  • Short stature, skeletal dysplasia, retinal degeneration, intellectual disability, sensorineural hearing loss syndrome
  • Sinoatrial node dysfunction and deafness
  • Spondyloepiphyseal dysplasia MacDermot type
  • Spondyloepiphyseal dysplasia, sensorineural hearing loss, intellectual disability, Leber congenital amaurosis syndrome
  • Steroid-resistant nephrotic syndrome
  • Sudden hearing loss
  • Sudden sensorineural hearing loss
  • Syndromic sensorineural deafness due to combined oxidative phosphorylation defect
  • Thiamine-responsive megaloblastic anemia
  • Thong Douglas Ferrante syndrome
  • Tungland Bellman syndrome
  • Wolfram syndrome
  • Wolfram syndrome type 1
  • Wolfram syndrome type 2
  • Woodhouse Sakati syndrome
  • X-linked sensorineural hearing loss

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Central hearing loss NOS
  • Congenital deafness NOS
  • Neural hearing loss NOS
  • Perceptive hearing loss NOS
  • Sensorineural deafness NOS
  • Sensory hearing loss NOS

Type 1 Excludes

  • abnormal auditory perception H93.2
  • psychogenic deafness F44.6

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Deafness(acquired) (complete) (hereditary) (partial)
      • congenital
    • Deafness(acquired) (complete) (hereditary) (partial)
      • sensorineural
    • Loss(of)
      • hearing
        • central NOS
    • Loss(of)
      • hearing
        • neural NOS
    • Loss(of)
      • hearing
        • perceptive NOS
    • Loss(of)
      • hearing
        • sensorineural NOS
    • Loss(of)
      • hearing
        • sensory NOS

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EAR004
Hearing loss
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Dentinogenesis Imperfecta

    an autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. the dentin develops poorly with low mineral content while the pulp canal is obliterated.

  • Hypertelorism

    abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.

  • Narcolepsy

    a condition characterized by recurrent episodes of daytime somnolence and lapses in consciousness (microsomnias) that may be associated with automatic behaviors and amnesia. cataplexy; sleep paralysis, and hypnagogic hallucinations frequently accompany narcolepsy. the pathophysiology of this disorder includes sleep-onset rapid eye movement (rem) sleep, which normally follows stage iii or iv sleep. (from neurology 1998 feb;50(2 suppl 1):s2-s7)

  • Essential Tremor

    a relatively common disorder characterized by a fairly specific pattern of tremors which are most prominent in the upper extremities and neck, inducing titubations of the head. the tremor is usually mild, but when severe may be disabling. an autosomal dominant pattern of inheritance may occur in some families (i.e., familial tremor). (mov disord 1988;13(1):5-10)

  • Wolfram Syndrome

    a hereditary condition characterized by multiple symptoms including those of diabetes insipidus; diabetes mellitus; optic atrophy; and deafness. this syndrome is also known as didmoad (first letter of each word) and is usually associated with vasopressin deficiency. it is caused by mutations in gene wfs1 encoding wolframin, a 100-kda transmembrane protein.

  • AXIN2-Associated Polyposis|ODCRCS|Oligodontia-Colorectal Cancer Syndrome

    a rare autosomal dominant syndrome caused by constitutional (germline) loss-of-function variants in axin2 gene. it is characterized by the presence of multiple colorectal adenomatous polyps and an increased risk of colorectal carcinoma. oligodontia and ectodermal dysplasia may or may not be present.

  • EDA wt Allele|ECTD1|ED1|ED1-A1|ED1-A2|EDA|EDA-A1|EDA-A2|EDA1|EDA2|Ectodermal Dysplasia 1, Anhidrotic Gene|Ectodysplasin A wt Allele|Ectodysplasin Gene|HED|HED1|ODT1|Oligodontia 1 Gene|STHAGX1|TNLG7C|XHED|XLHED

    human eda wild-type allele is located in the vicinity of xq13.1 and is approximately 423 kb in length. this allele, which encodes ectodysplasin-a protein, is involved in the morphogenesis of ectodermally derived tissues. mutation of the gene is associated with x-linked hypohidrotic ectodermal dysplasia type 1 and x-linked, selective tooth agenesis type 1.

  • Oligodontia

    the congenital absence of six or more permanent teeth with the exclusion of third molars.

  • Dentinogenesis Imperfecta

    a congenital tooth development disorder caused by mutations in the dspp gene. the teeth are weak, discolored, and translucent.

  • Autosomal Recessive Distal Renal Tubular Acidosis-4 with Hemolytic Anemia|DRTA4

    an autosomal recessive type of distal renal tubular acidosis caused by mutation(s) in the slc4a1 gene, encoding band 3 anion transport protein. additionally, it may be characterized by hemolytic anemia.

  • Distal Renal Tubular Acidosis

    failure of the renal tubules of the kidney to excrete urine of sufficient acidity, resulting in metabolic acidosis.

  • Narcolepsy

    a sleep disorder characterized by a tendency for excessive sleepiness during the day which occurs even after adequate sleep in the nighttime. the persons who suffer from this condition experience fatigue and may fall asleep at inappropriate times during the day.

  • Narcolepsy in Conditions Classified Elsewhere with Cataplexy|Narcolepsy in conditions classified elsewhere with cataplexy

    evidence of narcolepsy in conditions classified elsewhere with cataplexy.

  • Narcolepsy in Conditions Classified Elsewhere without Cataplexy|Narcolepsy in conditions classified elsewhere without cataplexy

    evidence of narcolepsy in conditions classified elsewhere without cataplexy.

  • Narcolepsy with Cataplexy|Narcolepsy with cataplexy

    evidence of narcolepsy with cataplexy.

  • Narcolepsy without Cataplexy|Narcolepsy without cataplexy

    evidence of narcolepsy without cataplexy.

  • Essential Tremor

    a movement disorder characterized by involuntary and rhythmic shaking of parts of the body, most often the hands or arms, that can be triggered or worsened by physical or environmental stressors. essential tremor may be progressive and can be inherited in an autosomal dominant manner.

  • Central Hearing Loss

    hearing loss resulting from disorders of the central nervous system auditory pathways.

  • Congenital Kyphosis

    an abnormally increased curvature of the thoracic portion of the spine that is present at the time of birth.

  • Sensory Hearing Loss

    hearing loss caused by damage to the cochlea in the inner ear.

Patient EducationClinical

Hearing Disorders and Deafness

It's frustrating to be unable to hear well enough to enjoy talking with friends or family. Hearing disorders make it hard, but not impossible, to hear. They can often be helped. Deafness can keep you from hearing sound at all.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H90.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
389.10 Sensorneur hear loss NOS
Approximate The match is approximate rather than exact.
ICD-9-CM
389.14 Central hearing loss
Approximate The match is approximate rather than exact.
ICD-9-CM
389.16 Sensoneur hear loss asym
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H90.5Overview

Is H90.5 (Conductive and sensorineural hearing loss) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report unspecified sensorineural hearing loss on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does H90.5 group to?

When unspecified sensorineural hearing loss is the principal diagnosis on an inpatient stay, it groups to MS-DRG 154, 155, 156, with relative weights from 0.6911 to 1.5635 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H90.5?

Under the General Equivalence Mappings, unspecified sensorineural hearing loss converts to ICD-9-CM 389.10 (sensorneur hear loss NOS), 389.14 (central hearing loss), and 389.16 (sensoneur hear loss asym). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.