ICD-10 Diagnosis Code Q04.3

Other reduction deformities of brain

Diagnosis Code Q04.3

ICD-10: Q04.3
Short Description: Other reduction deformities of brain
Long Description: Other reduction deformities of brain
This is the 2017 version of the ICD-10-CM diagnosis code Q04.3

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of brain (Q04)

Information for Medical Professionals

Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q04.3 is exempt from POA reporting.

  • Abnormality of neurogenesis
  • Absence of septum pellucidum
  • Agenesis of cerebellum
  • Agenesis of cerebrum
  • Agenesis of corpus callosum
  • Aicardi's syndrome
  • Anomalies of hypothalamus
  • Aplasia of cerebellum
  • Aplasia of corpus callosum
  • Aplasia of the vermis
  • Atelencephaly
  • Atrophy of corpus callosum
  • Cerebral cortical dysgenesis
  • Cerebral dysgenesis
  • Cerebral dysgenesis
  • Congenital absence of part of brain
  • Congenital agenesis of brainstem nuclei
  • Congenital anomaly of cerebrum
  • Congenital bilateral perisylvian syndrome
  • Congenital cerebellar hypoplasia
  • Congenital chorioretinal degeneration
  • Congenital hypoplasia of brain
  • Congenital hypoplasia of cerebrum
  • Congenital hypoplasia of inner granular layer of cerebellum
  • Congenital hypoplasia of part of brain
  • Congenital malformation of corpus callosum
  • Congenital pontocerebellar hypoplasia
  • Defect of telencephalic division
  • Dyke-Davidoff-Masson syndrome
  • Dysgenesis of the brainstem
  • Dysgenesis of the cerebellum
  • Dysplasia of cerebral cortex
  • Early secondary malformation of the central nervous system
  • Endosteal hyperostoses
  • Endosteal hyperostoses with cerebellar hypoplasia
  • Familial aplasia of the vermis
  • Granular cell hypoplasia
  • Hemispheric cerebellar agenesis
  • Hemispheric cerebral agenesis
  • Hydranencephaly
  • Hydranencephaly with proliferative vasculopathy
  • Hypoplasia of brain gyri
  • Lissencephaly
  • Microgyria
  • Osteochondrodysplasia with osteopetrosis
  • Partial absence of septum pellucidum
  • Pontoneocerebellar hypoplasia
  • Reduction anomaly of hypothalamus
  • Reduction deformities of brain
  • Rhombencephalosynapsis
  • Type 1 lissencephaly
  • Type 2 lissencephaly

Index of Diseases and Injuries
References found for the code Q04.3 in the Index of Diseases and Injuries:

Information for Patients

Brain Malformations

Also called: Cephalic disorders

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines, infections, or radiation during pregnancy interferes with brain development. Parts of the brain may be missing, abnormally small or large, or not fully developed.

Treatment depends upon the problem. In many cases, treatment only helps with symptoms. It may include antiseizure medicines, shunts to drain fluid from the brain, and physical therapy.

There are head malformations that do not involve the brain. Craniofacial disorders are the result of abnormal growth of soft tissue and bones in the face and head. It's common for new babies to have slightly uneven heads, but parents should watch the shape of their baby's head for possible problems.

NIH: National Institute of Neurological Disorders and Stroke

  • Brain surgery
  • Brain surgery - discharge

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Isolated lissencephaly sequence Isolated lissencephaly sequence (ILS) is a condition that affects brain development before birth. Normally, the cells that make up the exterior of the brain (cerebral cortex) are well-organized, multi-layered, and arranged into many folds and grooves (gyri). In people with ILS, the cells of the cerebral cortex are disorganized, and the brain surface is abnormally smooth with an absence (agyria) or reduction (pachygyria) of folds and grooves. In most cases, these abnormalities impair brain growth, causing the brain to be smaller than normal (microcephaly). This underdevelopment of the brain causes severe intellectual disability, delayed development, and recurrent seizures (epilepsy) in individuals with ILS.More than 90 percent of individuals with ILS develop epilepsy, often within the first year of life. Up to 80 percent of infants with ILS have a type of seizure called infantile spasms, these seizures can be severe enough to cause brain dysfunction (epileptic encephalopathy). After the first months of life, most children with ILS develop a variety of seizure types, including persisting infantile spasms, short periods of loss of consciousness (absence seizures); sudden episodes of weak muscle tone (drop attacks); rapid, uncontrolled muscle jerks (myoclonic seizures); and episodes of muscle rigidity, convulsions, and loss of consciousness (tonic-clonic seizures).Infants with ILS may have poor muscle tone (hypotonia) and difficulty feeding, which leads to poor growth overall. Hypotonia also affects the muscles used for breathing, which often causes breathing problems that can lead to a life-threatening bacterial lung infection known as aspiration pneumonia. Children with ILS often develop muscle stiffness (spasticity) in their arms and legs and an abnormal side-to-side curvature of the spine (scoliosis). Rarely, the muscle stiffness will progress to paralysis (spastic paraplegia). Individuals with ILS cannot walk and rarely crawl. Most children with ILS do not develop communication skills.
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X-linked lissencephaly with abnormal genitalia X-linked lissencephaly with abnormal genitalia (XLAG) is a condition that affects the development of the brain and genitalia. It occurs most often in males.XLAG is characterized by abnormal brain development that results in the brain having a smooth appearance (lissencephaly) instead of its normal folds and grooves. Individuals without any folds in the brain (agyria) typically have more severe symptoms than people with reduced folds and grooves (pachygyria). Individuals with XLAG may also have a lack of development (agenesis) of the tissue connecting the left and right halves of the brain (corpus callosum). The brain abnormalities can cause severe intellectual disability and developmental delay, abnormal muscle stiffness (spasticity), weak muscle tone (hypotonia), and feeding difficulties. Starting soon after birth, babies with XLAG have frequent and recurrent seizures (epilepsy). Most children with XLAG do not survive past early childhood.Another key feature of XLAG in males is abnormal genitalia that can include an unusually small penis (micropenis), undescended testes (cryptorchidism), or external genitalia that do not look clearly male or clearly female (ambiguous genitalia).Additional signs and symptoms of XLAG include chronic diarrhea, periods of increased blood sugar (transient hyperglycemia), and problems with body temperature regulation.
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Lissencephaly with cerebellar hypoplasia Lissencephaly with cerebellar hypoplasia (LCH) affects brain development, resulting in the brain having a smooth appearance (lissencephaly) instead of its normal folds and grooves. In addition, the part of the brain that coordinates movement is unusually small and underdeveloped (cerebellar hypoplasia). Other parts of the brain are also often underdeveloped in LCH, including the hippocampus, which plays a role in learning and memory, and the part of the brain that is connected to the spinal cord (the brainstem).Individuals with LCH have moderate to severe intellectual disability and delayed development. They have few or no communication skills, extremely poor muscle tone (hypotonia), problems with coordination and balance (ataxia), and difficulty sitting or standing without support. Most affected children experience recurrent seizures (epilepsy) that begin within the first months of life. Some affected individuals have nearsightedness (myopia), involuntary eye movements (nystagmus), or puffiness or swelling caused by a buildup of fluids in the body's tissues (lymphedema).
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